A case of systemic malignant atrophic papulosis (Köhlmeier-Degos' disease).
Malignant atrophic papulosis (MAP) is a rare and clinically distinctive vasculopathy. It is characterized by narrowing and occlusion of the lumen by intimal proliferation and thrombosis, which leads to ischemia and infarction in the involved organ systems. Its rarity and rapidly fatal course make the disease a difficult diagnostic and therapeutic challenge.
Fernández-Pérez
Evans R
ER
Department of Critical Care Medicine, Mayo Clinic College of Medicine, Rochester, MN, USA. fernandez.evans@mayo.edu
Grabscheid
Erica
E
Scheinfeld
Noah S
NS
D015746:Abdominal Pain / Q000209:etiology; D000328:Adult; D002544:Cerebral Infarction / Q000209:etiology; D003967:Diarrhea / Q000209:etiology; D006801:Humans; D008297:Male; D010996:Pleural Effusion / Q000209:etiology; D012008:Recurrence; D017444:Skin Diseases, Papulosquamous / Q000150:complications*; D017445:Skin Diseases, Vascular / Q000150:complications*; D013919:Thromboangiitis Obliterans / Q000150:complications*; D014839:Vomiting / Q000209:etiology