Nevoid basal cell carcinoma syndrome: a review of the literature.
The nevoid basal cell carcinoma syndrome (NBCCS) or Gorlin-Goltz Syndrome is an autosomal dominant disorder principally characterized by cutaneous basal cell carcinomas, multiple keratocysts, and skeletal anomalies. The present report reviews current knowledge of this disorder that has profound relevance to specialists in Oral and Maxillo-Facial Surgery, Oral Medicine and Radiology.
Manfredi
M
M
Sezione di Odontostomatologia--Dipartimento Scienze Otorino-Odonto Oftalmologiche e Cervico-Facciali, Università degli Studi di Parma, Italy. maddalenamanfredi@hotmail.com
Vescovi
P
P
Bonanini
M
M
Porter
S
S
D001478:Basal Cell Nevus Syndrome / Q000235:genetics / Q000473:pathology / Q000601:surgery; D002899:Chromosomes, Human, Pair 9; D019465:Craniofacial Abnormalities / Q000235:genetics / Q000473:pathology; D005799:Genes, Dominant; D005817:Genetic Counseling; D006801:Humans; D012878:Skin Neoplasms / Q000235:genetics / Q000473:pathology / Q000601:surgery