title: [Primary hypertrophic osteoarthropathy without cutaneous involvement (Currarino's disease)].
abstract: BACKGROUND
  Hypertrophic osteoarthropathy (HOA) is a syndrome associating hippocratic fingers, arthropathy and periostosis of long bones. Currarino's disease, considered at present as a clinical form of primary HOA, is characterized by the absence of pachydermia.
  
  
  METHODS
  A 24-year-old Caucasian man, consulted for a painful swelling of both ankles that had developed over the past year. Clinical examination revealed hippocratic fingers without pachydermia. The ankles were swollen. The X-rays showed periosteal apposition and an acro-osteolysis. In view of this triad: arthropathy, hippocratic fingers and periostosis, primary HOA without cutaneous involvement or Currarino's disease was diagnosed. The search for a secondary cause remained negative. Clinical improvement was obtained after 15 months with non-steroidal anti-inflammatory drugs (NSAID) and colchicine.
  
  
  CONCLUSIONS
  Although exceptional, primary HOA without cutaneous involvement is a genetic disease which must not be ignored.
authors.affiliation: Service de médecine interne, Hôpital des forces de sécurité intérieure de la Marsa, Tunis.
authors.forename: S K
authors.initials: SK
authors.lastname: Ben Hamida
authors.forename: H
authors.initials: H
authors.lastname: Kédadi
authors.forename: F
authors.initials: F
authors.lastname: Derbel
authors.forename: M
authors.initials: M
authors.lastname: Kchir
authors.forename: H
authors.initials: H
authors.lastname: Bouhaoula
authors.forename: S M
authors.initials: SM
authors.lastname: Hadj
authors.forename: A
authors.initials: A
authors.lastname: Mestiri
authors.forename: R
authors.initials: R
authors.lastname: Zouari
authors.forename: M H
authors.initials: MH
authors.lastname: Dougui
mesh_terms: D000328:Adult; D006801:Humans; D008297:Male; D010004:Osteoarthropathy, Primary Hypertrophic / Q000000981:diagnostic imaging*; D011859:Radiography