Hemophagocytic lymphohistiocytosis: a rare cause of pancytopenia.
A 36-year-old man with fever and pancytopenia due to Hemophagocytic Lymphohistiocytosis is reported. The patient was started on the HLH-94 based treatment. Two weeks after the initiation of therapy the patient's pancytopenia had resolved and he was discharged to complete treatment as an outpatient. The initial clinical presentation, diagnostic criteria, pathophysiology and treatment will be discussed.
King
Robert S
RS
Department of Medicine, Tripler Army Medical Center, Honolulu, HI 96859, USA. robert.king@haw.tamc.amedd.army.mil
Preston
Glenn G
GG
Berenberg
Jeffrey L
JL
Fraser
Susan L
SL
Gress
Francis M
FM
D000328:Adult; D003937:Diagnosis, Differential; D015616:Histiocytosis, Non-Langerhans-Cell / Q000150:complications / Q000175:diagnosis* / Q000473:pathology; D006801:Humans; D008297:Male; D010198:Pancytopenia / Q000175:diagnosis* / Q000209:etiology / Q000473:pathology; D035583:Rare Diseases / Q000175:diagnosis