Keratoconus associated with hyperimmunoglobulin E syndrome.
OBJECTIVE
To report a case of keratoconus in a patient with hyper-IgE syndrome.


METHODS
A case report of a 28-year-old man with hyperimmunoglobulin E syndrome (HIES) who presented with chronic eczematous dermatitis of the eyelids and severe eye itching.


RESULTS
Best corrected visual acuity was 20/25 in the right eye and 20/30 in the left eye. There was a scissoring reflex in both eyes with retinoscopy. Biomicroscopy of the cornea was normal, but corneal topography showed bilateral keratoconus.


CONCLUSIONS
It is difficult to establish a direct correlation between keratoconus and HIES due to the rarity of the latter disorder. It is, however, important to consider this association and obtain a corneal topography to rule out corneal ectasia in patients with HIES.
Kim
Jeehee
J
Department of Ophthalmology, University of Washington, Box 356485, Seattle, WA 98195-6485, USA. devgroves@excite.com
Netto
Marcelo V
MV
D000328:Adult; D019781:Corneal Topography; D003937:Diagnosis, Differential; D006801:Humans; D007589:Job Syndrome / Q000150:complications*; D007640:Keratoconus / Q000150:complications* / Q000175:diagnosis / Q000503:physiopathology; D008297:Male; D014792:Visual Acuity