title: [Early-onset of primary intestinal lymphangiectasia. A case report and diet treatment].
abstract: Primary intestinal lymphangiectasia is a rare disorder, characterized by hypoproteinemia due to obstruction of the intestinal lymphatic vessels and loss of lymph fluid in the gastrointestinal tract. The case of a 3-month old patient with protein-losing enteropathy due to a primitive intestinal lymphangiectasia diagnosed with duodenal histology is reported. The adapted formula was replaced by a formula enriched with medium-chain triglycerides (MCT) and the patient presented a clinical and biochemical improvement. The importance of an early diagnosis and the efficacy of treatment with MCT is stressed.
authors.affiliation: Dipartimento di Pediatria, Università degli Studi di Catania, Catania, Italy. filippogreco@tiscali.it
authors.forename: F
authors.initials: F
authors.lastname: Greco
authors.forename: G
authors.initials: G
authors.lastname: Piccolo
authors.forename: A
authors.initials: A
authors.lastname: Sorge
authors.forename: P
authors.initials: P
authors.lastname: Pavone
authors.forename: T
authors.initials: T
authors.lastname: Triglia
authors.forename: M
authors.initials: M
authors.lastname: Spina
authors.forename: G
authors.initials: G
authors.lastname: Sorge
mesh_terms: D005260:Female; D006801:Humans; D007223:Infant; D008201:Lymphangiectasis, Intestinal / Q000175:diagnosis / Q000178:diet therapy*