Desmoplastic fibroma of the skull in an infant.
METHODS
A 1-year-old girl presented with a 10-month history of progressive protuberance of the left frontal skull. Magnetic resonance imaging and computed tomography demonstrated a large osteolytic interosseous mass extending to the frontal sinus and temporal base without any intracranial invasion. A fronto-temporo-parietal craniectomy of the outer skull table and excision of an interosseous tumor resulted in local dural exposure in the temporal area that was covered by cranioplasty. Pathological examination identified desmoplastic fibroma (DF) of the skull. The patient's cranial asymmetry was improved without recurrence of the tumor up to the 12th month after excision.


CONCLUSIONS
In the literature, 11 cases of DF of the skull have been reported, two of which have involved children (one an infant). We report the second known infantile case of DF of the skull.
Yoon
Soo-Han
SH
Department of Neurosurgery, School of Medicine, Ajou University, Paldal-Gu, Wonchon-Dong, San#5, Suwon, South Korea.
Kim
Se Hyek
SH
Shin
Yong Sam
YS
Ahn
Young-Whan
YW
Cho
Kyung-Gi
KG
Lee
Ki Bum
KB
Cho
Ki Hong
KH
D005260:Female; D018220:Fibroma, Desmoplastic / Q000473:pathology* / Q000601:surgery; D006801:Humans; D021621:Imaging, Three-Dimensional / Q000379:methods; D007223:Infant; D008279:Magnetic Resonance Imaging / Q000379:methods; D012888:Skull Neoplasms / Q000473:pathology* / Q000601:surgery; D014057:Tomography, X-Ray Computed / Q000379:methods