Keloidal scleroderma.
Progressive systemic sclerosis (PSS) can involve the skin diffusely or in a limited way. Rarely cutaneous involvement can assume a hypertrophic form, described in the literature as keloidal scleroderma. The authors describe a PSS patient who presented cutaneous manifestations compatible with the diagnosis of this clinical situation. The clinical features, pathogenic mechanism and therapeutic approach are discussed and a broad review of the literature is given.
Santiago
Mittermayer
M
Escola Bahiana de Medicina e Saúde Pública, Bahia, Brazil. mitter@svn.com.br
de Castro
Dálvaro Oliveira
DO
Costa
Cíntia Andrade
CA
Passos
Edgard Souza
ES
Paixão
Ariene
A
D000328:Adult; D018501:Antirheumatic Agents / Q000627:therapeutic use; D001379:Azathioprine / Q000627:therapeutic use; D005260:Female; D006801:Humans; D007627:Keloid / Q000188:drug therapy / Q000209:etiology* / Q000473:pathology; D010396:Penicillamine / Q000627:therapeutic use; D045743:Scleroderma, Diffuse / Q000150:complications* / Q000188:drug therapy / Q000473:pathology; D016896:Treatment Outcome
D018501:Antirheumatic Agents; D010396:Penicillamine; D001379:Azathioprine