Combined general and epidural anesthesia for a child with alagille syndrome: a case report.
Alagille syndrome (syndromic paucity of interlobular bile ducts) is the most common form of familial intrahepatic cholestasis. We describe the perioperative management of a pediatric patient with Alagille syndrome undergoing ileal exclusion and the specific issues associated with epidural anesthesia with this syndrome.
Department of Anesthesiology and Critical Care Medicine, Beth Israel Deaconess Medical Center, Harvard Medical School, Boston, MA 02115, USA.
Kathirvel
K
Subramaniam
Laura B
LB
Myers
D016738:Alagille Syndrome / Q000601:surgery*; D000767:Anesthesia, Epidural / Q000379:methods*; D000768:Anesthesia, General / Q000379:methods*; D019162:Anesthetics, Combined / Q000627:therapeutic use*; D018685:Anesthetics, Inhalation / Q000627:therapeutic use; D018686:Anesthetics, Intravenous / Q000627:therapeutic use; D000779:Anesthetics, Local / Q000627:therapeutic use; D001279:Atracurium / Q000031:analogs & derivatives* / Q000627:therapeutic use; D002045:Bupivacaine / Q000627:therapeutic use; D002675:Child, Preschool; D003125:Colostomy / Q000379:methods; D005283:Fentanyl / Q000627:therapeutic use*; D006801:Humans; D007082:Ileum / Q000601:surgery; D007442:Intubation, Intratracheal / Q000379:methods; D007530:Isoflurane / Q000627:therapeutic use; D008297:Male; D008874:Midazolam / Q000627:therapeutic use; D009466:Neuromuscular Blocking Agents / Q000627:therapeutic use; D013874:Thiopental / Q000627:therapeutic use
D019162:Anesthetics, Combined; D018685:Anesthetics, Inhalation; D018686:Anesthetics, Intravenous; D000779:Anesthetics, Local; D009466:Neuromuscular Blocking Agents; D001279:Atracurium; D007530:Isoflurane; D013874:Thiopental; C101584:cisatracurium; D008874:Midazolam; D005283:Fentanyl; D002045:Bupivacaine