Chediak-Higashi syndrome in the intensive care unit.
Chediak-Higashi Syndrome is a rare autosomal recessive disease characterized by recurrent infections, giant cytoplasmic granules and oculocutaneous albinism. We describe the clinical and laboratory findings of a patient with Chediak-Higashi syndrome who was diagnosed and treated in the intensive care unit because of bleeding tendency after surgery.
Demirkiran
Oktay
O
Department of Anaesthesiology, Cerrahpasa Medical School, Istanbul University, Sadi Sun ICU, Istanbul, Turkey. odemirkiran@superonline.com
Utku
Tughan
T
Urkmez
Seval
S
Dikmen
Yalim
Y
D000151:Acinetobacter Infections / Q000175:diagnosis / Q000188:drug therapy; D000900:Anti-Bacterial Agents / Q000627:therapeutic use; D001803:Blood Transfusion / Q000379:methods; D002609:Chediak-Higashi Syndrome / Q000175:diagnosis*; D002648:Child; D003422:Critical Care / Q000379:methods*; D005260:Female; D006400:Hematocrit / Q000379:methods; D006801:Humans; D007362:Intensive Care Units; D007442:Intubation, Intratracheal / Q000379:methods; D008991:Monitoring, Physiologic / Q000379:methods; D019647:Oral Surgical Procedures / Q000009:adverse effects; D010949:Plasma; D019106:Postoperative Hemorrhage / Q000628:therapy; D011552:Pseudomonas Infections / Q000175:diagnosis / Q000188:drug therapy; D012121:Respiration, Artificial / Q000379:methods
D000900:Anti-Bacterial Agents