Postoperative death in a patient with unrecognized arrhythmogenic right ventricular dysplasia syndrome.
Arrhythmogenic right ventricular dysplasia is an inherited disease causing fatty replacement of heart tissue. This disease often presents as T-wave inversion in the anterior leads of the electrocardiogram (ECG) with life-threatening ventricular arrhythmias. In older patients, progressive right and left ventricular failure can develop. This is a case report of postoperative death occurring in a 59-yr-old woman with undiagnosed arrhythmogenic right ventricular dysplasia after hepatic cystectomy. The patient had T-wave inversion in the inferior ECG leads and no history of arrhythmias. During general anesthesia, cardiovascular collapse occurred in the absence of arrhythmias that was unresponsive to resuscitation.
Toh
Khay-Wee
KW
Department of Anesthesiology, Faculty of Medicine, University of Malaya, 27 Jalan Burhanuddin Helmi, Taman Tun Dr. Ismail, 60000 Kuala Lumpur, West Malaysia. tohkhaywee@hotmail.com
Nadesan
Kasinathan
K
Sie
Ming Yao
MY
Vijeyasingam
Raja
R
Tan
Patrick Seow Koon
PS
D000758:Anesthesia; D019571:Arrhythmogenic Right Ventricular Dysplasia / Q000150:complications / Q000473:pathology*; D003560:Cysts / Q000601:surgery; D004562:Electrocardiography; D017809:Fatal Outcome; D005260:Female; D006352:Heart Ventricles / Q000473:pathology; D006439:Hemodynamics / Q000502:physiology; D006801:Humans; D008107:Liver Diseases / Q000601:surgery; D008875:Middle Aged; D011183:Postoperative Complications / Q000473:pathology; D012770:Shock, Cardiogenic / Q000209:etiology