Deforming chondrosarcoma of the fingers secondary to a long-term enchondromatosis of 28 years.
Enchondromatosis of the hand in the context of the Oilier disease is an infrequent pathologie associated with a high rate of malignancy. In this work, we present a case with multiple enchondromas affecting mainly the fourth and fifth rays of the hand, and with multiple ipsilateral lesions in the foot, sacroiliac joint and iliac bone. This patient is, in addition, an unusual case for a long-term progression (28 years), serious deforming appearance and for the double malignant degeneration to chondrosarcoma of the affected fingers. Clinical features, tumor factors, criterion of diagnosis and prognosis, surgical strategy and follow-up evaluation are analysed, as well as a review of the literature.
Martínez Villén
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Department of Traumatology and Orthopedic Surgery, Section of Hand Surgery and Microsurgery, Miguel Servet University Hospital of Zaragoza, P Isabel la Católica, 1-3, Zaragoza 50009, Spain. gmarvil@terra.es
Hernández Rossi
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Martínez Tello
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Herrera Rodríguez
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D001859:Bone Neoplasms / Q000209:etiology* / Q000473:pathology* / Q000601:surgery; D002813:Chondrosarcoma / Q000209:etiology* / Q000473:pathology* / Q000601:surgery; D018450:Disease Progression; D004687:Enchondromatosis / Q000150:complications*; D005260:Female; D006227:Hand Deformities, Acquired / Q000473:pathology* / Q000601:surgery; D006801:Humans; D008875:Middle Aged; D011379:Prognosis; D013997:Time Factors