title: Telangiectasia macularis eruptiva perstans with an associated myeloproliferative disorder.
abstract: Telangiectasia macularis eruptiva perstans (TMEP) is a cutaneous form of mastocytosis. It has been rarely associated with an underlying myeloproliferative disorder. We report the case of a patient, while receiving treatment for thrombocytosis, with both platelet production and function inhibitors presented with TMEP. TMEP is often refractory to therapy; however, our patient responded to treatment with PUVA.
authors.affiliation: Department of Dermatology and Cutaneous Surgery, University of Miami School of Medicine, University of Miami, Miami, FL 33125, USA.
authors.forename: Lucy K
authors.initials: LK
authors.lastname: Martin
authors.forename: Paolo
authors.initials: P
authors.lastname: Romanelli
authors.forename: Yeon Soong
authors.initials: YS
authors.lastname: Ahn
authors.forename: Robert S
authors.initials: RS
authors.lastname: Kirsner
mesh_terms: D005260:Female; D006801:Humans; D007868:Leg Dermatoses / Q000188:drug therapy / Q000209:etiology*; D034701:Mastocytosis, Cutaneous / Q000188:drug therapy / Q000209:etiology*; D008875:Middle Aged; D011701:PUVA Therapy; D011087:Polycythemia Vera / Q000150:complications; D017445:Skin Diseases, Vascular / Q000188:drug therapy / Q000209:etiology*; D013684:Telangiectasis / Q000188:drug therapy / Q000209:etiology*; D013922:Thrombocytosis / Q000150:complications*