[Primary multicentric cutaneous epithelioid angiosarcoma of the hand. Case report and review of the literature].
METHODS
The case of a primary multicentric cutaneous epithelioid angiosarcoma is described. A 39-year-old female patient presented with a tumor on the left distal forearm and the fourth finger of the left hand. Partial amputation of the left hand and local excision of the tumor on the left forearm were performed. For the next three years the patient was free of local or systemic recurrence. After this time period, a left shoulder exarticulation had to be performed because of tumor recurrence in the left axilla. The patient died 64 months after diagnosis.


CONCLUSIONS
Cutaneous epithelioid angiosarcoma is a highly malignant tumor which has only been described once on the hand. The treatment primarily is a surgical one. If possible, the function of the extremity should be preserved as long as possible.
Bock
P
P
Abteilung für Orthopädie, Donauspital Wien, Wien, Osterreich. peter.bock@wienkav.at.
Jahn
R
R
Piza-Katzer
H
H
D000328:Adult; D001365:Axilla / Q000601:surgery; D014408:Biomarkers, Tumor / Q000032:analysis; D001940:Breast / Q000473:pathology; D004188:Disarticulation; D017809:Fatal Outcome; D005260:Female; D005385:Fingers / Q000601:surgery*; D005500:Follow-Up Studies; D005542:Forearm / Q000601:surgery*; D006801:Humans; D008408:Mastectomy; D009361:Neoplasm Invasiveness / Q000473:pathology; D009364:Neoplasm Recurrence, Local / Q000473:pathology / Q000601:surgery; D009378:Neoplasms, Multiple Primary / Q000473:pathology / Q000601:surgery*; D012086:Reoperation; D012878:Skin Neoplasms / Q000473:pathology / Q000601:surgery*
D014408:Biomarkers, Tumor