[Long-term follow-up of a case of eyelid myoclonia with absences].
We reported a case of eyelid myoclonia with absences treated for 10 years. Seizures of eyelid myoclonia accompanied by absence, precipitated by sunlight, began at the age of 4 years and disappeared at the age of 11 years. Non-convulsive status epilepticus, occurring shortly after awakening, began at the age of 10 years and have occurred intermittently until the age of 18 years. While generalized EEG abnormalities disappeared after initiation of treatment, the patient still had occipital spikes on interictal EEG at the age of 18 years, suggesting occipital hyperexcitability as the basis of photosensitivity. Along with poor drug compliance due to her living apart from her parents, it was difficult to completely suppress non-convulsive status epilepticus, posing serious concern in her adult life.
Department of Pediatrics, Ehime Prefecture Niihama Hospital, Niihama, Ehime. hirwaka@shikoku.ne.jp
Hiroyuki
H
Wakamoto
Masatoshi
M
Hayashi
Hideo
H
Nagao
D000293:Adolescent; D002998:Clonazepam / Q000627:therapeutic use; D004359:Drug Therapy, Combination; D004569:Electroencephalography; D005013:Ethosuximide / Q000627:therapeutic use; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D009207:Myoclonus / Q000175:diagnosis / Q000188:drug therapy / Q000209:etiology / Q000503:physiopathology*; D010349:Patient Compliance; D020795:Photophobia / Q000150:complications; D013997:Time Factors; D014635:Valproic Acid / Q000627:therapeutic use
D002998:Clonazepam; D005013:Ethosuximide; D014635:Valproic Acid