Fibrosing mediastinitis causing rapidly progressive dyspnea, pulmonary edema and death in a 16 yr old male.
Idiopathic fibrosing mediastinitis is a rare entity involving more severely the more compliant structures within the mediastinum. In this report a rare case of simultaneous involvement of both the superior vena cava (SVC) and pulmonary veins is described in a 16--year old male with progressive dyspnea on exertion, cough and a three months' history of blood--tinged sputum. Physical examination and imaging studies revealed signs of pulmonary venous hypertension (PVH) and SVC stenosis. Fibrosing mediastinitis was confirmed by multiple biopsy samples.
Malagari
K
K
2nd Department of Radiology, Athens Medical School, National and Capodistrian University of Athens, Evgenidion Hospital, 20 Athens, Greece. kmalag@acn.gr
Papiris
S
S
D000293:Adolescent; D004417:Dyspnea / Q000209:etiology*; D017809:Fatal Outcome; D005355:Fibrosis; D006801:Humans; D006976:Hypertension, Pulmonary / Q000209:etiology; D008297:Male; D008480:Mediastinitis / Q000150:complications*; D011654:Pulmonary Edema / Q000000981:diagnostic imaging / Q000209:etiology*; D013479:Superior Vena Cava Syndrome / Q000209:etiology; D014057:Tomography, X-Ray Computed