title: A case of inflammatory pseudotumor of the liver hilum successfully treated with aggressive hepatectomy.
abstract: Inflammatory pseudotumor (IPT) of the liver is a rare, benign tumor. When the tumor involves the hepatic hilum, however, the clinical course of the patient becomes problematic because of obstructive jaundice and portal hypertension. Complete removal of the tumor sometimes is difficult when the hepatic hilum is extensively involved, and liver transplantation becomes necessary for such an unresectable tumor. This report concerns a 7-year-old boy who presented with obstructive jaundice and portal hypertension owing to an inflammatory pseudotumor of the hepatic hilum and was treated successfully with aggressive hepatectomy, vascular reconstructions of both the portal vein and the hepatic artery, and biliary reconstruction. The patient was discharged after 39 days of hospitalization. Eight months later, portal vein obstruction was detected and treated successfully with percutaneous transhepatic balloon dilatation of the obstructed site. The liver has continued to function well for 11 months after the tumor resection.
authors: Department of Transplantation Immunology, Kyoto University Faculty of Medicine, Kyoto, Japan.
authors: Mikiko
authors: M
authors: Ueda
authors: Yonekawa
authors: Y
authors: Yukihide
authors: Kohei
authors: K
authors: Ogawa
authors: Hirouori
authors: H
authors: Haga
authors: Yasuhiro
authors: Y
authors: Ogura
authors: Takashi
authors: T
authors: Ito
authors: Koichi
authors: K
authors: Tanaka
mesh_terms: D001652:Bile Ducts / Q000601:surgery; D002404:Catheterization; D002648:Child; D003137:Common Bile Duct Diseases / Q000209:etiology / Q000601:surgery; D003251:Constriction, Pathologic / Q000209:etiology / Q000601:surgery; D006104:Granuloma, Plasma Cell / Q000150:complications / Q000601:surgery*; D006498:Hepatectomy; D006499:Hepatic Artery / Q000601:surgery; D006801:Humans; D008107:Liver Diseases / Q000150:complications / Q000601:surgery*; D008297:Male; D011169:Portal Vein / Q000601:surgery; D011183:Postoperative Complications; D015912:Thrombolytic Therapy; D013927:Thrombosis / Q000188:drug therapy; D020246:Venous Thrombosis / Q000209:etiology / Q000628:therapy