[Congenital respiratory cystic dysplasias in children].
Diagnosis and treatment of congenital respiratory cystic dysplasias - more complicated than acquired pulmonary diseases. In 20% of cases treatment should be started in newborn age because of respiratory distress syndrome.


METHODS
During the period of 1990-2002 we have diagnosed and treated 30 patients due to congenital respiratory cystic dysplasias. Clinical symptoms, diagnostic methods, indications for the operation and results of the surgical treatment were analyzed.


RESULTS
We operated on 18 boys and 12 girls. Age of the patients - 6 newborns, 8 infants, 3 children from 1 till 3 years, 13 patients from 7 till 15 years. Lobectomy was performed for 13 patients, segmentectomy in 1 case, and removal of the cyst in 14 cases. In 1 case videotoracoscopy and in 1 case angiography was made. All patients survived. Other diseases were found in 16 cases.


CONCLUSIONS
Congenital respiratory cystic dysplasias are serious respiratory disease of newborns and children which can cause respiratory distress syndrome. 1. Because of respiratory distress, possible infection and malignant transformation surgical treatment is recommended. 2. Antenatal diagnosis of congenital respiratory cystic dysplasias could enable the neonatologist and surgeon to prepare for the treatment, because in 20% of cases the treatment is necessary in early postnatal period.
Maknavicius
Stanislovas Jonas
SJ
Clinic of Pediatric Surgery, Children's Hospital, Vilnius University, Santariskiu 7, Vilnius 2600, Lithuania. gintas.posiunas@rvuvl.vu.lt
Posiūnas
Gintas
G
Strupas
Sigitas
S
D000293:Adolescent; D000367:Age Factors; D001994:Bronchogenic Cyst / Q000150:complications / Q000175:diagnosis; D002648:Child; D002675:Child, Preschool; D015615:Cystic Adenomatoid Malformation of Lung, Congenital / Q000150:complications / Q000175:diagnosis / Q000601:surgery; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D008171:Lung Diseases / Q000151:congenital* / Q000175:diagnosis; D008297:Male; D011013:Pneumonectomy; D011247:Pregnancy; D011296:Prenatal Diagnosis; D011656:Pulmonary Emphysema / Q000151:congenital / Q000175:diagnosis; D012127:Respiratory Distress Syndrome, Newborn / Q000175:diagnosis / Q000209:etiology; D012737:Sex Factors; D013906:Thoracoscopy