Subarcuate venous malformation causing audio-vestibular symptoms similar to those in superior canal dehiscence syndrome.
OBJECTIVE
To present a patient with symptoms similar to those of superior canal dehiscence syndrome due to another cause.


METHODS
Case report.


METHODS
University hospital, tertiary referral center.


METHODS
The 65-year-old woman had suffered for 4 years from hearing loss, tinnitus, and pressure-induced vertigo.


METHODS
Audio-vestibular testing, high-resolution computed tomography, and magnetic resonance angiography.


METHODS
The superior canal dehiscence syndrome is caused by failure of normal postnatal bone development in the middle cranial fossa leading to absence of bone at the most superior part of the superior semicircular canal. The typical features for this syndrome are sound and pressure-induced vertigo with torsional eye movements, pulse synchronous tinnitus and apparent conductive hearing loss in spite of normal middle ear function. We present a patient with very similar symptoms and findings, who instead had a superior canal dehiscence close to the common crus. Neuroradiologic findings suggested that the dehiscence was related to a venous malformation.


CONCLUSIONS
Symptoms and findings suggesting superior canal dehiscence syndrome can have a different cause.
Brantberg
Krister
K
Departments of Audiology, Karolinska Hospital, St. Eriks Eye Hospital, Stockholm, Sweden. krister.brantberg@ks.se
Greitz
Dan
D
Pansell
Tony
T
D000368:Aged; D001301:Audiometry, Pure-Tone; D035301:Cranial Fossa, Middle / Q000098:blood supply / Q000473:pathology; D004584:Electronystagmography; D019054:Evoked Potentials, Motor; D005133:Eye Movements; D005260:Female; D034381:Hearing Loss / Q000209:etiology* / Q000503:physiopathology; D006801:Humans; D007427:Intracranial Pressure; D009759:Nystagmus, Pathologic / Q000209:etiology* / Q000503:physiopathology; D012665:Semicircular Canals / Q000098:blood supply / Q000000981:diagnostic imaging / Q000473:pathology* / Q000503:physiopathology; D013577:Syndrome; D014012:Tinnitus / Q000209:etiology* / Q000503:physiopathology; D014057:Tomography, X-Ray Computed; D014636:Valsalva Maneuver; D014680:Veins / Q000002:abnormalities; D014717:Vertigo / Q000209:etiology* / Q000503:physiopathology