[Oral aspects of porphyria].
Porphyria is a disease of specific enzymes in the biosynthesis of heme, caused by either genetic defects or environmental factors. This review of the literature presents the different types of porphyria and describes their possible causes, clinical signs, diagnosis and therapy. In addition, oral findings observed in patients with porphyria and the potential implications of the disease for dental treatment are discussed.
Kooijman
M M
MM
Afdeling Tandheelkundige Basiswetenschappen, sectie Orale Biochemie, Academisch Centrum Tandheelkunde Amsterdam (ACTA), Amsterdam.
Brand
H S
HS
D003729:Dental Care / Q000379:methods* / Q000592:standards; D003731:Dental Caries / Q000209:etiology / Q000517:prevention & control*; D006801:Humans; D009055:Mouth / Q000201:enzymology; D009910:Oral Hygiene; D011164:Porphyrias / Q000150:complications*; D013472:Sunlight / Q000009:adverse effects