title: Malignant haemangiopericytoma of the mesorectum.
abstract: The authors report the case of a malignant haemangiopericytoma found in an uncommon location, namely the mesorectum. Haemangiopericytomas of the mesorectum are rare mesenchymal tumours of vascular origin that usually occur in the musculature of the extremities, retroperitoneum, pelvis (uterus, ovary and urinary bladder), head, neck and lungs. Rare sites include the liver, pancreas, stomach and greater omentum. Because of their rarity the overall experience has not been significant and little has been published concerning such tumours. In addition, the difficult interpretation of the histological evidence and the poor prognosis of the disease may still give rise to problems in terms of clinical management. Haemangiopericytomas of the retrorectal space, however, seem to behave like malignant tumours: the clinical course is poor and survival short, despite radical surgery, due to early distant metastases and local recurrence. Surgery still remains the mainstay of treatment. Adjuvant therapies should be considered.
authors.affiliation: Department of Surgical Oncology, Division of Digestive Surgery and Liver Transplantation, Regina Elena Cancer Institute, Rome.
authors.forename: Giovanni
authors.initials: G
authors.lastname: Vennarecci
authors.forename: Arianna
authors.initials: A
authors.lastname: Boschetto
authors.forename: Alessandro
authors.initials: A
authors.lastname: Esposito
authors.forename: Luca
authors.initials: L
authors.lastname: Giovannelli
authors.forename: Francesco
authors.initials: F
authors.lastname: Buscaglia
authors.forename: Valerio
authors.initials: V
authors.lastname: Corazza
authors.forename: Roberto
authors.initials: R
authors.lastname: Santoro
authors.forename: Pietro
authors.initials: P
authors.lastname: Mancini
authors.forename: Riccardo
authors.initials: R
authors.lastname: Lorusso
authors.forename: Mirella
authors.initials: M
authors.lastname: Marino
authors.forename: Giuseppe Maria
authors.initials: GM
authors.lastname: Ettorre
mesh_terms: D000328:Adult; D005260:Female; D006393:Hemangiopericytoma / Q000175:diagnosis / Q000000981:diagnostic imaging / Q000401:mortality / Q000473:pathology / Q000601:surgery; D006801:Humans; D008279:Magnetic Resonance Imaging; D009362:Neoplasm Metastasis; D010534:Peritoneal Neoplasms / Q000175:diagnosis / Q000000981:diagnostic imaging / Q000401:mortality / Q000473:pathology / Q000601:surgery; D010537:Peritoneum / Q000473:pathology; D013997:Time Factors; D014057:Tomography, X-Ray Computed