Esophageal involvement in cicatricial pemphigoid: a rare cause of dysphagia.
Cicatricial pemphigoid is a rare, autoimmune, blistering disorder affecting the mucous membranes and skin. Esophageal involvement affects a small proportion of affected individuals and may present up to 10 years after the initial onset of the disease. We present a case of esophageal cicatricial pemphigoid that presented initially as linear IgA disease. We describe the successful treatment of dysphagia by graded esophageal dilatations.
Syn
W-K
WK
Gastroenterology Department, Department of Medicine, Good Hope Hospital, Birmingham, UK. wsyn@doctors.org.uk
Ahmed
M M
MM
D003680:Deglutition Disorders / Q000209:etiology*; D004106:Dilatation / Q000379:methods; D004940:Esophageal Stenosis / Q000209:etiology* / Q000503:physiopathology / Q000628:therapy; D004947:Esophagus / Q000473:pathology*; D006801:Humans; D008297:Male; D008875:Middle Aged; D009092:Mucous Membrane / Q000473:pathology; D010390:Pemphigoid, Benign Mucous Membrane / Q000150:complications* / Q000503:physiopathology / Q000628:therapy