Telangiectasia macularis eruptiva perstans with an associated myeloproliferative disorder.
Telangiectasia macularis eruptiva perstans (TMEP) is a cutaneous form of mastocytosis. It has been rarely associated with an underlying myeloproliferative disorder. We report the case of a patient, while receiving treatment for thrombocytosis, with both platelet production and function inhibitors presented with TMEP. TMEP is often refractory to therapy; however, our patient responded to treatment with PUVA.
Martin
Lucy K
LK
Department of Dermatology and Cutaneous Surgery, University of Miami School of Medicine, University of Miami, Miami, FL 33125, USA.
Romanelli
Paolo
P
Ahn
Yeon Soong
YS
Kirsner
Robert S
RS
D005260:Female; D006801:Humans; D007868:Leg Dermatoses / Q000188:drug therapy / Q000209:etiology*; D034701:Mastocytosis, Cutaneous / Q000188:drug therapy / Q000209:etiology*; D008875:Middle Aged; D011701:PUVA Therapy; D011087:Polycythemia Vera / Q000150:complications; D017445:Skin Diseases, Vascular / Q000188:drug therapy / Q000209:etiology*; D013684:Telangiectasis / Q000188:drug therapy / Q000209:etiology*; D013922:Thrombocytosis / Q000150:complications*