Anesthetic management of Turner syndrome: a systematic approach.
Turner syndrome is a complex and common genetic disorder that affects women and is associated with a wide variety of anatomic and physiological disorders. These abnormalities, especially those relating to the airway and cardiovascular system, pose a challenge to the anesthesiologist. We report a case of Turner syndrome associated with mental retardation and difficult airway, followed by a discussion of the perioperative management and review of the relevant literature. We also provide a concise tabular summary of the many problems associated with Turner syndrome and give guidelines for a systematic perioperative approach.
Mashour
George A
GA
Department of Anesthesia and Critical Care, Massachusetts General Hospital, Harvard Medical School, Boston, MA 02114, USA. gmashour@partners.org
Sunder
Neelakantan
N
Acquadro
Martin A
MA
D000758:Anesthesia / Q000379:methods*; D005260:Female; D005336:Fiber Optic Technology; D005592:Fracture Fixation; D006801:Humans; D007442:Intubation, Intratracheal; D008875:Middle Aged; D014424:Turner Syndrome / Q000235:genetics / Q000473:pathology*