title: [A case of malignant peripheral nerve sheath tumor requiring thoracotomy].
abstract: A 32-year-old woman with Von Recklinghausen's disease had a malignant peripheral nerve sheath tumor that had progressed to malignancy from a neurofibroma arising in the left phrenic nerve. The tumor was removed combining a neck incision and thoracotomy. It should be more widely recognized that neurofibroma associated with Von Recklinghausen's disease may progress to malignancy. Primary treatment requires a broad surgical excision to obtain an adequate margin.
authors.affiliation: Department of Otolaryngology, Head and Neck Surgery, Omiya Medical Center, Jichi Medical School, Saitama.
authors.forename: Takeshi
authors.initials: T
authors.lastname: Shinozaki
authors.forename: Kousuke
authors.initials: K
authors.lastname: Ishii
authors.forename: Keiju
authors.initials: K
authors.lastname: Tsubaki
authors.forename: Yasushi
authors.initials: Y
authors.lastname: Ota
authors.forename: Hideo
authors.initials: H
authors.lastname: Adachi
mesh_terms: D000328:Adult; D005260:Female; D006801:Humans; D018317:Nerve Sheath Neoplasms / Q000601:surgery*; D009456:Neurofibromatosis 1 / Q000150:complications; D010791:Phrenic Nerve; D013908:Thoracotomy