title: [Pulmonary Artery Sarcoma - diagnostic and treatment difficulties].
abstract: Primary Pulmonary Artery Sarcoma is a rare entity, which shares some clinical features with Thromboembolic Pulmonary Disease (TEPD), complicating differential diagnosis. The authors report a Clinical Case of a Primary Pulmonary Artery Sarcoma in a 59 years old man, admitted with a history of dyspnoea on exertion, chest pain and general symptoms. Chest X-ray, Computed Tomography Scan, Angiographies and Magnetic Resonance Imaging suggested TEPD. Blood Analysis performed before anticoagulation therapy: Lupus Anticoagulant-and Ig M Anticardiolipin +. Our presumptive initial diagnosis was TEPD in a patient with a hypercoagulable state. Intravenous heparin was started, with some clinical improvement but 2 months later he was readmitted, due to clinical and radiological deterioration. Pulmonary Thromboendarterectomy was considered but a right pneumonectomy was necessary because of bleeding. He died of ARDS in a single lung in the 7th day after surgery. Pathology revealed pulmonary artery sarcoma with pulmonary and pleural metastases.
authors.affiliation: Centro Hospitalar de Vila Nova de Gaia.
authors.forename: Sofia
authors.initials: S
authors.lastname: Neves
authors.forename: J
authors.initials: J
authors.lastname: San José
authors.forename: H Vaz
authors.initials: HV
authors.lastname: Velho
authors.forename: M
authors.initials: M
authors.lastname: Oliveira
authors.forename: I
authors.initials: I
authors.lastname: Esteves
authors.forename: S
authors.initials: S
authors.lastname: Torres
authors.forename: A M
authors.initials: AM
authors.lastname: Magalhães
mesh_terms: D006801:Humans; D008297:Male; D008875:Middle Aged; D011651:Pulmonary Artery; D012509:Sarcoma / Q000175:diagnosis / Q000628:therapy; D019043:Vascular Neoplasms / Q000175:diagnosis / Q000628:therapy
vernacular_title: Sarcoma da artéria pulmonar-dificuldades diagnósticas e terapêuticas.