Common variable immunodeficiency syndrome with right aortic arch: a case report.
BACKGROUND
Common variable immunodeficiency syndrome predominantly affects adults. It is characterized by low production of all the major classes of immunoglobulins. We report a case of common variable immunodeficiency syndrome with right aortic arch. An association of right-sided arch and common variable immunodeficiency syndrome has not been previously reported.


METHODS
A 41-year-old female patient presented with a history of recurrent pneumonia, sinusitis, otitis media, diarrhoea, cystitis since childhood. Biochemical and immunocytochemical analysis revealed common variable immunodeficiency syndrome and radiological evaluation confirmed right aortic arch and aberrant left subclavian artery.


CONCLUSIONS
Common variable immunodeficiency syndrome syndrome is a clinical entity that should be kept in mind in patients with recurrent infections of different sites.
Department of Internal Medicine, Pamukkale University, Medicine Faculty, Denizli, Turkey. adidyal@yahoo.com
Arzu Didem
AD
Yalcin
Nese
N
Aydemir
Huseyin
H
Turgut
Riza Hakan
RH
Erbay
Ata Nevzat
AN
Yalcin
D000328:Adult; D001015:Aortic Arch Syndromes / Q000150:complications*; D018376:Cardiovascular Abnormalities / Q000150:complications*; D017074:Common Variable Immunodeficiency / Q000150:complications*; D005260:Female; D006801:Humans; D007239:Infections / Q000150:complications / Q000473:pathology; D012008:Recurrence; D013348:Subclavian Artery / Q000002:abnormalities*