Moyamoya disease with repeated intracranial haemorrhage in two consecutive pregnancies.
A 26-year-old woman presented with an intraventricular haemorrhage during the 27th week of gestation in July 1996, and recovered without general or neurological complications after external ventricular drainage. The fetus was delivered spontaneously through the vagina at the 30th week of gestation, but eventually died. Cerebral angiography demonstrated typical appearances of moyamoya disease with occlusion of the supraclinoid portion of both internal carotid arteries and presence of abnormal collateral vessels. Five years later the second haemorrhage, an intracerebral haematoma in the right temporoparietooccipital area, occurred during the 28th week of pregnancy. Emergency craniotomy was performed and the intracerebral haematoma was removed totally. It is still unknown whether repeated pregnancy increases the risk of cerebrovascular accident in moyamoya disease. A long-term follow up study of several patients with haemorrhagic moyamoya disease is needed to clarify risk factors for rebleeding.
Kim
Tae-Sun
TS
Department of Neurosurgery, Chonnam National University Hospital & Medical School, Kwangju, South Korea. taesun@cnuh.chonnam.ac.kr
Lee
Je-Hyuk
JH
Kim
In-Young
IY
Lee
Jung-Kil
JK
Jung
Shin
S
Kim
Jae-Hyoo
JH
Kim
Soo-Han
SH
Kang
Sam-Suk
SS
D000328:Adult; D017023:Coronary Angiography / Q000379:methods; D005260:Female; D006801:Humans; D020300:Intracranial Hemorrhages / Q000209:etiology* / Q000473:pathology; D009072:Moyamoya Disease / Q000150:complications*; D011247:Pregnancy; D011249:Pregnancy Complications, Cardiovascular / Q000209:etiology* / Q000473:pathology; D012008:Recurrence