title: Langerhans' cell histiocytosis of the clivus: case report and literature review.
abstract: This report describes a 5-year-old girl with Langerhans' cell histiocytosis (LCH) of the clivus. To date only five patients, including our patient, have been described with LCH at this site. Our patient differs from those previously reported by her atypical clinical presentation with torticollis, but without a sixth nerve palsy. In addition, she is the first patient to present with concomitant disease elsewhere at the time of diagnosis, i.e. both femoral necks and left proximal humerus. Our patient thus presents unique features and underlines the importance of including LCH in the differential diagnosis of erosive lesions of the clivus.
authors.affiliation: Department of Radiology, Our Lady's Hospital for Sick Children, Crumlin, Dublin 12, Ireland. majadonhurley@eircom.net
authors.forename: Maja E
authors.initials: ME
authors.lastname: Hurley
authors.forename: Anne
authors.initials: A
authors.lastname: O'Meara
authors.forename: Esmond
authors.initials: E
authors.lastname: Fogarty
authors.forename: Roisin
authors.initials: R
authors.lastname: Hayes
mesh_terms: D002675:Child, Preschool; D003388:Cranial Fossa, Posterior; D005260:Female; D006646:Histiocytosis, Langerhans-Cell / Q000175:diagnosis*; D006801:Humans