Dental alterations associated with X-linked hypophosphatemic rickets.
The X-linked hypophosphatemic rickets is a rare metabolic disorder characterized by low serum phosphate levels caused by a decreased renal tubular reabsorption of inorganic phosphates. The initial complaints are a delay in the development of walking caused by deformity of the legs. Oral findings include poorly mineralized dentin, enlarged pulp chambers and root canals, and periradicular abscesses in caries-free teeth. We present three patients from the same family with X-linked hypophosphatemic rickets showing bone and dental alterations.
Pereira
Claudio Maranhão
CM
Department of Semiology and Oral Pathology, School of Dentistry of Piracicaba, State University of Campinas, Piracicaba/SP, Brazil.
de Andrade
Cleverton Roberto
CR
Vargas
Pablo Agustín
PA
Coletta
Ricardo Della
RD
de Almeida
Oslei Paes
OP
Lopes
Márcio Ajudarte
MA
D000328:Adult; D002648:Child; D003790:Dental Pulp Necrosis / Q000209:etiology / Q000628:therapy; D003824:Denture, Complete; D005260:Female; D006801:Humans; D007015:Hypophosphatemia, Familial / Q000150:complications*; D008297:Male; D010482:Periapical Abscess / Q000209:etiology; D012390:Root Canal Therapy; D014071:Tooth Abnormalities / Q000209:etiology* / Q000628:therapy