Acute pulmonary edema in a newborn with infracardiac type total anomalous pulmonary venous return and surgical repair.
Total anomalous pulmonary venous return (TAPVR) is a rare congenital pathology. Early diagnosis and urgent surgery are life-saving, especially in newborns with pulmonary venous obstruction, which is most commonly seen with infracardiac type. A three-day-old baby boy presented to another clinic with tachypnea and cyanosis. Initial work-up aimed at ruling out persistant pulmonary hypertension, respiratory distress syndrome and pneumonia. Acute pulmonary edema then developed, and on echocardiography obstructive type infracardiac TAPVR was suspected. Cardiac catheterization was done for definitive diagnosis. Urgent surgery was undertaken and pulmonary veins were anastomozed to left atrium with posterior approach. Patient was extubated at 10th day and discharged after three weeks. During one-year follow-up the patient was free of symptoms. Infracardiac type TAPVR is a rare pathology in which early diagnosis and urgent surgery with special postoperative case are mandatory for survival.
Yalçinbaş
Yusuf Kenan
YK
Istanbul Memorial Hospital, Istanbul, Turkey.
Erek
Ersin
E
Salihoğlu
Ece
E
Oztürk
Nilüfer
N
Mamur
Gökhan
G
Soybir
Nerime
N
Sarioğlu
Ayşe
A
Sarioğlu
Tayyar
T
D000208:Acute Disease; D006328:Cardiac Catheterization; D002406:Catheterization, Peripheral; D005500:Follow-Up Studies; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D011654:Pulmonary Edema / Q000209:etiology*; D011667:Pulmonary Veins / Q000002:abnormalities*; D011668:Pulmonary Veno-Occlusive Disease / Q000150:complications / Q000175:diagnosis / Q000601:surgery*; D016896:Treatment Outcome