[Poems syndrome. Report of one case].
Poems syndrome (polyneuropathy, organomegaly, endocrine abnormality, M-protein, plasma cell dyscrasia, and skin lesions) is a plasma cell dyscrasia whose pathogenesis is unknown. We report a 60 years old woman that presented a tetraparesis caused by a sensitive motor polyneuropathy. The subsequent work up revealed an IgA type monoclonal gammopathy, hepatomegaly, hyperestrogenism, primary adrenal failure, hypothyroidism, hyperpigmentation and erythematous lesions in the skin and ankle edema. The patient is being treated with prednisone 0.5 mg/kg and levothyroxine 100 microg/day, with partial remission of her symptoms.
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Departamento Medicina Interna, Facultad de Medicina, Universidad de Concepción.
Quevedo
Iván
I
D000893:Anti-Inflammatory Agents / Q000627:therapeutic use; D005260:Female; D006801:Humans; D007070:Immunoglobulin A / Q000032:analysis; D008875:Middle Aged; D016878:POEMS Syndrome / Q000175:diagnosis* / Q000188:drug therapy; D010265:Paraproteinemias / Q000175:diagnosis / Q000188:drug therapy; D011241:Prednisone / Q000627:therapeutic use
D000893:Anti-Inflammatory Agents; D007070:Immunoglobulin A; D011241:Prednisone
Síndrome de Poems: caso clínico.