Biliary atresia with associated complicated anorectal and urogenital malformations.
We report on a girl with biliary atresia (BA) who also suffered with anorectal agenesis without fistula and complicated urogenital malformation. The outcome of patients with these severe anomalies is poor, but she has survived without liver and/or renal transplantation for more than 3 years. A careful treatment plan for each anomaly in addition to prevention of cholangitis and urinary tract infection is indispensable for managing these complicated anomalies.
Amae
Shintaro
S
Department of Pediatric Surgery, Graduate School of Medicine, Tohoku University, 1-1 Seiryo-machi, 980-8574 Sendai, Aoba-ku, Japan.
Kamiyama
Takamichi
T
Nio
Masaki
M
Yoshida
Shigehiko
S
Hayashi
Yutaka
Y
Tanikaze
Saburo
S
Ohi
Ryoji
R
D000015:Abnormalities, Multiple; D000328:Adult; D001003:Anal Canal / Q000002:abnormalities; D001656:Biliary Atresia / Q000150:complications* / Q000601:surgery; D004108:Dilatation, Pathologic; D005260:Female; D005836:Genitalia, Female / Q000002:abnormalities*; D006801:Humans; D012007:Rectum / Q000002:abnormalities*; D014513:Ureter / Q000473:pathology; D014551:Urinary Tract / Q000002:abnormalities*