A case of primary diffuse tracheobronchial amyloidosis.
Tracheobronchial amyloidosis (TBA) is an uncommon localized form of amyloidosis with fewer than 150 reported cases in the literature. We report a case of primary diffuse tracheobronchial amyloidosis who presented with cough, wheezing, recurrent and progressive dyspnea as well as hemoptysis. Though there is no universally accepted treatment for the localized form, this patient was successfully treated with three sessions of bronchoscopic resection and adjuvant steroids. This report will review the various types of amyloidosis of the respiratory tract and their clinical features, in addition to discussing the different available treatment modalities for TBA.
Gibbaoui
Hayssam
H
Tawam Hospital, Abu Dhabi, United Arab Emirates. h.gibbaoui@voila.fr
Abouchacra
S
S
Yaman
M
M
D000686:Amyloidosis / Q000175:diagnosis / Q000000981:diagnostic imaging / Q000601:surgery*; D001982:Bronchial Diseases / Q000175:diagnosis / Q000000981:diagnostic imaging / Q000601:surgery*; D001999:Bronchoscopy; D005260:Female; D005938:Glucocorticoids / Q000627:therapeutic use; D006801:Humans; D008875:Middle Aged; D011239:Prednisolone / Q000627:therapeutic use; D012086:Reoperation; D014057:Tomography, X-Ray Computed; D014133:Tracheal Diseases / Q000175:diagnosis / Q000000981:diagnostic imaging / Q000601:surgery*
D005938:Glucocorticoids; D011239:Prednisolone