title: Recurrent primary cardiac malignant fibrous histiocytoma following orthotopic heart transplantation.
abstract: Malignant fibrous histiocytoma (MFH) is an extremely rare primary cardiac tumor. We describe a young patient who underwent orthotopic heart transplantation for an unresectable right ventricular MFH and presented 7 years later with a local recurrence in the native right atrium. This was treated by complete resection of the right atrial tumor and adjuvant chemotherapy. This case represents the only reported long-term survival following cardiac transplantation for MFH and describes our management strategy for local recurrence in this patient.
authors.affiliation: Division of Cardiac Surgery, University of Cincinnati College of Medicine, Cincinnati, Ohio 45267-0558, USA. shahab.akhter@uc.edu
authors.forename: Shahab A
authors.initials: SA
authors.lastname: Akhter
authors.forename: John
authors.initials: J
authors.lastname: McGinty
authors.forename: Joseph J
authors.initials: JJ
authors.lastname: Konys
authors.forename: Rosann M
authors.initials: RM
authors.lastname: Giesting
authors.forename: Walter H
authors.initials: WH
authors.lastname: Merrill
authors.forename: Lynne E
authors.initials: LE
authors.lastname: Wagoner
mesh_terms: D000328:Adult; D006338:Heart Neoplasms / Q000601:surgery*; D016027:Heart Transplantation; D018219:Histiocytoma, Benign Fibrous / Q000601:surgery*; D006801:Humans; D008297:Male; D009364:Neoplasm Recurrence, Local / Q000628:therapy