title: Phakomatosis pigmentovascularis type IIb associated with Sturge-Weber syndrome.
abstract: We describe a 23-month-old child with phakomatosis pigmentovascularis type IIb associated with Sturge-Weber syndrome. Phakomatosis pigmentovascularis type IIb is a rare cutaneous malformation characterized by the simultaneous occurrence of nevus flammeus and melanocytic nevi. A brief review of the literature is presented and classification of this rare disease is discussed.
authors.affiliation: Department of Medicine, King Faisal Specialist Hospital and Research Center, Riyadh 11211, Saudi Arabia.
authors.forename: Ahmad
authors.initials: A
authors.lastname: Al Robaee
authors.forename: Nusrat
authors.initials: N
authors.lastname: Banka
authors.forename: Abdullah
authors.initials: A
authors.lastname: Alfadley
mesh_terms: D001921:Brain / Q000473:pathology; D004569:Electroencephalography; D005260:Female; D006801:Humans; D007223:Infant; D008279:Magnetic Resonance Imaging; D020752:Neurocutaneous Syndromes / Q000145:classification / Q000150:complications* / Q000175:diagnosis; D019339:Port-Wine Stain / Q000175:diagnosis / Q000209:etiology; D012640:Seizures / Q000209:etiology; D012867:Skin / Q000473:pathology*; D013341:Sturge-Weber Syndrome / Q000150:complications*