[Shone's anomaly Fallbericht und Hintergrund].
Shone's anomaly was first described in 1963 as a developmental complex of four potentially obstructive cardiac lesions including a supravalvular fibrous mitral ring, deformity of the mitral and/or subvalvular apparatus, subvalvular aortic stenosis and coarctation of the aorta. While paediatric patients with Shone's anomaly have been reported in the literature, only a few adult patients presenting with this anomaly have been described in the perioperative period. However, patients with an undiagnosed, incomplete form of Shone's anomaly might occasionally present for non-cardiac surgery as adults. In this case report we describe the anaesthetic management of an adult patient scheduled for a non-cardiac operation, who suffered from Shone's anomaly that was unrecognised prior to the operation.
Derrer
F
F
Departement Anästhesie, Universitätsspital, Basel.
Gisin
S
S
Linka
A
A
Kindler
C H
CH
D000758:Anesthesia; D001017:Aortic Coarctation / Q000000981:diagnostic imaging / Q000473:pathology*; D001020:Aortic Stenosis, Subvalvular / Q000000981:diagnostic imaging / Q000473:pathology*; D005260:Female; D006349:Heart Valve Diseases / Q000000981:diagnostic imaging / Q000473:pathology*; D006439:Hemodynamics / Q000502:physiology; D006801:Humans; D007044:Hysterectomy; D008875:Middle Aged; D008946:Mitral Valve Stenosis / Q000000981:diagnostic imaging / Q000473:pathology*; D013577:Syndrome; D014463:Ultrasonography