[Early-onset of primary intestinal lymphangiectasia. A case report and diet treatment].
Primary intestinal lymphangiectasia is a rare disorder, characterized by hypoproteinemia due to obstruction of the intestinal lymphatic vessels and loss of lymph fluid in the gastrointestinal tract. The case of a 3-month old patient with protein-losing enteropathy due to a primitive intestinal lymphangiectasia diagnosed with duodenal histology is reported. The adapted formula was replaced by a formula enriched with medium-chain triglycerides (MCT) and the patient presented a clinical and biochemical improvement. The importance of an early diagnosis and the efficacy of treatment with MCT is stressed.
Greco
F
F
Dipartimento di Pediatria, Università degli Studi di Catania, Catania, Italy. filippogreco@tiscali.it
Piccolo
G
G
Sorge
A
A
Pavone
P
P
Triglia
T
T
Spina
M
M
Sorge
G
G
D005260:Female; D006801:Humans; D007223:Infant; D008201:Lymphangiectasis, Intestinal / Q000175:diagnosis / Q000178:diet therapy*