title: Kerinokeratosis papulosa with a type 2 segmental manifestation.
abstract: Kerinokeratosis papulosa is a synonym for "waxy keratoses of childhood" (Greek kerinos = waxy). Affected children show multiple disseminated shiny papules involving the entire skin, with a preponderance on the trunk, the upper arms, and the thighs. We describe an additional case supporting the notion that this is a distinctive disorder of keratinization. In this case, the disorder was superimposed by a linear area of excessive involvement affecting the left arm in the form of an epidermal nevus with a shiny, waxy appearance. This linear lesion may be best explained as a type 2 segmental manifestation of the disorder, which would imply that kerinokeratosis papulosa is inherited as an autosomal-dominant trait.
authors.affiliation: Department of Dermatology, Phillipp University of Marburg, Deutschhausstrasse 9, 35033 Marburg, Germany. happle@mailer.uni-marburg.de
authors.forename: Rudolf
authors.initials: R
authors.lastname: Happle
authors.forename: Joachim
authors.initials: J
authors.lastname: Fleiner
authors.forename: Ulrike
authors.initials: U
authors.lastname: Loskamp
mesh_terms: D002648:Child; D005260:Female; D006801:Humans; D007642:Keratosis / Q000473:pathology*; D012867:Skin / Q000473:pathology*