Anesthesia for cleft lip surgery in a child with Seckel syndrome--a case report.
We describe the anesthetic management of a 5-year-old girl diagnosed with Seckel syndrome, for cleft lip surgery. The syndrome is characterized by severe intrauterine and postnatal growth retardation with proportional dwarfism, typical beak-like triangular nose, and mental retardation, accounting for its various synonyms such as bird-headed dwarfism, microcephalic primordial dwarfism, nanocephalic dwarfism and Seckel-type dwarfism.
Rajamani
Arvind
A
Department of Anaesthesiology and Critical Care, Sri Ramachandra Medical College and Research Institute, Sri Ramachandra Nagar, Chennai, India. rrarvind@yahoo.com
Kamat
Vijaylakshmi
V
Murthy
Jyotsna
J
Hussain
Syed Altaf
SA
D000015:Abnormalities, Multiple / Q000601:surgery*; D000758:Anesthesia; D002675:Child, Preschool; D002971:Cleft Lip / Q000601:surgery*; D004392:Dwarfism; D005147:Facial Bones / Q000002:abnormalities; D005260:Female; D005317:Fetal Growth Retardation; D006801:Humans; D007442:Intubation, Intratracheal; D013577:Syndrome