title: A case of Arnold-Chiari syndrome with flaccid paralysis and huge syringomyelia.
abstract: METHODS
  A case report.
  
  
  METHODS
  Department of Orthopaedic Surgery, Shiga University of Medical Science, Japan.
  
  
  METHODS
  A 13-year-old woman presented progressive weakness in the lower extremities, with predominance on the right. Magnetic resonance (MR) imaging revealed a huge syrinx. The patient also showed scoliosis, cleft palate, hearing impairment, excessive sweating, hairiness, dural ectasia, and malformation of the skull. METHOD AND OBJECTIVES: We treated a very rare case of Arnold-Chiari syndrome, which presented with flaccid paralysis. Methods of differential diagnosis and suitable treatment are discussed.
  
  
  CONCLUSIONS
  Both the syrinx and muscle strength were quickly improved following placement of a syringo-peritoneal (S-P) shunt, after which the patient recovered the ability to walk. However, transient hypesthesia in the right hand occurred after the operation. The syrinx around the conus was thought to play a crucial role in the etiology of the patient case, which showed unique symptoms.
authors.affiliation: Department of Orthopaedic Surgery, Shiga University of Medical Science, Tsukinowa-cho, Seta, Otsu, Shiga, Japan.
authors.forename: T
authors.initials: T
authors.lastname: Mimura
authors.forename: S
authors.initials: S
authors.lastname: Asajima
authors.forename: Y
authors.initials: Y
authors.lastname: Saruhashi
authors.forename: Y
authors.initials: Y
authors.lastname: Matsusue
mesh_terms: D000293:Adolescent; D001139:Arnold-Chiari Malformation / Q000175:diagnosis* / Q000601:surgery*; D002557:Cerebrospinal Fluid Shunts; D005260:Female; D020233:Gait Disorders, Neurologic / Q000175:diagnosis / Q000601:surgery; D006801:Humans; D009123:Muscle Hypotonia / Q000175:diagnosis* / Q000601:surgery*; D018908:Muscle Weakness / Q000601:surgery; D010243:Paralysis / Q000175:diagnosis / Q000601:surgery; D012720:Severity of Illness Index; D013595:Syringomyelia / Q000175:diagnosis* / Q000601:surgery*; D016896:Treatment Outcome