title: The tongue-base suspension using Repose bone screw system in a child with Simpson-Golabi-Behmel syndrome. Case report.
abstract: Obstructive sleep apnea syndrome is one of the most frequent manifestations of upper airway obstruction. Several approaches have been proposed to solve this problem with the aim to avoid tracheotomy especially in children. We observed a child affected by Simpson-Golabi-Behmel syndrome presenting severe OSAS. He underwent tongue-base suspension using the Repose system with significant improvement of the polysomnographic parameters and of the clinical conditions. Tongue suspension with this technique effectively prevent tongue-base collapse, avoiding tracheotomy or increased morbidity caused by a more invasive procedure. Besides it does not interfere with the patient's cranio-facial growth and future occlusion.
authors.affiliation: Institute of Otolaryngology, Catholic University of the Sacred Heart, Largo A. Gemelli 8, 00168 Rome, Italy.
authors.forename: Gaetano
authors.initials: G
authors.lastname: Paludetti
authors.forename: Giuseppe
authors.initials: G
authors.lastname: Zampino
authors.forename: Giacomo
authors.initials: G
authors.lastname: Della Marca
authors.forename: Stefano
authors.initials: S
authors.lastname: Di Girolamo
authors.forename: Emanuele
authors.initials: E
authors.lastname: Scarano
authors.forename: Mario
authors.initials: M
authors.lastname: Rigante
mesh_terms: D001863:Bone Screws; D019465:Craniofacial Abnormalities / Q000150:complications*; D006801:Humans; D007223:Infant; D008297:Male; D013517:Otorhinolaryngologic Surgical Procedures / Q000379:methods*; D020181:Sleep Apnea, Obstructive / Q000209:etiology / Q000601:surgery*; D013536:Suture Techniques; D013577:Syndrome; D014059:Tongue / Q000601:surgery*