Congenital adrenocortical adenoma: case report and review of literature.
Congenital ardrenocortical neoplasms are exceedingly rare. Our review of the medical literature revealed 23 reported cases of adrenocortical neoplasm including this one. Eighteen of these cases were adrenocortical carcinoma and four were grouped as adrenocortical tumor. We have not found any reported case with a histological diagnosis of a congenital adrenocortical adenoma. We present this case of a congenital adrenocortical neoplasm with histological findings consistent with an adrenocortical adenoma in a premature infant aged 27 weeks and 4 days who had a prenatal sonogram showing a cystic right abdominal mass and a physical examination demonstrating a palpable mass.
Sarwar
Zahir U
ZU
Department of Pediatric Radiology, Children's Hospital Boston, 300 Longwood Avenue, Boston, MA 02115, USA. zahir88@comcast.net
Ward
Valerie L
VL
Mooney
David P
DP
Testa
Sylvia
S
Taylor
George A
GA
D000306:Adrenal Cortex Neoplasms / Q000151:congenital* / Q000175:diagnosis* / Q000000981:diagnostic imaging; D018246:Adrenocortical Adenoma / Q000151:congenital* / Q000175:diagnosis* / Q000000981:diagnostic imaging; D018268:Adrenocortical Carcinoma / Q000151:congenital / Q000175:diagnosis; D003937:Diagnosis, Differential; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D018615:Ultrasonography, Doppler, Color