Mitral valve morphology and morbidity/mortality in Shone's complex.
Early echocardiographic studies of 50 patients with Shone's complex were retrospectively examined to identify left-sided cardiac features associated with progressive mitral valve (MV) disease requiring intervention, as well as mortality. Thickened MV leaflets, shortened MV chordae coupled with either thickened MV leaflets or turbulence at or below the MV noted by color Doppler, left ventricular outflow tract obstruction without coarctation of the aorta, and mild or moderate aortic insufficiency were associated with a poor prognosis.
Ikemba
Catherine M
CM
University of Texas Southwestern, Children's Medical Center of Dallas, Division of Cardiology, Dallas, Texas, USA. catherine.ikemba@childrens.com
Eidem
Benjamin W
BW
Fraley
J Kennard
JK
Eapen
Reenu S
RS
Pignatelli
Ricardo
R
Ayres
Nancy A
NA
Bezold
Louis I
LI
D002648:Child; D002675:Child, Preschool; D018618:Echocardiography, Doppler, Color; D005260:Female; D006330:Heart Defects, Congenital / Q000000981:diagnostic imaging / Q000401:mortality* / Q000628:therapy; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D008297:Male; D008943:Mitral Valve / Q000002:abnormalities* / Q000000981:diagnostic imaging* / Q000601:surgery; D011379:Prognosis; D012189:Retrospective Studies; D013781:Texas / Q000453:epidemiology; D014694:Ventricular Outflow Obstruction / Q000000981:diagnostic imaging / Q000401:mortality* / Q000628:therapy