Susac syndrome: report of four cases and review of the literature.
Susac syndrome is a rare disease of unknown pathogenesis. It is caused by a microangiopathy affecting the arterioles of the brain, retina, and cochlea, giving the classic clinical triad of subacute encephalopathy, visual loss secondary to retinal branch occlusions, and sensorineural hearing loss. The features of four cases of this syndrome are presented. MR imaging, retinal fluorescein angiography, and audiography findings enable diagnosis. Early therapy may reduce sequelae and improve recovery.
Do
Tai Hung
TH
Department of Radiology, CHUS-Hôpital Fleurimont, Sherbrooke, Quebec, Canada.
Fisch
Christiane
C
Evoy
François
F
D000328:Adult; D001921:Brain / Q000473:pathology; D001925:Brain Damage, Chronic / Q000175:diagnosis*; D003937:Diagnosis, Differential; D005260:Female; D006319:Hearing Loss, Sensorineural / Q000175:diagnosis*; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D009460:Neurologic Examination; D015356:Retinal Artery Occlusion / Q000175:diagnosis*; D031300:Retinal Vasculitis / Q000175:diagnosis*; D013577:Syndrome; D020293:Vasculitis, Central Nervous System / Q000175:diagnosis*