[A case of malignant peripheral nerve sheath tumor requiring thoracotomy].
A 32-year-old woman with Von Recklinghausen's disease had a malignant peripheral nerve sheath tumor that had progressed to malignancy from a neurofibroma arising in the left phrenic nerve. The tumor was removed combining a neck incision and thoracotomy. It should be more widely recognized that neurofibroma associated with Von Recklinghausen's disease may progress to malignancy. Primary treatment requires a broad surgical excision to obtain an adequate margin.
Shinozaki
Takeshi
T
Department of Otolaryngology, Head and Neck Surgery, Omiya Medical Center, Jichi Medical School, Saitama.
Ishii
Kousuke
K
Tsubaki
Keiju
K
Ota
Yasushi
Y
Adachi
Hideo
H
D000328:Adult; D005260:Female; D006801:Humans; D018317:Nerve Sheath Neoplasms / Q000601:surgery*; D009456:Neurofibromatosis 1 / Q000150:complications; D010791:Phrenic Nerve; D013908:Thoracotomy