title: Caroli's syndrome. A case report and review of the literature.
abstract: Personal experience in the treatment of a female patient presenting a pure monolobar Caroli's disease, is described. The woman was asymptomatic so far; during the last 2 weeks she was admitted on 3 occasions with repeated attacks of cholangitis and obstructive jaundice. Surgery was performed for relief of the jaundice. A diagnosis of segmental Caroli's disease (congenital dilatation of intrahepatic bile ducts) with congenital fibrosis was made on the basis of marked fibrous septa with the characteristic ductal plate formation on left hepatectomy specimen and the cysts seen on ultrasound.
authors.affiliation: Department of Cytopathology, General Hospital of Chania, Crete, Greece.
authors.forename: D
authors.initials: D
authors.lastname: Tamiolakis
authors.forename: V
authors.initials: V
authors.lastname: Arvanitidou
authors.forename: S
authors.initials: S
authors.lastname: Nikolaidou
authors.forename: S
authors.initials: S
authors.lastname: Barbagadaki
authors.forename: K
authors.initials: K
authors.lastname: Avgidou
authors.forename: P
authors.initials: P
authors.lastname: Boglou
authors.forename: N
authors.initials: N
authors.lastname: Papadopoulos
mesh_terms: D015746:Abdominal Pain / Q000209:etiology; D000328:Adult; D016767:Caroli Disease / Q000145:classification / Q000175:diagnosis / Q000000981:diagnostic imaging / Q000601:surgery; D005260:Female; D006801:Humans; D008279:Magnetic Resonance Imaging; D014057:Tomography, X-Ray Computed; D016896:Treatment Outcome; D014463:Ultrasonography