Vascular ring due to double aortic arch with atretic left arch and left ligamentum arteriosum: report of one case.
A 1-day-old female infant presented with vomiting immediately after feeding and shortness of breath after birth. Esophagography revealed external compression of the esophagus. Echocardiography showed a right aortic arch with mirror image branching of brachiocephalic vessels without intracardiac anomalies. Left ventriculography confirmed the echocardiography findings and revealed a tenting of the proximal part of the left subclavian artery and a blind pouch of Kommerell diverticulum at the descending aorta. The patient underwent surgery, which revealed a complete vascular ring compressing the trachea and the esophagus. The ring was formed by a right aortic arch, atretic left arch and left ligamentum arteriosum. Following surgical division of the ligamentum arteriosum and the atretic left arch, the symptoms subsequently improved.
Hong
Yin-Tai
YT
Department of Pediatrics, Taichung Veterans General Hospital, No. 160, Sec. 3, Chung-Kang Road, Taichung 40705, Taiwan.
Fu
Yun-Ching
YC
Chen
Chao-Huei
CH
Jan
Sheng-Ling
SL
Wang
Teh-Ming
TM
Chang
Yen
Y
Chi
Ching-Shiang
CS
D001013:Aorta, Thoracic / Q000002:abnormalities*; D004947:Esophagus / Q000473:pathology; D005260:Female; D006801:Humans; D007231:Infant, Newborn; D011651:Pulmonary Artery / Q000473:pathology*; D014132:Trachea / Q000473:pathology