Emergent bullectomy for acute respiratory failure in Ehlers-Danlos syndrome.
A 49-year-old man with Ehlers-Danlos syndrome developed acute respiratory failure requiring mechanical ventilation. Chest computed tomography demonstrated giant right bulla extending into the contralateral hemithorax with mediastinal shift. Surgical bullectomy with pleurodesis relieved tension effects and allowed weaning.
Safdar
Zeenat
Z
Division of Pulmonary-Critical Care Medicine, Columbia University of Physicians & Surgeons, St. Luke's-Roosevelt Hospital Center, 432 W. 58th Street, Rm 520, New York, NY 10019, USA. zsafdar@chpnet.org.
O'Sullivan
Mary
M
Shapiro
Janet M
JM
D000208:Acute Disease; D000328:Adult; D001706:Biopsy; D003371:Cough / Q000209:etiology; D003422:Critical Care / Q000379:methods; D004417:Dyspnea / Q000209:etiology; D004535:Ehlers-Danlos Syndrome / Q000150:complications*; D004630:Emergencies; D005334:Fever / Q000209:etiology; D006801:Humans; D008297:Male; D011013:Pneumonectomy; D011175:Positive-Pressure Respiration / Q000009:adverse effects; D011656:Pulmonary Emphysema / Q000175:diagnosis / Q000209:etiology* / Q000601:surgery*; D012131:Respiratory Insufficiency / Q000175:diagnosis / Q000209:etiology* / Q000601:surgery*; D012307:Risk Factors; D012907:Smoking / Q000009:adverse effects; D014057:Tomography, X-Ray Computed; D016896:Treatment Outcome