Aerodigestive amyloidosis presenting as acute asthma.
Aerodigestive amyloidosis is a rare disorder characterized by fibrillar protein deposition in the aerodigestive tree. We present a case of a 19-year-old Chinese gentleman whose diagnosis was initially missed as he presented with features suggestive of severe bronchial asthma and was intubated and ventilated. He subsequently presented 2 years later with severe stridor and required emergency tracheostomy. Current literature is reviewed for the histopathology, common clinical features, radiological findings and treatment options for aerodigestive amyloidosis.
Sreetharan
S S
SS
ENT Department, Hospital Universiti Kebangsaan Malaysia, Jalan Tenteram, Cheras, 56000, Kuala Lumpur.
Prepageran
N
N
Razak
A
A
Valuyeetham
K A
KA
D000208:Acute Disease; D000328:Adult; D000686:Amyloidosis / Q000150:complications / Q000175:diagnosis* / Q000628:therapy; D001249:Asthma / Q000175:diagnosis / Q000209:etiology* / Q000628:therapy; D003937:Diagnosis, Differential; D004066:Digestive System Diseases / Q000150:complications / Q000175:diagnosis* / Q000628:therapy; D006801:Humans; D008297:Male; D012140:Respiratory Tract Diseases / Q000150:complications / Q000175:diagnosis* / Q000628:therapy