title: One and a half ventricle repair for Ebstein's anomaly.
abstract: The surgical strategy for patients having Ebstein's anomaly and hypoplastic right ventricle is controversial. An 11-year-old boy patient having such condition, with estimated end-diastolic volume index of the atrialized and functional right ventricle being 70% of normally expected values, underwent biventricular repair. Immediately after the surgery, however, he developed right heart failure with the central venous pressure of 11 mmHg. He consequently underwent additional bidirectional cavopulmonary anastomosis, thereby converting the biventricular repair into one and a half ventricle repair. He recovered uneventfully and is doing well 2 years after the surgery.
authors.affiliation: Department of Surgery II, Nippon Medical School, Tokyo, Japan.
authors.forename: Junko
authors.initials: J
authors.lastname: Akaishi
authors.forename: Hitoshi
authors.initials: H
authors.lastname: Yamauchi
authors.forename: Masami
authors.initials: M
authors.lastname: Ochi
authors.forename: Shunichi
authors.initials: S
authors.lastname: Ogawa
authors.forename: Toshihide
authors.initials: T
authors.lastname: Asou
authors.forename: Shigeo
authors.initials: S
authors.lastname: Tanaka
mesh_terms: D002496:Central Venous Pressure / Q000502:physiology; D002648:Child; D004437:Ebstein Anomaly / Q000503:physiopathology / Q000601:surgery*; D015150:Echocardiography, Doppler; D018610:Heart Bypass, Right; D006333:Heart Failure / Q000209:etiology / Q000503:physiopathology; D006344:Heart Septal Defects, Atrial / Q000503:physiopathology / Q000601:surgery; D006352:Heart Ventricles / Q000000981:diagnostic imaging / Q000473:pathology / Q000601:surgery; D006801:Humans; D007036:Hypothermia, Induced; D008297:Male; D012086:Reoperation; D013318:Stroke Volume / Q000502:physiology; D014262:Tricuspid Valve Insufficiency / Q000503:physiopathology / Q000601:surgery