title: Scimitar syndrome: morphological diagnosis and assessment of hemodynamic significance by magnetic resonance imaging.
abstract: Scimitar syndrome has a variable presentation depending on the age at which the diagnosis is made. We report a case of a young woman (age 18 years) with suspected right pulmonary hypoplasia in whom a scimitar syndrome was diagnosed. Using MRI morphological findings and hemodynamic significance of the syndrome were assessed. Left-to-right shunt was calculated from blood flow measurements performed in the ascending aorta, the main pulmonary artery, and the aberrant scimitar vein.
authors.affiliation: Department of Diagnostic Radiology, University of Tuebingen, Hoppe-Seyler-Strasse 3, 72076 Tuebingen, Germany. ulrich.kramer@med.uni-tuebingen.de
authors.forename: Ulrich
authors.initials: U
authors.lastname: Kramer
authors.forename: Volker
authors.initials: V
authors.lastname: Dörnberger
authors.forename: Michael
authors.initials: M
authors.lastname: Fenchel
authors.forename: Norbert
authors.initials: N
authors.lastname: Stauder
authors.forename: Claus D
authors.initials: CD
authors.lastname: Claussen
authors.forename: Stephan
authors.initials: S
authors.lastname: Miller
mesh_terms: D000293:Adolescent; D005260:Female; D005500:Follow-Up Studies; D006439:Hemodynamics / Q000502:physiology*; D006801:Humans; D007091:Image Processing, Computer-Assisted; D018810:Magnetic Resonance Angiography / Q000379:methods*; D011859:Radiography; D012587:Scimitar Syndrome / Q000000981:diagnostic imaging* / Q000503:physiopathology; D012680:Sensitivity and Specificity; D012720:Severity of Illness Index