Aortic valvar atresia, interrupted aortic arch, and quadricuspid pulmonary valve: a rare combination.
Aortic atresia and interrupted aortic arch is a rare cardiac combination. Review of the literature revealed nine cases. We present two patients with this combination and the additional finding of quadricuspid pulmonary valves, one of which was severely stenotic. In the latter patient, an aortopulmonary window was present. The other had a unique blood supply to the brachiocephalic arteries and ascending aorta from systemic collateral arteries. To the best of our knowledge, the association of a quadricuspid pulmonary valve with this combination has not been previously reported.
Yew
G
G
Paediatric and Congenital Cardiac Services, Green Lane Hospital, Auckland, New Zealand.
Coleman
D
D
Calder
L
L
D000015:Abnormalities, Multiple; D001013:Aorta, Thoracic / Q000002:abnormalities*; D001018:Aortic Diseases / Q000151:congenital / Q000175:diagnosis* / Q000601:surgery; D001021:Aortic Valve / Q000002:abnormalities*; D006348:Cardiac Surgical Procedures; D002932:Cineangiography; D017809:Fatal Outcome; D006330:Heart Defects, Congenital / Q000175:diagnosis* / Q000601:surgery; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D008297:Male; D011664:Pulmonary Valve / Q000002:abnormalities*; D014656:Vascular Surgical Procedures