title: Cervico-medullary desmoplastic infantile ganglioglioma: an unusual case with diffuse leptomeningeal dissemination at diagnosis.
abstract: Desmoplastic infantile ganglioglioma (DIG) is a rare intracranial tumor affecting newborns and infants, and generally arising in the supratentorial region. We report a case of an unusual DIG, arising at the cervico-medullary junction, with diffuse leptomeningeal seeding at diagnosis that was treated with chemotherapy (CT) and delayed partial surgery. The case we describe demonstrates that DIG can occur in the subtentorial region and can show leptomeningeal dissemination like other low-grade gliomas.
authors.affiliation: Dipartimento di Emato-Oncologia, Istituto Giannina Gaslini, Genova, Italia.
authors.forename: Claudia
authors.initials: C
authors.lastname: Milanaccio
authors.forename: Paolo
authors.initials: P
authors.lastname: Nozza
authors.forename: Marcello
authors.initials: M
authors.lastname: Ravegnani
authors.forename: Andrea
authors.initials: A
authors.lastname: Rossi
authors.forename: Alessandro
authors.initials: A
authors.lastname: Raso
authors.forename: Claudio
authors.initials: C
authors.lastname: Gambini
authors.forename: Maria Luisa
authors.initials: ML
authors.lastname: Garrè
authors.forename: Torsten
authors.initials: T
authors.lastname: Pietsch
mesh_terms: D018303:Ganglioglioma / Q000000981:diagnostic imaging* / Q000473:pathology* / Q000628:therapy; D006801:Humans; D007223:Infant; D008279:Magnetic Resonance Imaging / Q000379:methods; D008297:Male; D008577:Meningeal Neoplasms / Q000000981:diagnostic imaging* / Q000473:pathology* / Q000628:therapy; D011859:Radiography