title: Anesthetic management of a difficult airway in a patient with epidermolysis bullosa: a case report.
abstract: Epidermolysis bullosa is an inherited skin disease that leads to an array of medical problems. Patients are susceptible to blistering and scar formation following even minor trauma. These patients may present with scarring, limiting the range of motion of their temporal mandibular joint. This case report describes a 15-year-old patient with epidermolysis bullosa presenting for contracture release, with a difficult airway.
authors.affiliation: St Christopher's Hospital for Children, Philadelphia, PA, USA.
authors.forename: Kelly L
authors.initials: KL
authors.lastname: Crowley
authors.forename: Yuri O
authors.initials: YO
authors.lastname: Shevchenko
mesh_terms: D000293:Adolescent; D000769:Anesthesia, Inhalation / Q000379:methods* / Q000451:nursing; D016292:Procedural Sedation / Q000379:methods / Q000451:nursing; D003286:Contracture / Q000209:etiology / Q000601:surgery*; D004820:Epidermolysis Bullosa / Q000150:complications*; D005336:Fiber Optic Technology / Q000379:methods; D006227:Hand Deformities, Acquired / Q000209:etiology / Q000601:surgery*; D006801:Humans; D007430:Intraoperative Care / Q000379:methods / Q000451:nursing; D007442:Intubation, Intratracheal / Q000295:instrumentation / Q000379:methods* / Q000451:nursing; D008297:Male; D009719:Nurse Anesthetists; D009730:Nursing Assessment