Mesectodermal leiomyosarcoma of the ciliary body.
We report a case of low-grade mesectodermal leiomyosarcoma of the ciliary body, an extremely rare tumor of neural crest origin, occurring in a 12-year-old boy. MR imaging showed a well-marginated, ovoid soft tissue mass at the right temporal ciliary body, accompanied by total retinal detachment. The mass was slightly hyperintense relative to contralateral vitreous on T1-weighted images and markedly hypointense on T2-weighted images and enhanced very well. Initial biopsy of the mass suggested a peripheral nerve sheath tumor. The mass grew rapidly after biopsy, and enucleation was performed. The final diagnosis based on histology and immunohistochemistry was a low-grade mesectodermal leiomyosarcoma. To our knowledge, this is the first reported case of a malignant form of mesectodermal leiomyoma of the ciliary body.
Park
Sun-Won
SW
Department of Radiology, Inha University Hospital, Incheon, Korea.
Kim
Hyung-Jin
HJ
Chin
Hee-Seung
HS
Tae
Kee-Sun
KS
Han
Jee-Young
JY
D002648:Child; D002924:Ciliary Body; D003937:Diagnosis, Differential; D006801:Humans; D007890:Leiomyosarcoma / Q000175:diagnosis* / Q000473:pathology; D008279:Magnetic Resonance Imaging; D008297:Male; D014604:Uveal Neoplasms / Q000175:diagnosis* / Q000473:pathology