Congenital analgia syndrome.
Hereditary sensory and autonomic neuropathy is a rare syndrome which is seen in early childhood. Five different types have been described. Absence of pain and self-mutilation are characteristic findings of this syndrome. This report describes one female and two male children with the syndrome. The most severe oral consequence of their disorder was damage to the oral tissues and tongue. The primary aim in management was to monitor the eruption of the permanent teeth.
Aren
Gamze
G
University of Istanbul Faculty of Dentistry, Department of Pediatric Dentistry, Capa, Istanbul, Turkey. gamzearen@hotmail.com
Sepet
Elif
E
Erbay
Elif
E
Ermiş
Ismail
I