Scimitar syndrome: morphological diagnosis and assessment of hemodynamic significance by magnetic resonance imaging.
Scimitar syndrome has a variable presentation depending on the age at which the diagnosis is made. We report a case of a young woman (age 18 years) with suspected right pulmonary hypoplasia in whom a scimitar syndrome was diagnosed. Using MRI morphological findings and hemodynamic significance of the syndrome were assessed. Left-to-right shunt was calculated from blood flow measurements performed in the ascending aorta, the main pulmonary artery, and the aberrant scimitar vein.
Kramer
Ulrich
U
Department of Diagnostic Radiology, University of Tuebingen, Hoppe-Seyler-Strasse 3, 72076 Tuebingen, Germany. ulrich.kramer@med.uni-tuebingen.de
Dörnberger
Volker
V
Fenchel
Michael
M
Stauder
Norbert
N
Claussen
Claus D
CD
Miller
Stephan
S
D000293:Adolescent; D005260:Female; D005500:Follow-Up Studies; D006439:Hemodynamics / Q000502:physiology*; D006801:Humans; D007091:Image Processing, Computer-Assisted; D018810:Magnetic Resonance Angiography / Q000379:methods*; D011859:Radiography; D012587:Scimitar Syndrome / Q000000981:diagnostic imaging* / Q000503:physiopathology; D012680:Sensitivity and Specificity; D012720:Severity of Illness Index