title: Congenital infantile hepatic hemangioendothelioma type II treated with orthotopic liver transplantation.
abstract: The authors describe a 10-week-old girl with infantile hepatic hemangioendothelioma who initially presented with difficulty feeding, hepatomegaly, and multiple hemangiomas of the skin. Six weeks of steroid therapy and 2 weeks of chemotherapy failed to produce clinical improvement. The patient underwent split liver transplantation. A definitive diagnosis of hemangioendothelioma type II was made. Imaging studies cannot differentiate between hemangioendothelioma and angiosarcoma. Treatment modalities for this condition remain unclear. The patient continues to do well.
authors.affiliation: Department of Pediatrics, Children's Hospital at Westchester Medical Center, New York Medical College, Valhalla, New York, USA.
authors.forename: Rowan
authors.initials: R
authors.lastname: Walsh
authors.forename: John
authors.initials: J
authors.lastname: Harrington
authors.forename: Debra
authors.initials: D
authors.lastname: Beneck
authors.forename: M Fevzi
authors.initials: MF
authors.lastname: Ozkaynak
mesh_terms: D005260:Female; D006390:Hemangioendothelioma / Q000151:congenital* / Q000473:pathology / Q000601:surgery*; D006801:Humans; D007223:Infant; D008113:Liver Neoplasms / Q000151:congenital* / Q000473:pathology / Q000601:surgery*; D016031:Liver Transplantation; D014057:Tomography, X-Ray Computed; D016896:Treatment Outcome