Primary Intestinal Lymphangiectasia.
A high-protein, low-fat diet supplemented with medium chain triglycerides (MCT) is the simplest, most effective, and most widely prescribed treatment with the fewest side effects. Octreotide has been helpful in cases in which treatment with MCT has failed, but it is costly and requires parenteral administration. Antiplasmin therapy may have some role when evidence of increased fibrinolysis is present. Surgery is reserved for palliation of large ascites or resection of isolated lesions.
Bliss
Charles M.
CM
Section of Gastroenterology, Department of Medicine, Boston Medical Center, D408, 88 East Newton Street, Boston, MA 02118, USA. paul.schroy@bmc.org
Schroy III
Paul C.
PC