Anaesthesia in a child with Sotos syndrome.
Sotos syndrome is a rare condition characterized by typical facies, early accelerated growth, large body size, developmental delay and congenital heart defects. Reports of anaesthetic management of these children are very rare. We report a case of general anaesthesia in a 2(1/2)-year-old boy with this condition, undergoing inguinal hernia repair. The child had a marked developmental delay, hypotonia and mitral regurgitation. The key points in the management of anaesthesia in Sotos syndrome are discussed.
Adhami
Eftim J
EJ
Department of Anesthesiology, University of Florida at Gainesville, Gainesville, FL LeBonheur Children's Medical Center, Memphis, TN, USA.
Cancio-Babu
Consolacion V
CV
D000759:Adjuvants, Anesthesia / Q000627:therapeutic use; D000768:Anesthesia, General; D018685:Anesthetics, Inhalation / Q000627:therapeutic use; D018686:Anesthetics, Intravenous / Q000627:therapeutic use; D001285:Atropine / Q000627:therapeutic use*; D002675:Child, Preschool; D005877:Gigantism / Q000150:complications*; D006330:Heart Defects, Congenital / Q000150:complications*; D006552:Hernia, Inguinal / Q000150:complications / Q000601:surgery; D006801:Humans; D007442:Intubation, Intratracheal; D008297:Male; D008738:Methyl Ethers / Q000627:therapeutic use*; D016343:Monitoring, Intraoperative; D015742:Propofol / Q000627:therapeutic use*; D012008:Recurrence; D012086:Reoperation; D000077149:Sevoflurane; D013577:Syndrome
D000759:Adjuvants, Anesthesia; D018685:Anesthetics, Inhalation; D018686:Anesthetics, Intravenous; D008738:Methyl Ethers; D000077149:Sevoflurane; D001285:Atropine; D015742:Propofol