Imaging findings in pleuropulmonary blastoma.
BACKGROUND
Pleuropulmonary blastoma (PPB) is a rare tumor of the chest seen in young children and recently recognized as distinct from the pulmonary blastoma typically encountered in adults.


OBJECTIVE
The purpose of this study is to review and describe the findings of PPB on radiography and CT in four patients.


METHODS
Radiographs and CT findings were reviewed in four patients with pathologically proven PPB.


RESULTS
All four cases demonstrated large masses in the right hemithorax with heterogeneous low attenuation, pleural effusion, contralateral mediastinal shift, and lack of chest wall invasion.


CONCLUSIONS
When a large pleural-based mass is identified in a young child, PPB should be considered. Suggestive findings include absence of chest wall invasion, presence of pleural fluid, right-sided location, and heterogeneous low attenuation.
Naffaa
Lena N
LN
Department of Radiology, Cincinnati Children's Hospital Medical Center, 3333 Burnet Avenue, Cincinnati, OH 45229-3039, USA.
Donnelly
Lane F
LF
D002648:Child; D002675:Child, Preschool; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D008175:Lung Neoplasms / Q000000981:diagnostic imaging*; D008207:Lymphatic Metastasis / Q000000981:diagnostic imaging; D008297:Male; D008482:Mediastinum / Q000000981:diagnostic imaging; D010996:Pleural Effusion / Q000000981:diagnostic imaging; D010997:Pleural Neoplasms / Q000000981:diagnostic imaging*; D018202:Pulmonary Blastoma / Q000000981:diagnostic imaging* / Q000556:secondary; D012187:Retroperitoneal Space; D012189:Retrospective Studies; D036542:Tomography, Spiral Computed