title: [Peutz-Jeghers syndrome].
abstract: Peutz-Jeghers syndrome is an autonomic dominant disease characterized by hamartomatous polyps and mucocutaneous hyperpigmentation. We present 16 cases; females were more affected. The most common presenting complaints were of gastrointestinal tract. All polyps found were hamartomatous with general distribution through gastrointestinal tract. Endoscopic polypectomy should be carried out for treatment. Radiologic, endoscopic and histologic studies should be conducted for long-term follow-up, because of high risk of malignancy.
authors.affiliation: Servicio de Gastroenterología y Nutrición Pediátrica, Instituto Nacional de Pediatría (INP), Insurgentes Sur 3700-C, Col. Insurgentes Cuicuilco, 04530 México, D.F. Correo.
authors.forename: Roberto
authors.initials: R
authors.lastname: Cervantes Bustamante
authors.forename: Luis Carlos
authors.initials: LC
authors.lastname: Ocampo del Prado
authors.forename: Flora
authors.initials: F
authors.lastname: Zárate Mondragón
authors.forename: Norberto
authors.initials: N
authors.lastname: Mata Rivera
authors.forename: Jaime A
authors.initials: JA
authors.lastname: Ramírez-Mayans
authors.forename: María Antonieta
authors.initials: MA
authors.lastname: Mora Tiscareño
authors.forename: L N
authors.initials: LN
authors.lastname: García Campos
mesh_terms: D000293:Adolescent; D016099:Endoscopy, Gastrointestinal; D005260:Female; D006801:Humans; D007417:Intestinal Polyps / Q000473:pathology; D008297:Male; D010375:Pedigree; D010580:Peutz-Jeghers Syndrome / Q000175:diagnosis / Q000453:epidemiology / Q000473:pathology