[Acute intermittent porphyria coexisting with chronic postinfectious renal failure].
In this paper a case of 46-year-old woman suffering from the acute intermittent porphyria (AIP) was presented. She developed the chronic renal failure due to the hypertension, reccurent urinary tract infections and neurogenic urinary bladder following the autonomic neuropathy. The patient eventually died in spite of haemodialysis. Skin lesions observed in the last stage of the disease could be an evidence of the possible conversion of AIP in variegate porphyria (VP). However, this suspicion is only the hypothesis due to the lack of the adequate enzymatic lab tests.
Szymańska-Chabowska
Anna
A
Katedra i Klinika Chorób Wewnetrznych, Zawodowych i Nadciśnienia Tetniczego AM we Wrocławiu.
Skoczyńska
Anna
A
Chlebda
Ewa
E
Andrzejak
Ryszard
R
D005260:Female; D006801:Humans; D007676:Kidney Failure, Chronic / Q000150:complications* / Q000382:microbiology* / Q000628:therapy; D007710:Klebsiella Infections / Q000382:microbiology*; D008875:Middle Aged; D017118:Porphyria, Acute Intermittent / Q000150:complications*; D006435:Renal Dialysis; D001750:Urinary Bladder, Neurogenic / Q000150:complications; D014552:Urinary Tract Infections / Q000382:microbiology