Neoaortic aneurysm after stage I Norwood reconstruction.
Treatment of hypoplastic left heart syndrome through staged repairs has resulted in patients surviving into adulthood. Use of either aortic or pulmonary homografts in performing the neoaortic reconstruction has become the standard of practice with relatively few problems. We report the case of an asymptomatic adolescent boy who had an enlarging neoaortic aneurysm and mild neoaortic regurgitation develop after undergoing a stage I Norwood procedure using a pulmonary homograft. Given the risk for rupture and a concern for further functional deterioration of the neoaortic valve, the patient underwent repair. Histologic examination showed a striking accumulation of myxoid material as well as abnormal vasculature in both the native and engrafted portions of the neoaorta.
Ehsan
Afshin
A
Division of Cardiothoracic Surgery, Tufts-New England Medical Center, Boston, Massachusetts 02111, USA. aehsan@tufts-nemc.org
Singh
Harbinder
H
Vargas
Sara O
SO
Sachweh
Joerg
J
Jonas
Richard A
RA
D000293:Adolescent; D001014:Aortic Aneurysm / Q000175:diagnosis / Q000209:etiology / Q000601:surgery*; D001021:Aortic Valve; D006348:Cardiac Surgical Procedures / Q000009:adverse effects / Q000379:methods; D006801:Humans; D018636:Hypoplastic Left Heart Syndrome / Q000601:surgery*; D008297:Male; D011183:Postoperative Complications / Q000175:diagnosis / Q000601:surgery*; D011664:Pulmonary Valve / Q000637:transplantation*