[Peutz-Jeghers syndrome].
Peutz-Jeghers syndrome is an autonomic dominant disease characterized by hamartomatous polyps and mucocutaneous hyperpigmentation. We present 16 cases; females were more affected. The most common presenting complaints were of gastrointestinal tract. All polyps found were hamartomatous with general distribution through gastrointestinal tract. Endoscopic polypectomy should be carried out for treatment. Radiologic, endoscopic and histologic studies should be conducted for long-term follow-up, because of high risk of malignancy.
Cervantes Bustamante
Roberto
R
Servicio de Gastroenterología y Nutrición Pediátrica, Instituto Nacional de Pediatría (INP), Insurgentes Sur 3700-C, Col. Insurgentes Cuicuilco, 04530 México, D.F. Correo.
Ocampo del Prado
Luis Carlos
LC
Zárate Mondragón
Flora
F
Mata Rivera
Norberto
N
Ramírez-Mayans
Jaime A
JA
Mora Tiscareño
María Antonieta
MA
García Campos
L N
LN
D000293:Adolescent; D016099:Endoscopy, Gastrointestinal; D005260:Female; D006801:Humans; D007417:Intestinal Polyps / Q000473:pathology; D008297:Male; D010375:Pedigree; D010580:Peutz-Jeghers Syndrome / Q000175:diagnosis / Q000453:epidemiology / Q000473:pathology