[Intra-abdominal desmoplastic small round cell tumor. A case report].
Intra-abdominal desmoplastic small round cell tumor is an extremely rare and aggressive neoplasm that predominantly occurs in young adult men; it has an uncertain histogenesis, and predominant or exclusive intra-abdominal localisation without visceral origin involvement. This tumor is characterized by its distinct morphology and its multiphenotypic differentiation. We report a case of an intra-abdominal desmoplastic round cell tumor in a 24 years old woman. In the light of this case, the clinical morphological immunohistochemical and molecular of this rare desease are revewed.
Maliki
M
M
Service d'anatomie pathologique, CHU Ibn Sina Rabat, Maroc.
Mahassini
N
N
Zouaidia
F
F
Bernoussi
Z
Z
Mansouri
F
F
El Hachimi
A
A
D000008:Abdominal Neoplasms / Q000473:pathology*; D000328:Adult; D005260:Female; D006801:Humans