title: [Severe cyanosis after total cavopulmonary connection, corrected by surgical ligation of the suprahepatic veins].
abstract: We describe a patient with a diagnosis of heterotaxia and independent drainage of the suprahepatic veins into the venous atrium who underwent total extracardiac cavopulmonary connection in which hepatic vein drainage remained directly into the atrium. In the immediate postoperative period she showed increasing cyanosis that suggested substantial right-to-left shunt. Surgical ligation of the suprahepatic veins resolved the complication effectively without signs of hepatic congestion or portal hypertension.
authors.affiliation: Servicio de Cirugía Cardíaca Infantil, Hospital Universitario La Paz, Madrid, Spain. dborches.hulp@madrid.salud.org
authors.forename: Daniel
authors.initials: D
authors.lastname: Borches
authors.forename: Gustavo
authors.initials: G
authors.lastname: Brochet
authors.forename: Angel
authors.initials: A
authors.lastname: Aroca
authors.forename: Luis
authors.initials: L
authors.lastname: García-Guereta
authors.forename: Ernesto
authors.initials: E
authors.lastname: Sanz
authors.forename: Gregorio
authors.initials: G
authors.lastname: Cordovilla
mesh_terms: D000293:Adolescent; D003490:Cyanosis / Q000209:etiology* / Q000601:surgery*; D005260:Female; D018729:Fontan Procedure / Q000009:adverse effects*; D006503:Hepatic Veins; D006801:Humans; D008026:Ligation; D012720:Severity of Illness Index