Gastroschisis with omphalomesenteric artery remnant, colonic atresia and arthrogryposis multiplex congenita.
The pathogenesis of gastroschisis (GS) is controversial. We present a case of GS complicated by colonic atresia and arthrogryposis multiplex congenita. This association is attributed to intrauterine vascular compromise. Furthermore, a probable omphalomesenteric artery (OMA) remnant was found on the right side of the defect opposite the umbilicus and extended with bifurcation to the mesenteries of the colon and ileum, between which colonic atresia occurred. This provided further evidence in support of the hypothesis that GS is caused by an intrauterine interruption of OMA.
Komuro
H
H
Department of Paediatric Surgery, Institute of Clinical Medicine, University of Tsukuba, Ibaraki, Japan. hiro-kom@md.tsukuba.ac.jp
Watanabe
M
M
Matoba
K
K
Kaneko
M
M
D000015:Abnormalities, Multiple; D001176:Arthrogryposis; D003106:Colon / Q000002:abnormalities*; D020139:Gastroschisis; D006801:Humans; D007230:Infant, Low Birth Weight; D007231:Infant, Newborn; D007234:Infant, Premature; D007409:Intestinal Atresia; D008297:Male; D008638:Mesenteric Arteries / Q000002:abnormalities*; D014472:Umbilicus / Q000002:abnormalities*