title: Composite aortoplasty for recurrent coarctation after neonatal repair in Williams syndrome.
abstract: Supravalvar aortic stenosis is the most frequent operation required for Williams syndrome; however, coarctation repair is more common in patients requiring surgery in the first few months of life. We report on a child with Williams syndrome in whom extensive reoperation was required 5 months after neonatal aortic coarctation repair. A composite left subclavian artery flap and allograft patch aortoplasty of the aortic arch and descending aorta was performed through a left thoracotomy using cardiopulmonary bypass and circulatory arrest. Detailed anatomic evaluation of the aortic arch and descending aorta is recommended before initial coarctation repair in neonates with Williams syndrome.
authors.affiliation: Department of Surgery, University of Colorado Health Sciences Center, Denver, Colorado, USA.
authors.forename: Jeni L
authors.initials: JL
authors.lastname: Marks
authors.forename: Max B
authors.initials: MB
authors.lastname: Mitchell
authors.forename: David N
authors.initials: DN
authors.lastname: Campbell
authors.forename: Warren H
authors.initials: WH
authors.lastname: Toews
mesh_terms: D001017:Aortic Coarctation / Q000601:surgery*; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D011183:Postoperative Complications / Q000601:surgery*; D012008:Recurrence; D012086:Reoperation; D014656:Vascular Surgical Procedures / Q000379:methods; D018980:Williams Syndrome / Q000601:surgery*