Renal sarcoma associated with adult polycystic kidney disease. A case report and literature review.
The development of renal cell carcinoma in Adult Polycystic Kidney Disease (APKD) has been reported in the literature; one of the features of renal malignancy in APKD is the difficulty to make a diagnosis, and the majority of cases reported are incidental findings at surgery or autopsy. We report a rare case of renal sarcoma in a patient with APKD. Sarcoma associated with APKD does not seem to have particular biological characteristics when compared with primary renal sarcoma; however the polycystic kidney represents an aggravating circumstance, because of the difficulty in making an early diagnosis of a disease with a poor prognosis.
Minardi
Daniele
D
Institute of Urology, Polytechnic University of the Marche Region, Ancona, Italy.
Mantovani
Paolo
P
Dellabella
Marco
M
Dell'Atti
Lucio
L
Mazzucchelli
Roberta
R
Santinelli
Alfredo
A
Scarpelli
Marina
M
Muzzonigro
Giovanni
G
D006801:Humans; D007680:Kidney Neoplasms / Q000150:complications*; D008297:Male; D008875:Middle Aged; D007690:Polycystic Kidney Diseases / Q000150:complications*; D012509:Sarcoma / Q000150:complications*