Ectomesenchymoma: case report and review of the literature.
Ectomesenchymoma (EMCH) is a rare tumor that may arise in the brain or soft tissue. This tumor type is defined as a form including ectodermal components represented by neuroblasts or ganglion cells and differentiated mesenchymal structures of various types. The mesenchymal component is most often a rhabdomyosarcoma, but liposarcoma, malignant fibrous histiocytoma, leiomyosarcoma, chondrosarcoma, malignant schwannoma, and osseous elements have also been recorded. We report a case of an abdominal malignant ectomesenchymoma, containing three components, schwannoma, embryonal rhabdomyosarcoma, and ganglion cells, in a four-month-old infant. We also review 43 previously reported cases.
Kösem
Mustafa
M
Department of Pathology, Yüzuuncü Yil University Faculty of Medicine, Van, Turkey.
Ibiloğlu
Ibrahim
I
Bakan
Vedat
V
Köseoğlu
Burhan
B
D000008:Abdominal Neoplasms / Q000000981:diagnostic imaging / Q000473:pathology* / Q000628:therapy; D006801:Humans; D007223:Infant; D008297:Male; D018193:Neoplasms, Complex and Mixed / Q000000981:diagnostic imaging / Q000473:pathology* / Q000628:therapy; D011859:Radiography