title: [Telangiectatic osteogenic sarcoma].
abstract: The authors treated 6 children with sarcoma telangiectaticum (SOT). Their average ages was 7.8 years (ranging from 4 to 15 years of age). In 3 children the tumor was located in the proximal epiphysis of the femur and in the remaining 3 cases in the distal epiphysis of the femur. Clinical symptoms were present on average 8.6 weeks (ranging from 2 to 20 weeks) before the final diagnosis was made. In 3 children the final diagnosis was made after performing 1 biopsy, while in the remaining 3 cases a second biopsy was required to confirm the diagnosis. All cases were given pre-op chemotherapy (Cisplatin, Adriablastine). In all cases quick growth of the tumor was noted and in all cases a pathological fracture occurred. In 2 children mutilating surgical procedures were performed, 1 child had an endoprosthesis implanted outside our facility and 1 child was treated for lung metastases. Two children are alive, but no information about their medical condition is available.
authors.affiliation: Oddział Ortopedyczno-Urazowy, Katedra i Klinika Chirurgii Pediatrycznej, Uniwersytecki Szpital Dzieciecy, Wydział Lekarski Uniwersytetu Jagiellońskiego.
authors.forename: Tadeusz
authors.initials: T
authors.lastname: Lejman
authors.forename: Jerzy
authors.initials: J
authors.lastname: Sułko
mesh_terms: D000293:Adolescent; D002648:Child; D002675:Child, Preschool; D005260:Female; D005266:Femoral Neoplasms / Q000150:complications / Q000000981:diagnostic imaging / Q000473:pathology / Q000628:therapy; D005598:Fractures, Spontaneous / Q000209:etiology; D006801:Humans; D008297:Male; D009362:Neoplasm Metastasis; D012516:Osteosarcoma / Q000150:complications / Q000000981:diagnostic imaging / Q000473:pathology / Q000628:therapy; D011859:Radiography; D012189:Retrospective Studies; D013684:Telangiectasis / Q000150:complications / Q000000981:diagnostic imaging / Q000473:pathology / Q000628:therapy; D013997:Time Factors