Reversal of protein-losing enteropathy with calcium replacement in a patient after Fontan operation.
Protein-losing enteropathy occurs in patients following the modified Fontan procedure. Treatment is still controversial. We describe a boy who developed protein-losing enteropathy 18-months after an extracardiac Fontan procedure. Treatment with calcium for hypocalcemia attenuated the protein loss with subsequent normalization of serum total protein and albumin levels. Decrease of oral calcium and subsequent decrease of serum ionized calcium level were associated with relapse of hypoalbuminemia. This was again treated successfully with calcium and vitamin D replacement.
Kim
Soo-Jin
SJ
Department of Pediatric Cardiology, Sejong Heart Institute, Sosa-Ku Pucheon City, Kyunggi-do, Korea. ksoojn@yahoo.co.kr
Park
In-Seung
IS
Song
Jin-Young
JY
Lee
Jae-Young
JY
Shim
Woo-Sup
WS
D000284:Administration, Oral; D001798:Blood Proteins / Q000032:analysis; D002118:Calcium / Q000097:blood; D002125:Calcium Gluconate / Q000008:administration & dosage*; D018729:Fontan Procedure / Q000009:adverse effects*; D006801:Humans; D007223:Infant; D008297:Male; D011504:Protein-Losing Enteropathies / Q000097:blood / Q000209:etiology / Q000628:therapy*; D012709:Serum Albumin / Q000032:analysis
D001798:Blood Proteins; D012709:Serum Albumin; D002125:Calcium Gluconate; D002118:Calcium