Extraocular sebaceous carcinoma in a patient with Muir-Torre syndrome.
BACKGROUND
Sebaceous carcinoma is a rare, aggressive neoplasm that arises from the adnexal epithelium of sebaceous glands and is commonly associated with Muir-Torre syndrome.


OBJECTIVE
The metastatic potential of extraocular sebaceous carcinoma warrants a thorough evaluation to establish the extent of disease.


METHODS
We describe a 55-year-old man who presented with an asymptomatic abdominal wall mass 3 years after definitive diagnosis of Muir-Torre syndrome.


RESULTS
A biopsy of the surgical specimen revealed sebaceous carcinoma.


CONCLUSIONS
Dermatologists are crucial to the early recognition and diagnosis of extraocular sebaceous carcinoma. In our patient with documented Muir-Torre syndrome, continued surveillance allowed for prompt recognition and treatment of this associated cutaneous malignancy.
Harrington
Cynthia R
CR
Department of Dermatology, Stanford University Medical Center, Stanford, California 94305, USA.
Egbert
Barbara M
BM
Swetter
Susan M
SM
D000005:Abdomen; D018266:Adenocarcinoma, Sebaceous / Q000473:pathology*; D000236:Adenoma / Q000473:pathology*; D003110:Colonic Neoplasms / Q000473:pathology / Q000601:surgery; D006801:Humans; D007150:Immunohistochemistry; D008297:Male; D008875:Middle Aged; D012626:Sebaceous Gland Neoplasms / Q000473:pathology*; D012878:Skin Neoplasms / Q000473:pathology*; D013577:Syndrome