title: Atrophic dermatofibrosarcoma protuberans: an uncommon and misleading variant.
abstract: A 23-year-old man presented with an atrophic lesion on his left anterior shoulder that had been present for at least 10 years. A previous biopsy had suggested a fibrohistiocytic origin; however, clinically it resembled morphoea or atrophoderma, and the lesion was observed. Fifteen months later, the lesion was noted to have grown slightly. A repeat biopsy showed dermatofibrosarcoma protuberans, with a storiform spindle cell proliferation with positive CD34 staining. The lesion was excised with a 3-cm margin. Awareness of this rare presentation may assist in earlier diagnosis.
authors.affiliation: Department of Dermatology, Our Lady of Lourdes Hospital, Drogheda, Louth, Ireland. jasonkwu@hotmail.com
authors.forename: Jason K
authors.initials: JK
authors.lastname: Wu
authors.forename: Mohsin M
authors.initials: MM
authors.lastname: Malik
authors.forename: Conleth Anthony
authors.initials: CA
authors.lastname: Egan
mesh_terms: D000328:Adult; D018952:Antigens, CD34 / Q000032:analysis; D014408:Biomarkers, Tumor / Q000032:analysis; D018223:Dermatofibrosarcoma / Q000175:diagnosis* / Q000473:pathology / Q000601:surgery; D003937:Diagnosis, Differential; D005500:Follow-Up Studies; D006801:Humans; D008297:Male; D012782:Shoulder; D012878:Skin Neoplasms / Q000175:diagnosis* / Q000473:pathology / Q000601:surgery; D016896:Treatment Outcome
chemical_list: D018952:Antigens, CD34; D014408:Biomarkers, Tumor