title: Nutritional follow-up of cystic fibrosis patients: the role of nutrition education.
abstract: OBJECTIVE
  To evaluate the nutritional status of a group of cystic fibrosis patients and establish the role of nutrition education addressed to them in a comparative study before and after intervention.
  
  
  METHODS
  All cystic fibrosis patients in regular follow-up in the pulmonology clinic of Instituto da Crianca during 1996-99 were prospectively monitored for 3.5 years. Measurements of weight, height, mid upper arm circumference, skinfolds and calculations of weight/age, height/age, weight/height, mid upper arm circumference and triceps z scores, percentage of ideal weight for height, percentage of body fat, check of the use of enzymes with meals and of the use of nutritional supplements were performed at four points in time: initial (I), 7 (II), 13 (III) and 43 (IV) months after the first evaluation. Nutritional counseling was given both verbally and in writing (booklet) to all patients.
  
  
  RESULTS
  Seventy-four patients, 38F/36M, age range 6 months to 18.4 years were evaluated. At study entry the anthropometric data showed: percentage of ideal weight for height = 94+/-13, percentage of body fat = 15+/-7.1, z scores for weight/age = -1.13+/-1.3, z scores for height/age = -0.94+/-1.2, z scores for weight/height = -0.69+/-1.1, z scores for mid upper arm circumference = -1.35+/-1.3, triceps z scores = -0.74+/-0.9. Compliance with enzyme therapy and use of high-calorie supplements improved during the study period. There was a significant increase in weight/height and triceps z scores and percentage of body fat throughout the study period. After stratifying patients into three age groups the anthropometric improvement was only significant among children under 5 years of age
  
  
  CONCLUSIONS
  Mild malnutrition was present in this group of cystic fibrosis patients. The nutrition education led to an improvement in compliance with enzyme therapy, use of nutritional supplements and in nutritional status, mostly among the younger patients.
authors.affiliation: Instituto da Criança, Hospital das Clínicas, School of Medicine, Universidade de São Paulo (USP), São Paulo, SP. fabiva@tierra.co.br
authors.forename: Fabíola V
authors.initials: FV
authors.lastname: Adde
authors.forename: Joaquim C
authors.initials: JC
authors.lastname: Rodrigues
authors.forename: Ary L
authors.initials: AL
authors.lastname: Cardoso
mesh_terms: D000293:Adolescent; D017677:Age Distribution; D002648:Child; D002675:Child, Preschool; D003550:Cystic Fibrosis / Q000150:complications* / Q000628:therapy; D019587:Dietary Supplements; D002149:Energy Intake; D004812:Epidemiologic Methods; D005260:Female; D006801:Humans; D007223:Infant; D008297:Male; D044342:Malnutrition / Q000175:diagnosis / Q000209:etiology*; D015596:Nutrition Assessment; D009752:Nutritional Status; D010353:Patient Education as Topic / Q000379:methods*