Poison and antidote: a novel model to study pathogenesis and therapy of LHON.
Giovanni
G
Manfredi
M Flint
MF
Beal
D000818:Animals; D004195:Disease Models, Animal; D042967:Electron Transport Complex I; D015316:Genetic Therapy / Q000379:methods*; D006801:Humans; D008565:Membrane Proteins / Q000235:genetics; D051379:Mice; D009245:NADH Dehydrogenase; D029242:Optic Atrophy, Hereditary, Leber / Q000235:genetics / Q000503:physiopathology / Q000628:therapy*; D013482:Superoxide Dismutase / Q000235:genetics; D000099156:Superoxide Dismutase 2
D042967:Electron Transport Complex I; D008565:Membrane Proteins; D009245:NADH Dehydrogenase; D013482:Superoxide Dismutase; D000099156:Superoxide Dismutase 2; C492251:Ndufa1 protein, mammalian; C118736:NDUFA1 protein, human; C492250:Ndufa1 protein, mouse