[Orbit xanthogranulomatosis. Erdheim-Chester disease].
METHODS
A patient was studied because of upper lid bilateral edema and xanthelasmae-like lesions after three years of evolution. During the ophthalmologic examination orange-yellowish lesions and two symmetrical tumours were observed on the temporal part of both upper lids. Corticoid-therapy was undertaken which reduced the size of the tumours, however the size increased again after the discontinuation of treatment. A biopsy was performed and lid xanthogranulomatosis was diagnosed. Other systemic examinations were normal.


CONCLUSIONS
Erdheim-Chester disease is a xanthogranulomatosis that can affect ocular and periorbital structures. Combination of xanthelasmae-like lesions and bilateral orbital masses should make us consider this process and try to locate any associated systemic conditions.
Rozas Reyes
P
P
Hospital Universitario Central de Asturias, Spain. prozas@telecable.es
Señaris González
A
A
González Rodríguez
C M
CM
D000328:Adult; D031249:Erdheim-Chester Disease / Q000175:diagnosis / Q000188:drug therapy; D005260:Female; D006801:Humans; D009916:Orbital Diseases / Q000175:diagnosis / Q000188:drug therapy