[Isolated myocardial noncompaction in childhood-case report and review of the literature].
The diagnostic work-up for the first syncopal episode of a 14-year-old female adolescent revealed the morphology of an isolated myocardial non-compaction on echography. Angiography and biopsy of the left ventricle confirmed the diagnosis. Despite a reduced shortening fraction (FS 21%) and frequent premature atrial beats, there were no further cardiac or extracardiac symptoms. After establishment of therapy with beta-blockade, digitalis, angiotensin converting enzyme inhibition and acetylsalic acid, the follow-up over 24 months was good; the implantation of an automatic implantable cardioverter-defibrillator is planned.
Binz
G
G
Olgahospital Akademisches Lehrkrankenhaus der Universität Tübingen, Bismarckstr. 8, 70176 Stuttgart, Germany. G.Binz@Olgahospital.de
Knirsch
W
W
Lewin
M A G
MA
Haas
N A
NA
Koch
W
W
Kandolf
R
R
Uhlemann
F
F
D000293:Adolescent; D000792:Angiography; D018880:Atrial Premature Complexes / Q000151:congenital* / Q000175:diagnosis; D001706:Biopsy; D009202:Cardiomyopathies / Q000175:diagnosis*; D003937:Diagnosis, Differential; D004452:Echocardiography; D018618:Echocardiography, Doppler, Color; D004562:Electrocardiography; D004699:Endocardium / Q000473:pathology; D005260:Female; D006801:Humans; D009200:Myocardial Contraction / Q000502:physiology; D009206:Myocardium / Q000473:pathology*; D013575:Syncope / Q000209:etiology*; D013617:Tachycardia, Supraventricular / Q000151:congenital* / Q000175:diagnosis