Meningioma in congenital adrenal hyperplasia.
A diversity of malignancies have been reported in patients with congenital adrenal hyperplasia. We report a case of multiple meningiomas, tumors which are more common in females and reported to have sex steroid receptors, in a 46,XX male (severe female hermaphrodite raised as a male) with 21-hydroxylase deficiency. The patient has been treated with glucocorticoids since 3 years of age and testosterone since puberty.
Strumph
P S
PS
University of Pittsburgh School of Medicine Division of Endocrinology & Metabolism, and Children's Hospital of Pittsburgh, Division of Endocrinology, Metabolism & Diabetes, Pittsburgh, Pennsylvania 15213, USA.
Stechison
M T
MT
Lee
P A
PA