Severe deficiency of VWF-cleaving protease (ADAMTS13) activity defines a distinct population of thrombotic microangiopathy patients.
D051722:ADAM Proteins; D000071120:ADAMTS13 Protein; D003404:Creatinine / Q000097:blood; D006801:Humans; D008666:Metalloendopeptidases / Q000097:blood / Q000172:deficiency*; D010951:Plasma Exchange; D012074:Remission Induction; D012189:Retrospective Studies; D013927:Thrombosis / Q000097:blood* / Q000209:etiology* / Q000628:therapy
D003404:Creatinine; D051722:ADAM Proteins; D008666:Metalloendopeptidases; D000071120:ADAMTS13 Protein; C099604:ADAMTS13 protein, human