title: Pulmonary capillary hemangiomatosis with severe pulmonary hypertension.
abstract: Pulmonary capillary hemangiomatosis (PCH) is a rare idiopathic lung disorder that occurs in young patients and leads to pulmonary hypertension (PH). It is difficult to diagnosis in the early stage and is often mistaken for primary PH; in almost all cases of PCH, the correct diagnosis is not made until autopsy. In the present case of PCH, the patient had severe pulmonary hypertension and died of respiratory failure. Pathologically, PCH is characterized by proliferation of benign thin-walled capillary sized blood vessels in the lung parenchyma.
authors.affiliation: Department of Cardiovascular Medicine, Kyushu University Graduate School of Medical Sciences, Fukuoka, Japan.
authors.forename: Koji
authors.initials: K
authors.lastname: Ito
authors.forename: Toshihiro
authors.initials: T
authors.lastname: Ichiki
authors.forename: Keiji
authors.initials: K
authors.lastname: Ohi
authors.forename: Kensuke
authors.initials: K
authors.lastname: Egashira
authors.forename: Mituhiko
authors.initials: M
authors.lastname: Ohta
authors.forename: Kenichi
authors.initials: K
authors.lastname: Taguchi
authors.forename: Akira
authors.initials: A
authors.lastname: Takeshita
mesh_terms: D000328:Adult; D003937:Diagnosis, Differential; D004452:Echocardiography; D004562:Electrocardiography; D017809:Fatal Outcome; D018324:Hemangioma, Capillary / Q000150:complications* / Q000175:diagnosis* / Q000473:pathology; D006801:Humans; D006976:Hypertension, Pulmonary / Q000209:etiology*; D008175:Lung Neoplasms / Q000150:complications* / Q000175:diagnosis* / Q000473:pathology; D008297:Male; D013902:Radiography, Thoracic; D014057:Tomography, X-Ray Computed