title: Bilateral adrenal cystic neuroblastoma with superior vena cava syndrome and massive intracystic haemorrhage.
abstract: Bilateral cystic adrenal tumours are a rare presentation of neuroblastoma. Intratumoural haemorrhage is a frequent finding in neuroblastoma, but is rarely symptomatic. We present an 11-month-old girl with predominantly cystic bilateral neuroblastomas and distant lymph-node metastasis. Massive intracystic haemorrhage and superior vena cava (SVC) syndrome were ominous prognostic factors, leading to death. Large tumours with intracystic haemorrhage might require a conservative approach.
authors.affiliation: Department of Paediatric Oncology, Medical Faculty, Ondokuz Mayis University, Samsun, Turkey. fgpinarli1@ttnet.net.tr
authors.forename: Faruk Guclu
authors.initials: FG
authors.lastname: Pinarli
authors.forename: Murat
authors.initials: M
authors.lastname: Danaci
authors.forename: Burak
authors.initials: B
authors.lastname: Tander
authors.forename: Ayhan
authors.initials: A
authors.lastname: Dagdemir
authors.forename: Baris
authors.initials: B
authors.lastname: Diren
authors.forename: Sabri
authors.initials: S
authors.lastname: Acar
authors.forename: Riza
authors.initials: R
authors.lastname: Rizalar
mesh_terms: D000310:Adrenal Gland Neoplasms / Q000175:diagnosis* / Q000473:pathology; D003952:Diagnostic Imaging; D017809:Fatal Outcome; D005260:Female; D006470:Hemorrhage / Q000175:diagnosis*; D006801:Humans; D007223:Infant; D008207:Lymphatic Metastasis; D009447:Neuroblastoma / Q000175:diagnosis* / Q000473:pathology; D013479:Superior Vena Cava Syndrome / Q000175:diagnosis*