title: Dorsal intramedullary dermoids.
abstract: We report a case of a 31-year-old woman with an intramedullary thoracic dermoid, who had progressive spastic paraparesis in her lower extremities over a period of three years, as well as loss of bowel and bladder control. She had been operated for "spina bifida" at three days of age but had no neurologic deficit. MRI of the thoracic spine showed an intramedullary hypointense lesion at T7-T8, associated with an intramedullary lipoma at a higher level. Intracapsular resection of an intramedullary dermoid cyst was performed. We review the literature on intramedullary dermoids differentiating them from the more common, but still rare, lumbosacral subdural juxtamedullary dermoids. We discuss the associated malformations with these lesions, as well as their pathophysiology and treatment. Although uncommon, dorsal intramedullary dermoids should be suspected and treated in a timely manner, especially in presence of other congenital anomalies.
authors.affiliation: Dr. Erfan and Bagedo Hospitals, King Fahad St. (Al Sitteen), P.O. Box 6519, Jeddah, 21452, Saudi Arabia. mwnajjar@yahoo.com
authors.forename: Marwan W
authors.initials: MW
authors.lastname: Najjar
authors.forename: John A
authors.initials: JA
authors.lastname: Kusske
authors.forename: Anton N
authors.initials: AN
authors.lastname: Hasso
mesh_terms: D000328:Adult; D003884:Dermoid Cyst / Q000150:complications / Q000473:pathology / Q000601:surgery*; D005260:Female; D006801:Humans; D008067:Lipoma / Q000473:pathology; D008279:Magnetic Resonance Imaging; D019635:Neurosurgical Procedures; D020336:Paraparesis, Spastic / Q000209:etiology; D013122:Spinal Diseases / Q000151:congenital; D013125:Spinal Neoplasms / Q000150:complications / Q000473:pathology / Q000601:surgery*; D013131:Spine / Q000002:abnormalities
references.citation: Neurosurgery. 1988 Dec;23(6):765-7
references.pmid: 3216977
references.citation: J Neurosurg. 1949 Mar;6(2):97-112
references.pmid: 18114368
references.citation: Neurosurgery. 1989 Dec;25(6):955-9
references.pmid: 2689904
references.citation: Ann Surg. 1938 Jan;107(1):107-15
references.pmid: 17857105
references.citation: Arq Neuropsiquiatr. 2001 Mar;59(1):112-5
references.pmid: 11299443
references.citation: Acta Neurochir (Wien). 1969;21(2):197-204
references.pmid: 5365152
references.citation: Neuroradiology. 2000 Jan;42(1):51-3
references.pmid: 10663473
references.citation: J Neurol Neurosurg Psychiatry. 1966 Jun;29(3):262-4
references.pmid: 5937643
references.citation: Rev Neurol (Paris). 1952;86(4):339-40
references.pmid: 13004590
references.citation: Am J Roentgenol Radium Ther Nucl Med. 1969 Feb;105(2):386-9
references.pmid: 5764663
references.citation: No Shinkei Geka. 2000 Feb;28(2):155-60
references.pmid: 10666735
references.citation: J Neurosurg. 1970 Dec;33(6):676-81
references.pmid: 4921571
references.citation: Neurosurgery. 1989 Dec;25(6):860-4
references.pmid: 2601815
references.citation: J Neurol Neurosurg Psychiatry. 1956 Nov;19(4):241-59
references.pmid: 13377191
references.citation: Neurochirurgia (Stuttg). 1977 Jul;20(4):105-8
references.pmid: 895969
references.citation: Neurochirurgia (Stuttg). 1977 Jul;20(4):108-16
references.pmid: 895970
references.citation: Eur J Pediatr Surg. 1991 Apr;1(2):73-9
references.pmid: 1854713