[Polycystic hepatic and renal disease with portal hypertension and ascites (a case report)].
The case of a 50 years old man with polycystic liver and kidneys and ascites which had been diagnosed by laparoscopy and pyeloureterography, is reported. Chronic renal failure was the cause of death, and obvious signs of portal hypertension were found at necropsy. The loss of hepatic structure produced by pericystic fibrosis, regenerative nodules, thrombosis of portal branches, and necrotic areas, is stressed as an important cause of portal hypertension. This pathogenesis could be similar to that of cirrhosis. Both portal hypertension and ascites are highly uncommon facts in adults' polycystic livers.
Findor
J A
JA
Sala XII y Servicio de Anatomía Patológica del Hospital J. M. Ramos Mejía, Buenos Aires.
Matute
M I
MI
González Cueto
D
D
Benzecry
E
E
D001201:Ascites / Q000150:complications* / Q000473:pathology; D003560:Cysts / Q000150:complications* / Q000473:pathology; D017809:Fatal Outcome; D006801:Humans; D006975:Hypertension, Portal / Q000150:complications* / Q000473:pathology; D008107:Liver Diseases / Q000150:complications* / Q000473:pathology; D008297:Male; D008875:Middle Aged; D007690:Polycystic Kidney Diseases / Q000150:complications* / Q000473:pathology