Anesthesia in Beckwith-Wiedemann syndrome.
Anesthetic management of a 3-month-old boy with Beckwith-Wiedemann syndrome for bronchoscopy is reported. Management may be complicated by a difficult airway, congenital heart disease, and hypoglycemia. We did not have difficulty in airway management either with tracheal intubation or rigid bronchoscopy, but we could not extubate the baby because of tracheomalacia.
Celiker
V
V
Department of Anaesthesiology and Reanimation, Hacettepe University Faculty of Medicine, Ankara, Turkey.
Basgul
E
E
Karagoz
A H
AH
D000768:Anesthesia, General / Q000379:methods*; D018685:Anesthetics, Inhalation / Q000627:therapeutic use; D018686:Anesthetics, Intravenous / Q000627:therapeutic use; D001506:Beckwith-Wiedemann Syndrome / Q000601:surgery*; D001999:Bronchoscopy / Q000379:methods; D005283:Fentanyl / Q000627:therapeutic use; D006801:Humans; D007223:Infant; D007442:Intubation, Intratracheal / Q000009:adverse effects / Q000379:methods; D008297:Male; D008738:Methyl Ethers / Q000627:therapeutic use; D016343:Monitoring, Intraoperative / Q000379:methods; D009467:Neuromuscular Depolarizing Agents / Q000627:therapeutic use; D015742:Propofol / Q000627:therapeutic use; D000077149:Sevoflurane; D013390:Succinylcholine / Q000627:therapeutic use; D014132:Trachea / Q000002:abnormalities; D014133:Tracheal Diseases / Q000150:complications / Q000175:diagnosis / Q000503:physiopathology*
D018685:Anesthetics, Inhalation; D018686:Anesthetics, Intravenous; D008738:Methyl Ethers; D009467:Neuromuscular Depolarizing Agents; D000077149:Sevoflurane; D013390:Succinylcholine; D005283:Fentanyl; D015742:Propofol