Nevus lipomatosus cutaneous superficialis of the clitoris.
BACKGROUND
Nevus lipomatosus cutaneous superficialis (NLCS) is a relatively rare condition. Although NLCS can affect any region of the entire body, no case of NLCS in the clitoris has ever been reported.


OBJECTIVE
To report a case of NLCS of the clitoris that presented manifestations that were similar to female pseudohermaphrodism.


METHODS
This is a case report and review of the literature.


RESULTS
A congenital, soft, skin-colored lesion of the clitoris in a 1-year-old girl resembled female pseudohermaphrodism. It was resected, and the histologic diagnosis was NLCS. Postoperatively, there was no subsequent change in the lesion during the 3-year follow-up period.


CONCLUSIONS
We reported a case of congenital solitary NLCS of the clitoris. Although NLCS might be a relatively rare condition, we should consider it in the differential diagnosis of female pseudohermaphrodism.
Hattori
Ryo
R
Department of Plastic Surgery, Osaka University Graduate School of Medicine, Suita-shi, Japan.
Kubo
Tateki
T
Yano
Kenji
K
Tanemura
Atsushi
A
Yamaguchi
Yuji
Y
Itami
Satoshi
S
Hosokawa
Ko
K
D002987:Clitoris; D003937:Diagnosis, Differential; D012734:Disorders of Sex Development / Q000175:diagnosis*; D005260:Female; D006801:Humans; D007223:Infant; D008068:Lipomatosis / Q000151:congenital / Q000175:diagnosis / Q000473:pathology* / Q000601:surgery; D009506:Nevus / Q000151:congenital / Q000175:diagnosis / Q000473:pathology* / Q000601:surgery; D012878:Skin Neoplasms / Q000151:congenital / Q000175:diagnosis / Q000473:pathology* / Q000601:surgery