Total cavopulmonary connection in a bedridden patient with Sotos syndrome.
Sotos syndrome is an overgrowth disorder of unknown etiology associated with a high incidence of congenital heart defects. Of 60 patients with Sotos syndrome treated in our hospital, 6 had congenital heart defects. We describe a case of successful total cavopulmonary connection at 30 months of age in a patient having pulmonary atresia with intact ventricular septum and a patent ductus arteriosus who had walking disability. The postoperative course was uneventful.
Miyamoto
Takashi
T
Department of Cardiovascular Surgery, Kanagawa Children's Medical Center, Yokohama, Japan. tmiyamamoto-cvs@umin.ac.jp
Kitahori
Kazuo
K
Miyaji
Kagami
K
Nagata
Nobuhiro
N
Yasui
Seiyou
S
D000015:Abnormalities, Multiple / Q000601:surgery*; D002675:Child, Preschool; D004374:Ductus Arteriosus, Patent / Q000150:complications / Q000601:surgery; D005260:Female; D018729:Fontan Procedure / Q000379:methods; D006130:Growth Disorders / Q000150:complications / Q000601:surgery*; D018610:Heart Bypass, Right / Q000379:methods*; D006330:Heart Defects, Congenital / Q000150:complications / Q000601:surgery*; D006801:Humans; D007103:Immobilization; D018633:Pulmonary Atresia / Q000150:complications / Q000601:surgery*; D016896:Treatment Outcome