Ruptured aneurysm of the subclavian artery in a patient with von Recklinghausen's disease.
A vascular manifestation of von Recklinghausen's disease is rare, but may be fatal if it is disrupted. A 39-year-old male with von Recklinghausen's disease presented with a large and tender bruise extending from his left neck to his left shoulder and arm. Computerized axial tomography revealed a ruptured aneurysm of the left subclavian artery. The patient underwent emergency surgery to exclude the aneurysm, and cross-over bypass grafting of both subclavian arteries was performed. We present a brief review of vascular maintestation of von Recklinghausen's disease, as well as a discussion regarding the strategy for treating this rare presentation.
Tatebe
Shoh
S
Department of Thoracic and Cardiovascular Surgery, Mito Saiseikai General Hospital, Mito, Japan.
Asami
Fuyuki
F
Shinohara
Hirohiko
H
Okamoto
Takeshi
T
Kuraoka
Setsuo
S
D000328:Adult; D017542:Aneurysm, Ruptured / Q000209:etiology* / Q000601:surgery; D003288:Contusions / Q000209:etiology; D006801:Humans; D008297:Male; D009456:Neurofibromatosis 1 / Q000150:complications*; D013348:Subclavian Artery / Q000473:pathology* / Q000601:surgery; D014057:Tomography, X-Ray Computed