Kerinokeratosis papulosa with a type 2 segmental manifestation.
Kerinokeratosis papulosa is a synonym for "waxy keratoses of childhood" (Greek kerinos = waxy). Affected children show multiple disseminated shiny papules involving the entire skin, with a preponderance on the trunk, the upper arms, and the thighs. We describe an additional case supporting the notion that this is a distinctive disorder of keratinization. In this case, the disorder was superimposed by a linear area of excessive involvement affecting the left arm in the form of an epidermal nevus with a shiny, waxy appearance. This linear lesion may be best explained as a type 2 segmental manifestation of the disorder, which would imply that kerinokeratosis papulosa is inherited as an autosomal-dominant trait.
Happle
Rudolf
R
Department of Dermatology, Phillipp University of Marburg, Deutschhausstrasse 9, 35033 Marburg, Germany. happle@mailer.uni-marburg.de
Fleiner
Joachim
J
Loskamp
Ulrike
U
D002648:Child; D005260:Female; D006801:Humans; D007642:Keratosis / Q000473:pathology*; D012867:Skin / Q000473:pathology*