title: [Intra-abdominal desmoplastic small round cell tumor. A case report].
abstract: Intra-abdominal desmoplastic small round cell tumor is an extremely rare and aggressive neoplasm that predominantly occurs in young adult men; it has an uncertain histogenesis, and predominant or exclusive intra-abdominal localisation without visceral origin involvement. This tumor is characterized by its distinct morphology and its multiphenotypic differentiation. We report a case of an intra-abdominal desmoplastic round cell tumor in a 24 years old woman. In the light of this case, the clinical morphological immunohistochemical and molecular of this rare desease are revewed.
authors.affiliation: Service d'anatomie pathologique, CHU Ibn Sina Rabat, Maroc.
authors.forename: M
authors.initials: M
authors.lastname: Maliki
authors.forename: N
authors.initials: N
authors.lastname: Mahassini
authors.forename: F
authors.initials: F
authors.lastname: Zouaidia
authors.forename: Z
authors.initials: Z
authors.lastname: Bernoussi
authors.forename: F
authors.initials: F
authors.lastname: Mansouri
authors.forename: A
authors.initials: A
authors.lastname: El Hachimi
mesh_terms: D000008:Abdominal Neoplasms / Q000473:pathology*; D000328:Adult; D005260:Female; D006801:Humans