[Pityriasis rubra pilaris].
Pityriasis rubra pilaris (PRP) is a rare papulosquamous disease with typical onset during the first and fifth decades. The skin disorder normally starts on the scalp and spreads caudally within a few weeks. It often results in a generalized erythroderma with sharply demarcated islands of sparing ("nappes claires"). A 65-year-old patient with severe PRP showed good clinial improvement after 8 months of treatment when treated with acitretin in combination with phototherapy and systemic gluocorticosteroids.
Artik
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Hautklinik der Heinrich-Heine-Universität, Düsseldorf.
Kuhn
A
A
Neumann
N J
NJ
Ruzicka
T
T
Megahed
M
M
D000368:Aged; D001706:Biopsy; D003131:Combined Modality Therapy; D003937:Diagnosis, Differential; D005260:Female; D005938:Glucocorticoids / Q000627:therapeutic use; D006801:Humans; D007645:Keratoderma, Palmoplantar / Q000175:diagnosis / Q000473:pathology / Q000628:therapy; D011701:PUVA Therapy; D010916:Pityriasis Rubra Pilaris / Q000175:diagnosis* / Q000473:pathology / Q000628:therapy; D012867:Skin / Q000473:pathology; D014464:Ultrasonic Therapy
D005938:Glucocorticoids
Pityriasis rubra pilaris.