A child with undifferentiated sarcoma of the liver complicated with bronchobiliary fistula and detected by hepatobiliary scintigraphy.
Undifferentiated (embryonal) sarcoma of the liver (USL) is a rare malignant mesenchymal tumor principally affecting patients of pediatric age. Bronchobiliary fistula is a very rare complication in patients with liver tumor. To the authors' knowledge, this is the first report of a bronchobiliary fistula resulting from tumor invasion in a child with liver sarcoma. A 12-year-old boy was diagnosed to have USL of the right liver lobe, invading the diaphragm. An extended right hepatectomy and total resection of the mass was performed, leaving patchy tumoral invasion of the anterior diaphragmatic surface followed by combined chemotherapy regimen. Six months after the operation, the presence of bilious sputum suggested a bronchobiliary fistula, which was confirmed by hepatobiliary scintigraphy. The patient underwent a right thoracotomy and fistula division. Although bronchobiliary fistula is a very rare complication in patients with hepatic tumors, suspicion in the appropriate clinical setting is necessary to recognize this problem. Hepatobiliary scintigraphy is the useful diagnostic procedure to define bronchobiliary fistula in children with liver tumor and clinical suspicion of bronchobiliary fistula.
Corapçioglu
Funda
F
fundacorapcioglu@yahoo.com
Sarper
Nazan
N
Demir
Hakan
H
Güvenç
B Haluk
BH
Sözübir
Selami
S
Akansel
Gür
G
Berk
Fatma Sen
FS
D001660:Biliary Tract Diseases / Q000150:complications* / Q000000981:diagnostic imaging*; D001983:Bronchial Fistula / Q000150:complications* / Q000000981:diagnostic imaging*; D002648:Child; D006801:Humans; D008113:Liver Neoplasms / Q000150:complications* / Q000175:diagnosis / Q000601:surgery; D008297:Male; D018365:Neoplasm, Residual; D011877:Radionuclide Imaging; D012086:Reoperation; D012509:Sarcoma / Q000150:complications* / Q000175:diagnosis / Q000601:surgery; D019785:Technetium Tc 99m Disofenin
D019785:Technetium Tc 99m Disofenin