[Intra-articular myxofibrosarcoma of the hip in a 10-year-old child].
We report a case of intra-articular myxofibrosarcoma with acetabular involvement observed in a 10-Year-old boy. Myxofibrosarcoma is a frequent soft tIssue sarcoma usually observed in elderly subjects. It is extremely rare in children and has not been reported previously before the age of 22 Years. Myxofibrosarcoma is a specific type of soft tIssue tumor. Discussion continues concerning its relation with the myxoid variant of malignant fibrous histiocytoma. The myxoid matrix harbors fibroblastic cells with a curvilinear vessel configuration. Prognosis is good after complete resection and careful surveillance. Local recurrence may occur generally with progression of the tumor stage and risk of later metastasis. This is the first report of an intra-articular localization. We discuss the therapeutic options.
Viejo-Fuertes
D
D
Service de Chirurgie Orthopédique et de Traumatologie de l'Appareil Locomoteur, Cliniques Universitaires Saint-Luc (UCL), 1200 Bruxelles, Belgique.
Mousny
M
M
Docquier
P-L
PL
Dubuc
J-E
JE
Lecouvet
F
F
Noel
H
H
Rombouts
J-J
JJ
D002648:Child; D005354:Fibrosarcoma / Q000473:pathology* / Q000601:surgery; D006621:Hip Joint / Q000473:pathology* / Q000601:surgery; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D012983:Soft Tissue Neoplasms / Q000473:pathology* / Q000601:surgery