Bone marrow transplantation in young aspartylglucosaminuria mice: improved clearance of lysosomal storage in brain by using wild type as compared to heterozygote donors.
Laine
M
M
Ahtiainen
L
L
Rapola
J
J
Richter
J
J
Jalanko
A
A
D000818:Animals; D001227:Aspartylglucosylaminase / Q000652:urine*; D016026:Bone Marrow Transplantation; D001921:Brain / Q000378:metabolism* / Q000473:pathology; D006579:Heterozygote; D020140:Lysosomal Storage Diseases, Nervous System / Q000473:pathology / Q000628:therapy* / Q000652:urine; D008247:Lysosomes / Q000378:metabolism* / Q000473:pathology; D051379:Mice
D001227:Aspartylglucosylaminase