Unusual presentation of posterior mediastinal chordoma in a 2-year-old boy.
Chordoma is a rare and slow-growing malignant neoplasm that arises from the embryonic notochord. It is rare to see a thoracic chordoma presenting as a posterior mediastinal mass with pleural seeding in a child. The authors report a chordoma of the thoracic spine with posterior mediastinal extension and pleural seeding in a 2-year-old boy who presented with asymmetric bilateral hand temperature and lower limb paralysis. The clinical course progressed rapidly, resulting in death.
Huang
Shih-Ming
SM
Department of Pediatrics, Veterans General Hospital-Kaohsiung, National Yang-Ming University, Taiwan, Republic of China.
Chen
Chu-Chin
CC
Chiu
Pao-Chin
PC
Lai
Ping-Hong
PH
Ho
Jih-Tsun
JT
Tseng
Hui-Hwa
HH
D002675:Child, Preschool; D002817:Chordoma / Q000150:complications* / Q000175:diagnosis / Q000188:drug therapy / Q000532:radiotherapy / Q000556:secondary; D003131:Combined Modality Therapy; D017809:Fatal Outcome; D006225:Hand / Q000098:blood supply; D006801:Humans; D007035:Hypothermia / Q000209:etiology*; D007796:Laminectomy; D008175:Lung Neoplasms / Q000556:secondary; D008297:Male; D008479:Mediastinal Neoplasms / Q000150:complications* / Q000175:diagnosis / Q000188:drug therapy / Q000532:radiotherapy; D010264:Paraplegia / Q000209:etiology*; D010997:Pleural Neoplasms / Q000556:secondary; D018714:Radiotherapy, Adjuvant; D013117:Spinal Cord Compression / Q000209:etiology