Giant transdiaphragmatic duodenal duplication with an intraspinal neurenteric cyst as part of the split notochord syndrome: report of a case.
We report the case of a 6-month-old girl with a giant transdiaphragmatic duodenal duplication connecting to a cervical intraspinal cyst, which compressed the heart and lung, causing severe respiratory distress. We removed the intraspinal neurenteric cyst through a posterior cervical incision at the C6 and C7 level, and the duodenal duplication cyst in the mediastinum was removed through a right thoracotomy. Her respiratory symptoms were completely resolved by these operations.
Wakisaka
Munechika
M
Division of Pediatric Surgery, St. Marianna University School of Medicine, 2-16-1 Sugao, Miyamae-ku, Kawasaki 216-8511, Japan.
Nakada
Kounosuke
K
Kitagawa
Hiroaki
H
Shimada
Harutugu
H
Nosaka
Shunsuke
S
D000015:Abnormalities, Multiple; D004386:Duodenum / Q000002:abnormalities*; D005260:Female; D006801:Humans; D007223:Infant; D008279:Magnetic Resonance Imaging; D008476:Mediastinal Cyst / Q000175:diagnosis / Q000601:surgery; D009436:Neural Tube Defects / Q000150:complications / Q000601:surgery*; D009672:Notochord / Q000002:abnormalities*; D012131:Respiratory Insufficiency / Q000150:complications*; D013577:Syndrome