Intraosseous malignant peripheral nerve sheath tumor with local recurrence, lung metastases and death.
Malignant peripheral nerve sheath tumor (MPNST) is almost always seen in soft tissue. Skeletal involvement by MPNST is uncommon and usually results from secondary invasion. Primary MPNSTs are exceptionally rare. We report a surgically proven case of intraosseous MPNST, with local recurrence and lung metastasis during follow-up. The imaging and histological features of the case are described and the literature on the subject briefly reviewed.
Kendi
Tuba Karagülle
TK
Integra MR Imaging Center, Tahran Cad., No. 38, Kavaklidere, Ankara, Turkey. drtubakendi@yahoo.com
Erakar
Aziz
A
Yildiz
H Yusuf
HY
Saglik
Yener
Y
Erekul
Selim
S
D000328:Adult; D001859:Bone Neoplasms / Q000175:diagnosis / Q000473:pathology*; D006801:Humans; D008175:Lung Neoplasms / Q000556:secondary*; D008279:Magnetic Resonance Imaging; D008297:Male; D009364:Neoplasm Recurrence, Local; D018317:Nerve Sheath Neoplasms / Q000175:diagnosis / Q000473:pathology*; D014457:Ulna / Q000473:pathology*