Anesthetic and perioperative management of a patient with Bernard-Soulier syndrome.
We describe a patient with Bernard-Soulier syndrome who underwent emergency laparotomy for intraabdominal bleeding. Presentation of this recent case highlights some of the anesthetic and perioperative implications of the disease. Briefly, perioperative and anesthetic management of patients with Bernard-Soulier syndrome should include platelet transfusions and choice of appropriate anesthetic drugs and techniques. The potential benefit of desmopressin and corticosteroids should be considered. Thrombelastography, if available, is also useful.
Kostopanagiotou
Georgia
G
Department of Anesthesiology, School of Medicine, University of Athens, Athens, Greece. narkado@otenet.gr
Siafaka
Ioanna
I
Sikiotis
Constantinos
C
Smyrniotis
Vassilios
V
D000328:Adult; D000758:Anesthesia / Q000379:methods*; D001606:Bernard-Soulier Syndrome / Q000150:complications*; D003338:Corpus Luteum; D005260:Female; D006465:Hemoperitoneum / Q000209:etiology / Q000601:surgery*; D006801:Humans; D019990:Perioperative Care; D017713:Platelet Transfusion