[Pulmonary Artery Sarcoma - diagnostic and treatment difficulties].
Primary Pulmonary Artery Sarcoma is a rare entity, which shares some clinical features with Thromboembolic Pulmonary Disease (TEPD), complicating differential diagnosis. The authors report a Clinical Case of a Primary Pulmonary Artery Sarcoma in a 59 years old man, admitted with a history of dyspnoea on exertion, chest pain and general symptoms. Chest X-ray, Computed Tomography Scan, Angiographies and Magnetic Resonance Imaging suggested TEPD. Blood Analysis performed before anticoagulation therapy: Lupus Anticoagulant-and Ig M Anticardiolipin +. Our presumptive initial diagnosis was TEPD in a patient with a hypercoagulable state. Intravenous heparin was started, with some clinical improvement but 2 months later he was readmitted, due to clinical and radiological deterioration. Pulmonary Thromboendarterectomy was considered but a right pneumonectomy was necessary because of bleeding. He died of ARDS in a single lung in the 7th day after surgery. Pathology revealed pulmonary artery sarcoma with pulmonary and pleural metastases.
Neves
Sofia
S
Centro Hospitalar de Vila Nova de Gaia.
San José
J
J
Velho
H Vaz
HV
Oliveira
M
M
Esteves
I
I
Torres
S
S
Magalhães
A M
AM
D006801:Humans; D008297:Male; D008875:Middle Aged; D011651:Pulmonary Artery; D012509:Sarcoma / Q000175:diagnosis / Q000628:therapy; D019043:Vascular Neoplasms / Q000175:diagnosis / Q000628:therapy
Sarcoma da artéria pulmonar-dificuldades diagnósticas e terapêuticas.