Lymphangioleiomyomatosis with a giant bulla: report of a case.
We report a case of lymphangioleiomyomatosis (LAM) with a giant bulla. A 33-year-old woman was referred to our department for treatment of dyspnea. Chest computed tomography showed a giant bulla with many smaller bullae. To obtain a definitive diagnosis and relieve the dyspnea, we performed a lung biopsy and bullectomy, after which her symptoms and pulmonary function improved remarkably. She was commenced on progesterone, which improved her condition even further. This case report retrospectively follows the progression of her disease from the onset of symptoms 5 years before she was referred to us for treatment.
Fujiwara
Taiki
T
Department of Thoracic Surgery, Graduate School of Medicine, Chiba University, 1-8-1 Inohana, Chuo-ku, Chiba 260-8670, Japan.
Iyoda
Akira
A
Hiroshima
Kenzo
K
Yusa
Toshikazu
T
Igarashi
Natsuhiko
N
Tatsumi
Koichiro
K
Otsuji
Mizuto
M
Sekine
Yasuo
Y
Shibuya
Kiyoshi
K
Iizasa
Toshihiko
T
Saitoh
Yukio
Y
Fujisawa
Takehiko
T
D000328:Adult; D001707:Biopsy, Needle; D001999:Bronchoscopy / Q000379:methods; D004417:Dyspnea / Q000175:diagnosis / Q000209:etiology; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D007150:Immunohistochemistry; D018192:Lymphangioleiomyomatosis / Q000473:pathology* / Q000601:surgery; D011013:Pneumonectomy; D011656:Pulmonary Emphysema / Q000473:pathology* / Q000601:surgery; D012129:Respiratory Function Tests; D018570:Risk Assessment; D012720:Severity of Illness Index; D014057:Tomography, X-Ray Computed / Q000379:methods; D016896:Treatment Outcome