[Rare case of congenital transsphenoidal meningoencephalocele causing respiratory problems].
BACKGROUND
Congenital meningoencephalocele is a rare and severe malformation.


OBJECTIVE
The authors describe the case of congenital, basal transsphenoidal meningoencephalocele associated with other neurological malformations, which projected between the margins of palatoschisis producing respiratory problems at neonatal age.


METHODS
Presented with detailed photo-documentation.


RESULTS
Cranial meningoencephalocele reconstruction with an approach of bifrontal craniotomy was performed. The base of skull was closed multilaminarly with auto-graft gained from parietal bone and Lyodura. The closure of nasopharyngeal sac was performed in second sitting. Postoperatively the progression of hydrocephalus was so extensive, that implantation of ventriculo-peritoneal shunt was unavoidable. Later on closure of tracheotomy performed for continued air passage support was done. The authors report the course of disease and the surgeries performed.


CONCLUSIONS
Auto-graft from skull bone for closure of large basal-cranial defect proved to be ideal. Prognosis depends on other malformations. Successful treatment needs co-operation of different specialties.
Fücsek
Mihály
M
Petz Aladár Megyei Oktató Kórház, Csecsemó- és Gyermekgyógyászati Központ, Gyór.
Szarvas
István
I
Kelemen
Agnes
A
Pohárnok
László
L
Horváth
Imre
I
D004677:Encephalocele / Q000150:complications* / Q000175:diagnosis* / Q000601:surgery; D006801:Humans; D007231:Infant, Newborn; D008279:Magnetic Resonance Imaging; D008297:Male; D008588:Meningocele / Q000150:complications* / Q000175:diagnosis* / Q000601:surgery; D012120:Respiration Disorders / Q000209:etiology*; D013101:Sphenoid Sinus / Q000000981:diagnostic imaging / Q000473:pathology / Q000601:surgery; D014057:Tomography, X-Ray Computed