title: Left ventricular outflow obstruction after Fontan procedure involving a patient with complete atrioventricular septal defects complicated by a small left ventricle.
abstract: We report a 1-year-old girl who developed ventricular outflow tract obstruction early after a Fontan operation, necessitating surgical relief using the Damus-Kaye-Stansel procedure. The patient had a complete atrioventricular septal defect complicated by a muscular ventricular septal defect (VSD) and a small left ventricle, a morphology that has not previously been reported in cases of systemic outflow tract obstruction after the Fontan procedure. Postoperative systemic outflow obstruction must be considered as a possible sequela following Fontan surgery in patients with an atrioventricular septal defect and a small left ventricle.
authors.affiliation: Department of Pediatric Cardiology, Saitama Heart Institute, Saitama Medical School Hospital, Moroyama, Japan. hsenzaki@saitama-med.ac.jp
authors.forename: H
authors.initials: H
authors.lastname: Senzaki
authors.forename: T
authors.initials: T
authors.lastname: Kobayashi
authors.forename: M
authors.initials: M
authors.lastname: Morsy
authors.forename: H
authors.initials: H
authors.lastname: Asano
authors.forename: S
authors.initials: S
authors.lastname: Kyo
authors.forename: Y
authors.initials: Y
authors.lastname: Yokote
mesh_terms: D000359:Aftercare / Q000379:methods; D006328:Cardiac Catheterization; D017548:Echocardiography, Transesophageal; D004630:Emergencies; D017809:Fatal Outcome; D005260:Female; D018729:Fontan Procedure / Q000009:adverse effects* / Q000379:methods; D006344:Heart Septal Defects, Atrial / Q000150:complications / Q000175:diagnosis / Q000601:surgery*; D006345:Heart Septal Defects, Ventricular / Q000150:complications / Q000175:diagnosis / Q000601:surgery*; D006352:Heart Ventricles / Q000002:abnormalities*; D006801:Humans; D007223:Infant; D008480:Mediastinitis / Q000209:etiology; D019990:Perioperative Care / Q000379:methods; D011669:Pulmonary Wedge Pressure; D015635:Radionuclide Ventriculography; D012307:Risk Factors; D012772:Shock, Septic / Q000209:etiology; D013318:Stroke Volume; D014694:Ventricular Outflow Obstruction / Q000175:diagnosis / Q000209:etiology* / Q000601:surgery