title: Arrhythmogenic right ventricular dysplasia/cardiomyopathy.
abstract: Arrhythmogenic right ventricular dysplasia/cardiomyopathy is recognized as an important cause of death in young patients, particularly athletes. In the past 5 years, cardiac MRI techniques have evolved rapidly in an attempt to improve the noninvasive diagnosis of this disorder. Steady-state free precession sequences and more rapid fat saturation techniques have permitted a comprehensive and well-tolerated examination. The first formal testing of diagnostic accuracy among a broad range of readers has recently been completed. Despite these advances, limited spatial resolution and interobserver variability have prevented successful implementation of these methods. Future approaches may include high-field imaging at 3 Tesla, and viability imaging to improve diagnostic accuracy.
authors.affiliation: Department of Medicine, Cardiovascular Medicine Division, University of Pennsylvania School of Medicine, 9014 E. Gates Pavilion, 3400 Spruce Street, Philadelphia, PA 19014, USA. ferrariv@mail.med.upenn.edu
authors.forename: Victor A
authors.initials: VA
authors.lastname: Ferrari
authors.forename: Craig H
authors.initials: CH
authors.lastname: Scott
authors.forename: Cristina
authors.initials: C
authors.lastname: Basso
mesh_terms: D001145:Arrhythmias, Cardiac / Q000209:etiology; D019571:Arrhythmogenic Right Ventricular Dysplasia / Q000175:diagnosis* / Q000209:etiology / Q000235:genetics / Q000503:physiopathology; D016757:Death, Sudden, Cardiac / Q000209:etiology; D005544:Forecasting; D006801:Humans; D008279:Magnetic Resonance Imaging / Q000379:methods / Q000639:trends*