Giant malignant peripheral nerve sheath tumor of the neck in a patient with neurofibromatosis-1.
Sixteen-year-old mentally retarded male patient presented with a giant malignant peripheral nerve sheath tumor (MPNST) on his neck. Surgery was the chosen method of treatment by the help of a neurosurgeon for dissecting the mass from the nerves of the brachial plexus and a thoracic surgeon for removing the mass from the superior mediastinum. A mass of 2 kg in weight was excised gross totally. He had an early recurrence in the second month of the follow-up period despite postoperative irradiation therapy. He died of his disease due to the compression of vena cava superior.
Department Of Otolaryngology-Head and Neck Surgery, Faculty of Medicine, Hacettepe University, Ankara 06100, Turkey.
Ozgül
O
Topal
Taner
T
Yilmaz
Oğuz
O
Oğretmenoğlu
D000293:Adolescent; D001917:Brachial Plexus / Q000473:pathology* / Q000601:surgery; D017809:Fatal Outcome; D006258:Head and Neck Neoplasms / Q000175:diagnosis* / Q000601:surgery; D006801:Humans; D008297:Male; D008479:Mediastinal Neoplasms / Q000175:diagnosis* / Q000601:surgery; D009364:Neoplasm Recurrence, Local / Q000175:diagnosis; D018317:Nerve Sheath Neoplasms / Q000175:diagnosis* / Q000601:surgery; D009456:Neurofibromatosis 1 / Q000150:complications*