Right pulmonary agenesis associated with remaining bronchus stenosis, an equivalent of postpneumonectomy syndrome. Treatment by insertion of tissue expander in the thoracic cavity.
We report a case of right pulmonary agenesis with worsening of mediastinal shift during a viral bronchiolitis at the age of 5 months. The respiratory failure was due to stretching and narrowing of the remaining bronchus, as in postpneumonectomy syndrome. Weaning of respiratory assistance was possible after inserting a tissue expander in the empty side of the thoracic cavity. The correction of the shift brought a liberation of the left main stem bronchus. The main risk is heart compression. The child is now 3 years old and is at home. Filling of the prosthesis is done according to the clinical evolution.
Dobremez
E
E
Department of Pediatric Surgery, Hôpital Pellegrin-Enfants, Bordeaux, 33076, France. Eric.DOBREMEZ@wanadoo.fr
Fayon
M
M
Vergnes
P
P
D001982:Bronchial Diseases / Q000150:complications* / Q000601:surgery*; D003251:Constriction, Pathologic; D006801:Humans; D007223:Infant; D008168:Lung / Q000002:abnormalities*; D008297:Male; D015625:Tissue Expansion Devices