title: Energy expenditure in patients with propionic and methylmalonic acidaemias.
abstract: Resting energy expenditure (REE) was investigated in 8 children with propionic and methylmalonic acidaemias because a lowered REE has been reported in the literature. We observed a marginally elevated REE and think that adequate caloric intake and the use of a synthetic amino acid mixture are responsible for this.
authors.affiliation: Department of Metabolic Diseases, University Medical Centre Utrecht, The Netherlands.
authors.forename: C C
authors.initials: CC
authors.lastname: van Hagen
authors.forename: E
authors.initials: E
authors.lastname: Carbasius Weber
authors.forename: Th A M
authors.initials: TA
authors.lastname: van den Hurk
authors.forename: J H
authors.initials: JH
authors.lastname: Oudshoorn
authors.forename: L
authors.initials: L
authors.lastname: Dorland
authors.forename: R
authors.initials: R
authors.lastname: Berger
authors.forename: T
authors.initials: T
authors.lastname: de Koning
mesh_terms: D000592:Amino Acid Metabolism, Inborn Errors / Q000188:drug therapy / Q000378:metabolism*; D000596:Amino Acids / Q000627:therapeutic use; D002648:Child; D002675:Child, Preschool; D004338:Drug Combinations; D002149:Energy Intake; D004734:Energy Metabolism; D005260:Female; D006801:Humans; D007223:Infant; D008297:Male; D008764:Methylmalonic Acid / Q000378:metabolism*; D011422:Propionates / Q000378:metabolism*
chemical_list: D000596:Amino Acids; D004338:Drug Combinations; D011422:Propionates; D008764:Methylmalonic Acid