title: Hemihypertrophy and primary small intestinal lymphangiectasia in incontinentia pigmenti achromians.
abstract: A rare occurrence of primary small intestinal lymphangiectasia in an 8-year-old girl with incontinentia pigmenti achromians is reported. In addition, she had right sided hemihypertrophy. Though intestinal lymphangiectasia is known to have a few syndromic associations, its co-existence in a child with incontinentia pigmenti achromians has not yet been reported in the literature. Hemihypertrophy is also extremely rare in the latter and only very few instances of an association between the two have been documented previously.
authors.affiliation: Departments of Pediatrics, Medical College, Calicut, Kerala, India. saif_gem@hotmail.com.
authors.forename: A
authors.initials: A
authors.lastname: Riyaz
authors.forename: Najeeba
authors.initials: N
authors.lastname: Riyaz
authors.forename: P
authors.initials: P
authors.lastname: Anoop
authors.forename: B
authors.initials: B
authors.lastname: Chandni
authors.forename: K
authors.initials: K
authors.lastname: Noushad
mesh_terms: D001824:Body Constitution; D002648:Child; D005260:Female; D006801:Humans; D006984:Hypertrophy / Q000150:complications*; D007421:Intestine, Small / Q000473:pathology; D008201:Lymphangiectasis, Intestinal / Q000150:complications* / Q000473:pathology; D010859:Pigmentation Disorders / Q000150:complications* / Q000473:pathology