title: [Short-term results of the Fontan operation in patients with Down syndrome].
abstract: Despite an extensive experience with Fontan operation, there is a paucity of information to guide the indication of the procedure in patients with Down syndrome. Of 79 patients who had undergone a Fontan operation in our hospital between 1995 and 2003, 3 had Down syndrome. All 3 patients had complete atrioventricular septal defect with single ventricular physiology. Two patients survived, and 1 died of chylothorax and respiratory infection. The 2 survivors have done well in the short-term without complications. We consider that in appropriately selected patients with Down syndrome in whom biventricular repair is precluded, the Fontan operation is the choice of the procedures.
authors.affiliation: Department of Cardiovascular Surgery, Shakaihoken Chukyo Hospital, Nagoya, Japan.
authors.forename: H
authors.initials: H
authors.lastname: Sakurai
authors.forename: T
authors.initials: T
authors.lastname: Akita
authors.forename: N
authors.initials: N
authors.lastname: Kato
authors.forename: H
authors.initials: H
authors.lastname: Hasegawa
authors.forename: T
authors.initials: T
authors.lastname: Sakurai
authors.forename: J
authors.initials: J
authors.lastname: Sugiura
authors.forename: M
authors.initials: M
authors.lastname: Matsushima
authors.forename: M
authors.initials: M
authors.lastname: Maeda
mesh_terms: D002675:Child, Preschool; D002916:Chylothorax / Q000209:etiology; D004314:Down Syndrome / Q000150:complications*; D018729:Fontan Procedure; D006330:Heart Defects, Congenital / Q000601:surgery*; D006801:Humans; D007223:Infant; D011183:Postoperative Complications; D016896:Treatment Outcome