Mobilization of adenine nucleotide translocators as molecular bases of the biochemical threshold effect observed in mitochondrial diseases.
D033741:Adenine Nucleotide Translocator 1 / Q000737:chemistry; D000227:Adenine Nucleotides / Q000737:chemistry*; D000818:Animals; D001278:Atractyloside / Q000031:analogs & derivatives* / Q000494:pharmacology; D001706:Biopsy; D015153:Blotting, Western; D004579:Electron Transport; D004591:Electrophoresis, Polyacrylamide Gel; D006801:Humans; D007700:Kinetics; D008297:Male; D008928:Mitochondria / Q000378:metabolism; D000226:Mitochondrial ADP, ATP Translocases / Q000378:metabolism; D028361:Mitochondrial Diseases / Q000378:metabolism*; D008954:Models, Biological; D009132:Muscles / Q000378:metabolism; D009154:Mutation; D010085:Oxidative Phosphorylation; D010100:Oxygen / Q000378:metabolism; D010101:Oxygen Consumption; D010766:Phosphorylation; D011487:Protein Conformation; D020033:Protein Isoforms; D051381:Rats; D017208:Rats, Wistar; D014018:Tissue Distribution
D033741:Adenine Nucleotide Translocator 1; D000227:Adenine Nucleotides; D020033:Protein Isoforms; D001278:Atractyloside; D000226:Mitochondrial ADP, ATP Translocases; D010100:Oxygen; C003853:carboxyatractyloside