title: [Multiple congenital stenoses of the segmental pulmonary arteries in an elderly patient].
abstract: Congenital stenoses of the pulmonary artery are a rare cause of pulmonary arterial hypertension, usually diagnosed in childhood. We report the first description of multiple arterial pulmonary malformations in an elderly patient, revealed by an acute severe pulmonary embolism. Despite an immediate excellent response to fibrinolysis, persistent and elevated arterial pulmonary pressures were consistent with the presence of an underlying arterial pulmonary disease. Pulmonary angiography led to the diagnosis of type III multiple segmental arterial pulmonary stenoses. Eight years later, the patient remained well. This original report underlines the potential good outcome of pulmonary artery stenoses, and suggests the presence of such silent or misdiagnosed lesions in adulthood.
authors.affiliation: Unité de Pneumologie, DMAS, Hôpital A.-Michallon, CHU-Université J.-Fourier, BP 217, 38043 Grenoble 09.
authors.forename: L
authors.initials: L
authors.lastname: Masmoudi
authors.forename: F
authors.initials: F
authors.lastname: Arbib
authors.forename: G
authors.initials: G
authors.lastname: Ferretti
authors.forename: C
authors.initials: C
authors.lastname: Brambilla
authors.forename: G
authors.initials: G
authors.lastname: Devouassoux
mesh_terms: D000792:Angiography; D005260:Female; D006801:Humans; D006976:Hypertension, Pulmonary / Q000209:etiology / Q000473:pathology; D008875:Middle Aged; D011379:Prognosis; D011651:Pulmonary Artery / Q000473:pathology*; D011655:Pulmonary Embolism / Q000209:etiology*; D014652:Vascular Diseases / Q000150:complications / Q000151:congenital* / Q000175:diagnosis