Undifferentiated embryonal sarcoma in children: beware of the solitary liver cyst.
Undifferentiated embryonal sarcoma (UES) of liver is a rare form of liver tumor in children. It may have an atypical presentation leading to delay in diagnosis. The authors report on 3 consecutive children with this condition, each of them presenting in older children who presented with this condition and an initial diagnostic dilemma. One of them presented initially with a solitary cyst, the second with severe abdominal pain, and the third with intermittent fever. Preoperative chemotherapy was successful in shrinking the tumors in 2 children to allow anatomic liver resection with tumor-free margin. Both remain free of recurrence 2 years after completing treatment.
Chowdhary
S K
SK
Department of Pediatric Surgery, Post Graduate Institute of Medical Education and Research, Chandigarh, India.
Trehan
A
A
Das
A
A
Marwaha
R K
RK
Rao
K L N
KL
D015746:Abdominal Pain / Q000209:etiology; D002648:Child; D002675:Child, Preschool; D003131:Combined Modality Therapy; D003560:Cysts / Q000175:diagnosis*; D003937:Diagnosis, Differential; D005260:Female; D005334:Fever / Q000209:etiology; D006801:Humans; D008107:Liver Diseases / Q000175:diagnosis*; D008113:Liver Neoplasms / Q000175:diagnosis* / Q000628:therapy; D008297:Male; D012509:Sarcoma / Q000175:diagnosis* / Q000628:therapy