[Alagille syndrome and chronic renal failure].
Alagille syndrome is characterized by paucity of bile ducts leading to cholestasis and may be accompanied by renal and cardiovascular abnormalities. We report 42-years old patient with hypertension, chronic renal failure and Alagille syndrome. Ischemic nephropathy was suspected, which was not confirmed on angio-CT. It seems, that chronic renal failure in the patient was due to primary parenchymal pathology.
Kaczyńska
Anna
A
Katedra i Klinika Chorób Wewnetrznych i Nadciśnienia Tetniczego AM w Warszawie.
Lewandowski
Jacek
J
Pruszczyk
Piotr
P
Gaciong
Zbigniew
Z
D000328:Adult; D016738:Alagille Syndrome / Q000150:complications* / Q000175:diagnosis; D006801:Humans; D006973:Hypertension / Q000150:complications; D007511:Ischemia / Q000150:complications* / Q000175:diagnosis; D007668:Kidney / Q000098:blood supply* / Q000000981:diagnostic imaging; D007676:Kidney Failure, Chronic / Q000150:complications / Q000175:diagnosis; D008297:Male; D014057:Tomography, X-Ray Computed