Recurrent primary cardiac malignant fibrous histiocytoma following orthotopic heart transplantation.
Malignant fibrous histiocytoma (MFH) is an extremely rare primary cardiac tumor. We describe a young patient who underwent orthotopic heart transplantation for an unresectable right ventricular MFH and presented 7 years later with a local recurrence in the native right atrium. This was treated by complete resection of the right atrial tumor and adjuvant chemotherapy. This case represents the only reported long-term survival following cardiac transplantation for MFH and describes our management strategy for local recurrence in this patient.
Akhter
Shahab A
SA
Division of Cardiac Surgery, University of Cincinnati College of Medicine, Cincinnati, Ohio 45267-0558, USA. shahab.akhter@uc.edu
McGinty
John
J
Konys
Joseph J
JJ
Giesting
Rosann M
RM
Merrill
Walter H
WH
Wagoner
Lynne E
LE
D000328:Adult; D006338:Heart Neoplasms / Q000601:surgery*; D016027:Heart Transplantation; D018219:Histiocytoma, Benign Fibrous / Q000601:surgery*; D006801:Humans; D008297:Male; D009364:Neoplasm Recurrence, Local / Q000628:therapy