Rosai Dorfman disease.
We report an unusual presentation of sinus histiocytosis with massive lymphadenopathy (SHML), also called Rosai Dorfman disease. The child presented with bilateral proptosis with massive cervical lymphadenopathy. The patient had fair response to steroid therapy but relapsed during the course of the disease.
Mazhar
Erum
E
Department of Hematology, Liaquat National Hospital, Karachi. erumaaz@hotmail.com
Rahman
Naila
N
Qureshi
Hina
H
Bahar
Farkhunda
F
Zakai
Atif
A
Rahman
Arshalooz
A
Hashmi
Khalid Zafar
KZ
D002648:Child; D005094:Exophthalmos / Q000209:etiology; D005938:Glucocorticoids / Q000627:therapeutic use; D015618:Histiocytosis, Sinus / Q000150:complications / Q000175:diagnosis* / Q000188:drug therapy; D006801:Humans; D008297:Male; D011239:Prednisolone / Q000627:therapeutic use
D005938:Glucocorticoids; D011239:Prednisolone