title: Successful bladder management for a pure urogenital sinus anomaly.
abstract: We report on a case of a pure urogenital sinus anomaly presented with bladder distention. A seven-day-old girl with an abdominal distension was referred to the Division of Urology, Hakodate Central Hospital, Hakodate, Japan. A common urogenital sinus without abnormalities in the labium, clitoris or anus was found. A computed tomography (CT) scan documented a distended bladder without hydrometrocolpos or hydroureteronephrosis. Cystography performed at 44 days revealed a large flaccid bladder without ureteral reflux. Urinary management by an indwelling urethral catheter was maintained until 3 months, when an endoscopic examination was performed and a stenotic urethral-type urogenital sinus with low confluence was diagnosed. Parents successfully instituted clean intermittent catheterization as a temporary urinary management, and postvoid residual urine gradually decreased. At 2 years of age, flap vaginoplasty was performed. In an urodynamic study performed postoperatively, the detrusor pressure during voiding was 40-50 cmH(2)O. The patient maintained spontaneous voiding without consequences. Appropriate urinary care is essential to prevent urological complications in cases with a pure urogenital sinus anomaly.
authors.affiliation: Division of Urology, Hakodate Central Hospital, Hakodate, Japan. kitta@fb3.so-net.ne.jp
authors.forename: Takeya
authors.initials: T
authors.lastname: Kitta
authors.forename: Hidehiro
authors.initials: H
authors.lastname: Kakizaki
authors.forename: Daiki
authors.initials: D
authors.lastname: Iwami
authors.forename: Katutoshi
authors.initials: K
authors.lastname: Tanda
mesh_terms: D005260:Female; D006801:Humans; D007231:Infant, Newborn; D014521:Urethra / Q000002:abnormalities* / Q000601:surgery*; D001743:Urinary Bladder / Q000503:physiopathology; D014555:Urination Disorders / Q000503:physiopathology / Q000601:surgery*; D014563:Urodynamics; D014621:Vagina / Q000002:abnormalities* / Q000601:surgery*