Recurrent fatal pulmonary alveolar proteinosis after heart-lung transplantation in a child with lysinuric protein intolerance.
We present a case of recurrent pulmonary alveolar proteinosis after heart-lung transplantation in a child with lysinuric protein intolerance. The recurrence of the pulmonary disease provides further insight regarding the possible pathogenesis of pulmonary alveolar proteinosis and therapeutic options for this complication.
Department of Pediatrics, Federico II University, Naples, Italy.
Francesca
F
Santamaria
Gianluca
G
Brancaccio
Giancarlo
G
Parenti
Paola
P
Francalanci
Cosimo
C
Squitieri
Gianfranco
G
Sebastio
Carlo
C
Dionisi-Vici
Patrizia
P
D'argenio
Generoso
G
Andria
Francesco
F
Parisi
D020157:Amino Acid Transport Disorders, Inborn / Q000150:complications* / Q000652:urine; D017809:Fatal Outcome; D016041:Heart-Lung Transplantation; D006801:Humans; D007223:Infant; D008239:Lysine / Q000652:urine; D008297:Male; D011649:Pulmonary Alveolar Proteinosis / Q000150:complications* / Q000601:surgery*; D012008:Recurrence
D008239:Lysine