[Wilson's disease: study of 6 neurologic forms observed at the University Hospital in Conakry].
This report describes 6 cases of Wilson's disease observed at the University Hospital Center in Conakry, Guinea. Presenting symptoms involved extrapyramidal syndrome in 4 cases, psychomotor epilepsy in 1, and confusional syndrome in 1 case. Diagnosis was based on neuropsychic manifestations, Kayser-Fleicher corneal ring, liver failure, and impaired copper metabolism. Brain CT-scan depicted normal features in 3 cases, symmetric hypodensity of the lenticular nucleus in one, discrete ventricular dilatation of in one a and cortico-subcoetical atrophy in one.
Cissé
A
A
Service de neurologie, Hôpital Ignace Deen, Conakry, Guinée.
Morel
Y
Y
Coulibaly
M
M
Souaré
I S
IS
Cissé
A F
AF
Nabé
A
A
Camara
L M
LM
Cissé
B
B
Camara
S
S
Bangoura
S A
SA
Sylla
A
A
Dia
H
H
Da Silva
L
L
D000293:Adolescent; D000328:Adult; D001480:Basal Ganglia Diseases / Q000209:etiology; D001921:Brain / Q000473:pathology*; D002648:Child; D003221:Confusion / Q000209:etiology; D004827:Epilepsy / Q000209:etiology; D005260:Female; D016701:Guinea; D006527:Hepatolenticular Degeneration / Q000150:complications / Q000175:diagnosis / Q000473:pathology*; D006801:Humans; D008297:Male; D014057:Tomography, X-Ray Computed