title: Rosai Dorfman disease.
abstract: We report an unusual presentation of sinus histiocytosis with massive lymphadenopathy (SHML), also called Rosai Dorfman disease. The child presented with bilateral proptosis with massive cervical lymphadenopathy. The patient had fair response to steroid therapy but relapsed during the course of the disease.
authors.affiliation: Department of Hematology, Liaquat National Hospital, Karachi. erumaaz@hotmail.com
authors.forename: Erum
authors.initials: E
authors.lastname: Mazhar
authors.forename: Naila
authors.initials: N
authors.lastname: Rahman
authors.forename: Hina
authors.initials: H
authors.lastname: Qureshi
authors.forename: Farkhunda
authors.initials: F
authors.lastname: Bahar
authors.forename: Atif
authors.initials: A
authors.lastname: Zakai
authors.forename: Arshalooz
authors.initials: A
authors.lastname: Rahman
authors.forename: Khalid Zafar
authors.initials: KZ
authors.lastname: Hashmi
mesh_terms: D002648:Child; D005094:Exophthalmos / Q000209:etiology; D005938:Glucocorticoids / Q000627:therapeutic use; D015618:Histiocytosis, Sinus / Q000150:complications / Q000175:diagnosis* / Q000188:drug therapy; D006801:Humans; D008297:Male; D011239:Prednisolone / Q000627:therapeutic use
chemical_list: D005938:Glucocorticoids; D011239:Prednisolone