title: Reversal of protein-losing enteropathy with calcium replacement in a patient after Fontan operation.
abstract: Protein-losing enteropathy occurs in patients following the modified Fontan procedure. Treatment is still controversial. We describe a boy who developed protein-losing enteropathy 18-months after an extracardiac Fontan procedure. Treatment with calcium for hypocalcemia attenuated the protein loss with subsequent normalization of serum total protein and albumin levels. Decrease of oral calcium and subsequent decrease of serum ionized calcium level were associated with relapse of hypoalbuminemia. This was again treated successfully with calcium and vitamin D replacement.
authors.affiliation: Department of Pediatric Cardiology, Sejong Heart Institute, Sosa-Ku Pucheon City, Kyunggi-do, Korea. ksoojn@yahoo.co.kr
authors.forename: Soo-Jin
authors.initials: SJ
authors.lastname: Kim
authors.forename: In-Seung
authors.initials: IS
authors.lastname: Park
authors.forename: Jin-Young
authors.initials: JY
authors.lastname: Song
authors.forename: Jae-Young
authors.initials: JY
authors.lastname: Lee
authors.forename: Woo-Sup
authors.initials: WS
authors.lastname: Shim
mesh_terms: D000284:Administration, Oral; D001798:Blood Proteins / Q000032:analysis; D002118:Calcium / Q000097:blood; D002125:Calcium Gluconate / Q000008:administration & dosage*; D018729:Fontan Procedure / Q000009:adverse effects*; D006801:Humans; D007223:Infant; D008297:Male; D011504:Protein-Losing Enteropathies / Q000097:blood / Q000209:etiology / Q000628:therapy*; D012709:Serum Albumin / Q000032:analysis
chemical_list: D001798:Blood Proteins; D012709:Serum Albumin; D002125:Calcium Gluconate; D002118:Calcium