FAP with concurrent duodenal adenomatous polyposis and carcinoid tumor.
We report a patient with familial adenomatous polyposis (FAP) who developed duodenal adenomatosis with high-grade dysplasia and a periampullary carcinoid tumor several years after total colectomy. Only two prior case reports exist revealing carcinoid tumors in association with FAP. No genetic basis exists explaining the link between FAP and carcinoid tumors. However, the presence of two rare entities in the same patient might suggest an association and further research may be indicated.
Camp
E Ramsay
ER
Department of Surgery, University of Florida College of Medicine, Gainesville, Florida 32610, USA.
Hochwald
Steven N
SN
Liu
Chen
C
D000208:Acute Disease; D000236:Adenoma / Q000473:pathology* / Q000601:surgery; D011125:Adenomatous Polyposis Coli / Q000235:genetics / Q000473:pathology* / Q000601:surgery; D000328:Adult; D002276:Carcinoid Tumor / Q000473:pathology* / Q000601:surgery; D003082:Colectomy; D004379:Duodenal Neoplasms / Q000473:pathology* / Q000601:surgery; D004384:Duodenoscopy; D004945:Esophagoscopy; D006801:Humans; D007417:Intestinal Polyps / Q000473:pathology* / Q000601:surgery; D008297:Male; D010180:Pancreatectomy; D010195:Pancreatitis / Q000209:etiology / Q000601:surgery