Bilateral adrenal cystic neuroblastoma with superior vena cava syndrome and massive intracystic haemorrhage.
Bilateral cystic adrenal tumours are a rare presentation of neuroblastoma. Intratumoural haemorrhage is a frequent finding in neuroblastoma, but is rarely symptomatic. We present an 11-month-old girl with predominantly cystic bilateral neuroblastomas and distant lymph-node metastasis. Massive intracystic haemorrhage and superior vena cava (SVC) syndrome were ominous prognostic factors, leading to death. Large tumours with intracystic haemorrhage might require a conservative approach.
Pinarli
Faruk Guclu
FG
Department of Paediatric Oncology, Medical Faculty, Ondokuz Mayis University, Samsun, Turkey. fgpinarli1@ttnet.net.tr
Danaci
Murat
M
Tander
Burak
B
Dagdemir
Ayhan
A
Diren
Baris
B
Acar
Sabri
S
Rizalar
Riza
R
D000310:Adrenal Gland Neoplasms / Q000175:diagnosis* / Q000473:pathology; D003952:Diagnostic Imaging; D017809:Fatal Outcome; D005260:Female; D006470:Hemorrhage / Q000175:diagnosis*; D006801:Humans; D007223:Infant; D008207:Lymphatic Metastasis; D009447:Neuroblastoma / Q000175:diagnosis* / Q000473:pathology; D013479:Superior Vena Cava Syndrome / Q000175:diagnosis*