title: [Tetralogy of Fallot with pulmonary atresia and major aortopulmonary collateral arteries].
abstract: Patients with tetralogy of Fallot (TOF), pulmonary atresia (PA), and major aortopulmonary collateral artery (MAPCA) usually need some staged surgical procedures. There is no clear consensus to the initial procedure and also the most proper initial procedure is different in each case. We report here a case of 6-year-old girl with TOF, PA, and MAPCA. We performed right ventricular outflow tract reconstruction (RVOTR) for the initial procedure because her pulmonary artery was extremely diminutive. Her pulmonary artery got good growth after the palliative surgery. Five years later she underwent complete repair after two other surgeries and 1 interventional embolization. RVOTR is a useful procedure for pulmonary artery growth, but it should be well considered that what size of RVOTR is needed in each case.
mesh_terms: D019917:Blood Vessel Prosthesis Implantation; D006348:Cardiac Surgical Procedures / Q000379:methods*; D002648:Child; D003097:Collateral Circulation; D005260:Female; D006801:Humans; D018633:Pulmonary Atresia / Q000150:complications*; D011652:Pulmonary Circulation; D013771:Tetralogy of Fallot / Q000150:complications / Q000601:surgery*