Common variable immunodeficiency syndrome with right aortic arch: a case report.
BACKGROUND
Common variable immunodeficiency syndrome predominantly affects adults. It is characterized by low production of all the major classes of immunoglobulins. We report a case of common variable immunodeficiency syndrome with right aortic arch. An association of right-sided arch and common variable immunodeficiency syndrome has not been previously reported.


METHODS
A 41-year-old female patient presented with a history of recurrent pneumonia, sinusitis, otitis media, diarrhoea, cystitis since childhood. Biochemical and immunocytochemical analysis revealed common variable immunodeficiency syndrome and radiological evaluation confirmed right aortic arch and aberrant left subclavian artery.


CONCLUSIONS
Common variable immunodeficiency syndrome syndrome is a clinical entity that should be kept in mind in patients with recurrent infections of different sites.
Yalcin
Arzu Didem
AD
Department of Internal Medicine, Pamukkale University, Medicine Faculty, Denizli, Turkey. adidyal@yahoo.com
Aydemir
Nese
N
Turgut
Huseyin
H
Erbay
Riza Hakan
RH
Yalcin
Ata Nevzat
AN
D000328:Adult; D001015:Aortic Arch Syndromes / Q000150:complications*; D018376:Cardiovascular Abnormalities / Q000150:complications*; D017074:Common Variable Immunodeficiency / Q000150:complications*; D005260:Female; D006801:Humans; D007239:Infections / Q000150:complications / Q000473:pathology; D012008:Recurrence; D013348:Subclavian Artery / Q000002:abnormalities*