title: Outcome of aortic valve repair in children with congenital aortic valve insufficiency.
abstract: OBJECTIVE
  Surgical aortic valvotomy has a long history of providing excellent palliation for aortic stenosis in infancy and childhood. The fate of aortic valve repairs for dominant aortic regurgitation in this same age group is considerably less clear.
  
  
  METHODS
  From 1990 to 2000, a total of 21 patients underwent aortic valve repair for aortic regurgitation at our institution. Seventeen patients were younger than 17 years at the time of repair (3-17 years, mean 8.1 +/- 3.7 years). Of these 17 children, 6 (35%) had bicuspid valves and 11 (65%) had tricuspid valves. Type of repair varied with valve type, but repair generally consisted of commissure resuspension, partial commissure closure, triangular resection of redundant leaflets, or some combination.
  
  
  RESULTS
  There were no deaths. Follow-up ranged from 1 to 11 years (mean 5.3 +/- 2.4 years). At present 3 of 17 (17.6%) have mild aortic regurgitation according to echocardiography and 6 (35.2%) have moderate aortic regurgitation. In 8 of 17 cases (47.1%) the repair clearly failed, requiring reoperation from 0.5 to 73 months after the original operation (mean 18.9 months). Reoperation consisted of 6 Ross procedures and 2 mechanical aortic valve replacements. There were no deaths at the secondary operation.
  
  
  CONCLUSIONS
  Aortic valve repair in children with a dominant feature of aortic insufficiency tended to fail progressively and at a high rate. Leaflet thickening was associated with higher risk of repair failure in this series. The threshold for aortic valve replacement should remain low.
authors.affiliation: Division of Cardiothoracic Surgery, Loma Linda University Medical Center, CA 92354, USA. nahidh@pol.net
authors.forename: Nahidh
authors.initials: N
authors.lastname: Hasaniya
authors.forename: Steven R
authors.initials: SR
authors.lastname: Gundry
authors.forename: Anees J
authors.initials: AJ
authors.lastname: Razzouk
authors.forename: Neda
authors.initials: N
authors.lastname: Mulla
authors.forename: Leonard L
authors.initials: LL
authors.lastname: Bailey
mesh_terms: D000293:Adolescent; D001021:Aortic Valve / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000601:surgery*; D001022:Aortic Valve Insufficiency / Q000151:congenital* / Q000000981:diagnostic imaging / Q000601:surgery*; D002140:California; D002648:Child; D002669:Child Welfare; D002675:Child, Preschool; D015150:Echocardiography, Doppler; D017548:Echocardiography, Transesophageal; D005260:Female; D005500:Follow-Up Studies; D019918:Heart Valve Prosthesis Implantation; D006352:Heart Ventricles / Q000002:abnormalities / Q000000981:diagnostic imaging / Q000601:surgery; D006801:Humans; D008297:Male; D011183:Postoperative Complications / Q000000981:diagnostic imaging / Q000209:etiology; D012086:Reoperation; D012720:Severity of Illness Index; D016896:Treatment Outcome