Intraneural perineurioma in a child with Beckwith-Wiedemann syndrome.
To the authors' knowledge, this is the first report of an intraneural perineurioma in a child with Beckwith-Wiedemann syndrome. Intraneural perineurioma, previously known as localized hypertrophic neuropathy, is a rare benign peripheral nerve sheath tumor arising from perineurium. This report adds a new entity in the spectrum of tumor formation in Beckwith-Wiedemann syndrome.
Chen
Lugen
L
Department of Pathology and Laboratory Medicine, Nassau University Medical Center, East Meadow, NY 11554, USA.
Li
Yanhua
Y
Lin
Jen H
JH
D001506:Beckwith-Wiedemann Syndrome / Q000150:complications*; D002648:Child; D006801:Humans; D008297:Male; D018317:Nerve Sheath Neoplasms / Q000150:complications / Q000473:pathology* / Q000601:surgery; D010524:Peripheral Nervous System Neoplasms / Q000150:complications / Q000473:pathology* / Q000601:surgery; D014953:Wrist / Q000294:innervation / Q000473:pathology* / Q000601:surgery