Malignant PEComa of the skull base.
Perivascular epithelioid cell tumors (PEComas) are rare, usually benign lesions comprising a family of neoplasms including angiomyolipoma, lymphangioleiomyomatosis, clear cell "sugar" tumors, and clear cell myomelanocytic tumors. This report describes an apparent case of a malignant PEComa of the skull base in a 49-year-old woman, a previously undescribed location for this lesion.
Department of Pathology, Stanford University Medical Center, Stanford, CA 94305, USA. nlehman@stanford.edu
Norman L
NL
Lehman
D005260:Female; D006801:Humans; D008875:Middle Aged; D009375:Neoplasms, Glandular and Epithelial / Q000473:pathology*; D019292:Skull Base Neoplasms / Q000473:pathology*