Recurrent fatal pulmonary alveolar proteinosis after heart-lung transplantation in a child with lysinuric protein intolerance.
We present a case of recurrent pulmonary alveolar proteinosis after heart-lung transplantation in a child with lysinuric protein intolerance. The recurrence of the pulmonary disease provides further insight regarding the possible pathogenesis of pulmonary alveolar proteinosis and therapeutic options for this complication.
Santamaria
Francesca
F
Department of Pediatrics, Federico II University, Naples, Italy.
Brancaccio
Gianluca
G
Parenti
Giancarlo
G
Francalanci
Paola
P
Squitieri
Cosimo
C
Sebastio
Gianfranco
G
Dionisi-Vici
Carlo
C
D'argenio
Patrizia
P
Andria
Generoso
G
Parisi
Francesco
F
D020157:Amino Acid Transport Disorders, Inborn / Q000150:complications* / Q000652:urine; D017809:Fatal Outcome; D016041:Heart-Lung Transplantation; D006801:Humans; D007223:Infant; D008239:Lysine / Q000652:urine; D008297:Male; D011649:Pulmonary Alveolar Proteinosis / Q000150:complications* / Q000601:surgery*; D012008:Recurrence
D008239:Lysine