[Primary hypertrophic osteoarthropathy without cutaneous involvement (Currarino's disease)].
BACKGROUND
Hypertrophic osteoarthropathy (HOA) is a syndrome associating hippocratic fingers, arthropathy and periostosis of long bones. Currarino's disease, considered at present as a clinical form of primary HOA, is characterized by the absence of pachydermia.


METHODS
A 24-year-old Caucasian man, consulted for a painful swelling of both ankles that had developed over the past year. Clinical examination revealed hippocratic fingers without pachydermia. The ankles were swollen. The X-rays showed periosteal apposition and an acro-osteolysis. In view of this triad: arthropathy, hippocratic fingers and periostosis, primary HOA without cutaneous involvement or Currarino's disease was diagnosed. The search for a secondary cause remained negative. Clinical improvement was obtained after 15 months with non-steroidal anti-inflammatory drugs (NSAID) and colchicine.


CONCLUSIONS
Although exceptional, primary HOA without cutaneous involvement is a genetic disease which must not be ignored.
Ben Hamida
S K
SK
Service de médecine interne, Hôpital des forces de sécurité intérieure de la Marsa, Tunis.
Kédadi
H
H
Derbel
F
F
Kchir
M
M
Bouhaoula
H
H
Hadj
S M
SM
Mestiri
A
A
Zouari
R
R
Dougui
M H
MH
D000328:Adult; D006801:Humans; D008297:Male; D010004:Osteoarthropathy, Primary Hypertrophic / Q000000981:diagnostic imaging*; D011859:Radiography