Aerodigestive amyloidosis presenting as acute asthma.
Aerodigestive amyloidosis is a rare disorder characterized by fibrillar protein deposition in the aerodigestive tree. We present a case of a 19-year-old Chinese gentleman whose diagnosis was initially missed as he presented with features suggestive of severe bronchial asthma and was intubated and ventilated. He subsequently presented 2 years later with severe stridor and required emergency tracheostomy. Current literature is reviewed for the histopathology, common clinical features, radiological findings and treatment options for aerodigestive amyloidosis.
ENT Department, Hospital Universiti Kebangsaan Malaysia, Jalan Tenteram, Cheras, 56000, Kuala Lumpur.
S S
SS
Sreetharan
N
N
Prepageran
A
A
Razak
K A
KA
Valuyeetham
D000208:Acute Disease; D000328:Adult; D000686:Amyloidosis / Q000150:complications / Q000175:diagnosis* / Q000628:therapy; D001249:Asthma / Q000175:diagnosis / Q000209:etiology* / Q000628:therapy; D003937:Diagnosis, Differential; D004066:Digestive System Diseases / Q000150:complications / Q000175:diagnosis* / Q000628:therapy; D006801:Humans; D008297:Male; D012140:Respiratory Tract Diseases / Q000150:complications / Q000175:diagnosis* / Q000628:therapy