Composite aortoplasty for recurrent coarctation after neonatal repair in Williams syndrome.
Supravalvar aortic stenosis is the most frequent operation required for Williams syndrome; however, coarctation repair is more common in patients requiring surgery in the first few months of life. We report on a child with Williams syndrome in whom extensive reoperation was required 5 months after neonatal aortic coarctation repair. A composite left subclavian artery flap and allograft patch aortoplasty of the aortic arch and descending aorta was performed through a left thoracotomy using cardiopulmonary bypass and circulatory arrest. Detailed anatomic evaluation of the aortic arch and descending aorta is recommended before initial coarctation repair in neonates with Williams syndrome.
Marks
Jeni L
JL
Department of Surgery, University of Colorado Health Sciences Center, Denver, Colorado, USA.
Mitchell
Max B
MB
Campbell
David N
DN
Toews
Warren H
WH
D001017:Aortic Coarctation / Q000601:surgery*; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D011183:Postoperative Complications / Q000601:surgery*; D012008:Recurrence; D012086:Reoperation; D014656:Vascular Surgical Procedures / Q000379:methods; D018980:Williams Syndrome / Q000601:surgery*