[KID syndrome: a cause of pachydermatoglyphia].
BACKGROUND
The KID syndrome is a rare ectodermal dysplasia associating erythrokeratodermia, deafness and keratitis. Other disorders such as sensitivity to infections or hypohidrosis may be associated. Pachydermatoglyphia is characterized by diffuse hyperkeratosis in which the dermatoglyphe crests are accentuated in thickness and height.


METHODS
We report the case of a KID syndrome in a young girl, born of non-consanguine parents and without any familial context. The classical elements of this dysplasia were present: erythrokeratoderma with dryness and roughness of the whole tegument, plicatured pachydermia of the knees, facial erythema, grooves around the mouth, hypotrichosis of the lashes and eyebrows, deafness, and ophthalmologic involvement. Involvement of the palms was characterized by the pachydermatoglyphic aspect.


CONCLUSIONS
In this case report, the palmar keratoderma corresponded to the original description of pachydermatoglyphia and we consider that the KID syndrome should be integrated as a possible etiology of pachydermatoglyphia.
Stambouli
O Boudghene
OB
Service de Dermato-Vénéréologie, Centre Hospitalo Universitaire Dr T. Damerdji, Tlemcen, Algérie. omar_stambouli@hotmail.com
Belbachir
A
A
D002648:Child; D003638:Deafness / Q000150:complications*; D005260:Female; D006801:Humans; D007057:Ichthyosis / Q000150:complications*; D007634:Keratitis / Q000150:complications*; D018318:Neurofibroma, Plexiform / Q000209:etiology*; D012878:Skin Neoplasms / Q000209:etiology*; D013577:Syndrome