Severe pulmonary hypertension secondary to a parachute-like mitral valve, with the left superior caval vein draining into the coronary sinus, in a girl with Turner's syndrome.
A 17-year-old girl with Turner's syndrome underwent two cardiac operations due to severe mitral stenosis with pulmonary hypertension, caused by a parachute-like mitral valve. The anomaly was associated with persistence of the left superior caval vein, which drained to the coronary sinus, and non-compaction of the left ventricular myocardium. The association of these lesions is rare in patients with Turner's syndrome.
van Heerde
Marc
M
Department of Paediatrics, VU University Medical Center, Amsterdam, The Netherlands.
Hruda
Jaroslav
J
Hazekamp
Mark G
MG
D000293:Adolescent; D003330:Coronary Vessel Anomalies / Q000150:complications*; D005260:Female; D006801:Humans; D006976:Hypertension, Pulmonary / Q000209:etiology*; D008943:Mitral Valve / Q000002:abnormalities*; D014424:Turner Syndrome / Q000150:complications*; D014683:Vena Cava, Superior / Q000002:abnormalities