[Tetralogy of Fallot with absent pulmonary valve in a newborn and infant. Complete surgical correction].
We report two patients, a newborn and a 7-month old infant, with tetralogy of Fallot and absent pulmonary valve syndrome. Both had severe obstruction at the level of the ring with aneurysmal pulmonary artery branches, which compressed and displaced the trachea and main bronchial tubes. The neonate required mechanical ventilation from birth. Treatment was aggressive in both patients with interventricular septum defect closure, arterioplasty of the branches and homograft in the infant, and resection of the truncus and pulmonary branches with posterior face suture of both branches associated with a valved conduit in orthotopic position in the neonate. We believe that early treatment avoids airway degeneration and right ventricle volume overload.
Cabrera Duro
A
A
Servicio de Cardiología Pediátrica, Hospital de Cruces, Vizcaya, Spain.
Rodrigo Carbonero
D
D
Martínez Corrales
P
P
Aramendi Gallardo
J
J
Alcíbar Villa
J
J
López de Heredia Goya
J
J
Romero Ibarra
C
C
D000015:Abnormalities, Multiple / Q000601:surgery*; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D011664:Pulmonary Valve / Q000002:abnormalities* / Q000601:surgery*; D013771:Tetralogy of Fallot / Q000150:complications* / Q000601:surgery*