[Anesthetic management of a child with Schwartz-Jampel syndrome].
A 6-year-old child with Schwartz-Jampel syndrome (SJS) underwent tenotomy of bilateral lower limbs under general anesthesia. Patient with SJS has problems such as difficulty of intubation owing to microstomia and jaw muscle rigidity, and is susceptible to malignant hyperthermia by using volatile inhalation anesthetics. In this case, we used a laryngeal mask for airway management and anesthesia was maintained with inhalation of nitrous oxide and continuous i.v. infusion of propofol with caudal block, and his clinical course was uneventful.
Oue
Tomoyo
T
Department of Anesthesia, Kagawa Rosai Hospital, Marugame 763-0013.
Nishimoto
Masahiko
M
Kitaura
Michio
M
Samuta
Takeshi
T
Toda
Narushi
N
Koyama
Yusuke
Y
Inoue
Kazuyoshi
K
Danura
Tetsuya
T
D000768:Anesthesia, General / Q000379:methods; D018685:Anesthetics, Inhalation; D002648:Child; D000075202:Contraindications; D006801:Humans; D017214:Laryngeal Masks; D035002:Lower Extremity; D008297:Male; D008305:Malignant Hyperthermia / Q000209:etiology / Q000517:prevention & control; D009609:Nitrous Oxide; D010009:Osteochondrodysplasias / Q000601:surgery*; D015742:Propofol; D013710:Tendons / Q000601:surgery
D018685:Anesthetics, Inhalation; D009609:Nitrous Oxide; D015742:Propofol