[An autopsy case of intestinal Behcet's disease with sacroiliitis accompanied by myelodysplastic syndrome with trisomy 8. ].
Here we described an autopsy case of intestinal Behcet's disease with sacroiliitis associated with myelodysplastic syndrome (RAEB-t, 8+). Over twenty cases of Behcet's disease associated with myelodysplastic syndrome have been reported in preliterature so far. The majority of them are incomplete type of Behcet's disease having intestinal ulceration. Of those, trisomy 8 is the most common chromosomal abnormality. We reviewed similar cases reported and investigated the association of intestinal Behcet's disease with trisomy 8. The association of sacroiliitis with Behcet's disease is also studied.
Tsubata
Rieko
R
Department of Rheumatology, Tokyo Medical and Dental University, Tokyo, Japan.
Suzuki
Fumihito
F
Sugihara
Takehiko
T
Ogawa
Jun
J
Hagiyama
Hiroyuki
H
Nanki
Toshihiro
T
Kohsaka
Hitoshi
H
Kubota
Tetsuo
T
Miyasaka
Nobuyuki
N
D000368:Aged; D000754:Anemia, Refractory, with Excess of Blasts / Q000150:complications* / Q000235:genetics; D001528:Behcet Syndrome / Q000150:complications*; D002898:Chromosomes, Human, Pair 8; D006801:Humans; D007077:Ileal Diseases / Q000150:complications*; D008297:Male; D012447:Sacrum; D013166:Spondylitis / Q000150:complications*; D014314:Trisomy; D014456:Ulcer / Q000150:complications*