title: Anesthetic and perioperative management of a patient with Bernard-Soulier syndrome.
abstract: We describe a patient with Bernard-Soulier syndrome who underwent emergency laparotomy for intraabdominal bleeding. Presentation of this recent case highlights some of the anesthetic and perioperative implications of the disease. Briefly, perioperative and anesthetic management of patients with Bernard-Soulier syndrome should include platelet transfusions and choice of appropriate anesthetic drugs and techniques. The potential benefit of desmopressin and corticosteroids should be considered. Thrombelastography, if available, is also useful.
authors.affiliation: Department of Anesthesiology, School of Medicine, University of Athens, Athens, Greece. narkado@otenet.gr
authors.forename: Georgia
authors.initials: G
authors.lastname: Kostopanagiotou
authors.forename: Ioanna
authors.initials: I
authors.lastname: Siafaka
authors.forename: Constantinos
authors.initials: C
authors.lastname: Sikiotis
authors.forename: Vassilios
authors.initials: V
authors.lastname: Smyrniotis
mesh_terms: D000328:Adult; D000758:Anesthesia / Q000379:methods*; D001606:Bernard-Soulier Syndrome / Q000150:complications*; D003338:Corpus Luteum; D005260:Female; D006465:Hemoperitoneum / Q000209:etiology / Q000601:surgery*; D006801:Humans; D019990:Perioperative Care; D017713:Platelet Transfusion