Combined general and epidural anesthesia for a child with alagille syndrome: a case report.
Alagille syndrome (syndromic paucity of interlobular bile ducts) is the most common form of familial intrahepatic cholestasis. We describe the perioperative management of a pediatric patient with Alagille syndrome undergoing ileal exclusion and the specific issues associated with epidural anesthesia with this syndrome.
Subramaniam
Kathirvel
K
Department of Anesthesiology and Critical Care Medicine, Beth Israel Deaconess Medical Center, Harvard Medical School, Boston, MA 02115, USA.
Myers
Laura B
LB
D016738:Alagille Syndrome / Q000601:surgery*; D000767:Anesthesia, Epidural / Q000379:methods*; D000768:Anesthesia, General / Q000379:methods*; D019162:Anesthetics, Combined / Q000627:therapeutic use*; D018685:Anesthetics, Inhalation / Q000627:therapeutic use; D018686:Anesthetics, Intravenous / Q000627:therapeutic use; D000779:Anesthetics, Local / Q000627:therapeutic use; D001279:Atracurium / Q000031:analogs & derivatives* / Q000627:therapeutic use; D002045:Bupivacaine / Q000627:therapeutic use; D002675:Child, Preschool; D003125:Colostomy / Q000379:methods; D005283:Fentanyl / Q000627:therapeutic use*; D006801:Humans; D007082:Ileum / Q000601:surgery; D007442:Intubation, Intratracheal / Q000379:methods; D007530:Isoflurane / Q000627:therapeutic use; D008297:Male; D008874:Midazolam / Q000627:therapeutic use; D009466:Neuromuscular Blocking Agents / Q000627:therapeutic use; D013874:Thiopental / Q000627:therapeutic use
D019162:Anesthetics, Combined; D018685:Anesthetics, Inhalation; D018686:Anesthetics, Intravenous; D000779:Anesthetics, Local; D009466:Neuromuscular Blocking Agents; D001279:Atracurium; D007530:Isoflurane; D013874:Thiopental; C101584:cisatracurium; D008874:Midazolam; D005283:Fentanyl; D002045:Bupivacaine