title: Anesthetic management of a child with congenital central hypoventilation syndrome (CCHS, Ondine's curse) for dental treatment.
abstract: Congenital Central Hypoventilation Syndrome (CCHS, also known as Ondine's Curse) is a rare syndrome characterized by apnea, cyanosis, and hypotonia. A 4-year-old, 90-cm, 12-kg girl with CCHS, mental retardation (MR), and Hischsprung's disease (HD) was treated under general anesthesia. Intravenous drugs were not used, but sevoflurane, a volatile anesthetic, was used. As a result, the recovery time from the end of the operation to returning to the ward was very short, only 18 minutes. There was no trouble during the perioperative period. We safely performed general anesthesia and dental treatment for a girl who had CCHS with HD and MR.
authors.affiliation: Department of Anesthesiology, Nihon University School of Dentistry at Matsudo, Chiba, Japan. ishibash@mascat.nihon-u.ac.jp
authors.forename: Hajime
authors.initials: H
authors.lastname: Ishibashi
authors.forename: Koji
authors.initials: K
authors.lastname: Umezawa
authors.forename: Sachiyo
authors.initials: S
authors.lastname: Hayashi
authors.forename: Koh
authors.initials: K
authors.lastname: Shibutani
mesh_terms: D000766:Anesthesia, Dental / Q000379:methods*; D000768:Anesthesia, General / Q000379:methods; D018685:Anesthetics, Inhalation / Q000008:administration & dosage; D002675:Child, Preschool; D017742:Dental Care for Chronically Ill; D005260:Female; D006627:Hirschsprung Disease / Q000150:complications; D006801:Humans; D008607:Intellectual Disability / Q000150:complications; D008738:Methyl Ethers / Q000008:administration & dosage; D009609:Nitrous Oxide / Q000008:administration & dosage; D000077149:Sevoflurane; D020182:Sleep Apnea, Central / Q000150:complications / Q000151:congenital*; D013577:Syndrome
chemical_list: D018685:Anesthetics, Inhalation; D008738:Methyl Ethers; D000077149:Sevoflurane; D009609:Nitrous Oxide