Postural headache in a child with Marfan syndrome: case report and review of the literature.
The case of a 10-year-old female with Marfan syndrome and postural headache secondary to spontaneous intracranial hypotension is described. The patient was found to have multiple dural ectasias and a cerebrospinal fluid leak at the left cervicothoracic junction. Her presentation, diagnostic work-up, and management are reviewed, and the relevant literature is discussed. Spontaneous intracranial hypotension secondary to cerebrospinal fluid leaks from dural ectasia should be recognized as a potential complication in children with Marfan syndrome and other connective tissue diseases.
Rosser
Tena
T
Department of Neurology, Children's National Medical Center, The George Washington University, Washington, DC 20010, USA. trosser@cnmc.org
Finkel
Julie
J
Vezina
Gilbert
G
Majd
Massoud
M
D002648:Child; D004108:Dilatation, Pathologic / Q000150:complications; D004388:Dura Mater / Q000473:pathology; D005260:Female; D006261:Headache / Q000175:diagnosis / Q000209:etiology* / Q000628:therapy; D006801:Humans; D019585:Intracranial Hypotension / Q000175:diagnosis / Q000209:etiology* / Q000628:therapy; D008382:Marfan Syndrome / Q000150:complications* / Q000503:physiopathology*; D011187:Posture / Q000502:physiology