Feminising surgery in male pseudohermaphrodites.
In the framework of the international project between the paediatric surgery clinics of Kaunas Medical University and Copenhagen University Hospital, 34 patients raised as females were examined and treated. Eighteen patients were affected by androgen insensitivity syndrome, and 16 patients by mixed gonadal dysgenesis. All patients had a Y chromosome, although external genitalia was either typically female or had mixed features of both sexes. The particulars of diagnostics and treatment are discussed, focusing on surgical complications.
Zaparackaite
Indre
I
Kaunas Medical University Hospital, Paediatric Surgery Department, Eiveniu 2, LT-3007, Lithuania. indriuke@hotmail.com
Barauskas
Vidmantas
V
Nielsen
Ole Henrik
OH
D000367:Age Factors; D013734:Androgen-Insensitivity Syndrome / Q000235:genetics / Q000601:surgery; D002648:Child; D002675:Child, Preschool; D041322:Chromosomes, Human, Y / Q000235:genetics; D012809:Colon, Sigmoid / Q000601:surgery; D012734:Disorders of Sex Development / Q000235:genetics / Q000601:surgery*; D005260:Female; D005500:Follow-Up Studies; D006060:Gonadal Dysgenesis, Mixed / Q000235:genetics / Q000601:surgery; D006066:Gonads / Q000601:surgery; D006801:Humans; D007223:Infant; D008297:Male; D010641:Phenotype; D011183:Postoperative Complications; D014621:Vagina / Q000601:surgery