Method for measurement of peroxisomal very-long-chain fatty acid beta-oxidation in human skin fibroblasts using stable-isotope-labeled tetracosanoic acid.
Kemp
Stephan
S
University of Amsterdam, Academic Medical Center, Department of Pediatrics/Emma Children's Hospital, Laboratory for Genetic Metabolic Diseases, The Netherlands. s.kemp@amc.uva.nl
Valianpour
Fredoen
F
Mooyer
Petra A W
PA
Kulik
Willem
W
Wanders
Ronald J A
RJ
D000326:Adrenoleukodystrophy / Q000378:metabolism; D003903:Deuterium; D005227:Fatty Acids / Q000378:metabolism*; D005240:Feasibility Studies; D005347:Fibroblasts / Q000378:metabolism* / Q000648:ultrastructure; D006801:Humans; D007553:Isotope Labeling; D010084:Oxidation-Reduction; D020675:Peroxisomes / Q000378:metabolism*; D012867:Skin / Q000166:cytology / Q000378:metabolism*; D021241:Spectrometry, Mass, Electrospray Ionization
D005227:Fatty Acids; D003903:Deuterium; C010210:lignoceric acid