Chediak-Higashi syndrome in the intensive care unit.
Chediak-Higashi Syndrome is a rare autosomal recessive disease characterized by recurrent infections, giant cytoplasmic granules and oculocutaneous albinism. We describe the clinical and laboratory findings of a patient with Chediak-Higashi syndrome who was diagnosed and treated in the intensive care unit because of bleeding tendency after surgery.
Department of Anaesthesiology, Cerrahpasa Medical School, Istanbul University, Sadi Sun ICU, Istanbul, Turkey. odemirkiran@superonline.com
Oktay
O
Demirkiran
Tughan
T
Utku
Seval
S
Urkmez
Yalim
Y
Dikmen
D000151:Acinetobacter Infections / Q000175:diagnosis / Q000188:drug therapy; D000900:Anti-Bacterial Agents / Q000627:therapeutic use; D001803:Blood Transfusion / Q000379:methods; D002609:Chediak-Higashi Syndrome / Q000175:diagnosis*; D002648:Child; D003422:Critical Care / Q000379:methods*; D005260:Female; D006400:Hematocrit / Q000379:methods; D006801:Humans; D007362:Intensive Care Units; D007442:Intubation, Intratracheal / Q000379:methods; D008991:Monitoring, Physiologic / Q000379:methods; D019647:Oral Surgical Procedures / Q000009:adverse effects; D010949:Plasma; D019106:Postoperative Hemorrhage / Q000628:therapy; D011552:Pseudomonas Infections / Q000175:diagnosis / Q000188:drug therapy; D012121:Respiration, Artificial / Q000379:methods
D000900:Anti-Bacterial Agents