Bednar tumor.
Pigmented dermatofibrosarcoma protuberance DSFP, also known as Bednar tumor or formerly known as pigmented storiform neurofibroma is a rare variant of DSFP. Bednar first described it in 1957. The histology is striking because of the presence of multipolar pigment laden dendritic cells scattered among spindle shaped cells with a storiform pattern, the latter being characteristic of DSFP. The spindle cells are positive for CD34, and Vimentin and negative for S100. The pigment represents melanin. We describe such a tumor because of its rarity and very striking microscopic appearance.
Kuruvila
Sarah
S
Department of Histopathology, Royal Hospital, PB No. 1331, PC 111, Seeb, Muscat, Sultanate of Oman. alexp@omantel.net.com
Ramadan
Fatma A
FA
D000328:Adult; D014408:Biomarkers, Tumor / Q000032:analysis; D003713:Dendritic Cells / Q000473:pathology; D018223:Dermatofibrosarcoma / Q000473:pathology*; D003937:Diagnosis, Differential; D006801:Humans; D008297:Male; D012867:Skin / Q000473:pathology; D012878:Skin Neoplasms / Q000473:pathology*
D014408:Biomarkers, Tumor