Status Dystonicus: study of five cases.
Status Dystonicus (SD) is characterized by generalized muscle contractions in dystonic patients. We report 5 cases of SD, two of which in patients with dystonic cerebral palsy, one in a patient with primary segmental dystonia, one in a patient with Hallervorden-Spatz syndrome and one in a patient with Wilson's disease (WD). Three patients were admitted to an intensive care unit and treated with propofol and midazolam, and two were submitted to neurosurgical procedures (bilateral pallidotomy and bilateral pallidal deep brain stimulation). Triggering factors were identified in three patients as follows: infection, stress-induced and zinc therapy for WD. On follow-up, two patients presented with significant improvement of dystonia, whereas the other three cases the clinical picture ultimately returned to baseline pre-SD condition.
Teive
Hélio A G
HA
Serviço de Neurologia, Hospital de Clínicas, Universidade Federal do Paraná, Curitiba, PR, Brazil. hagteive@mps.com.br
Munhoz
Renato P
RP
Souza
Mônica M
MM
Antoniuk
Sérgio A
SA
Santos
Mara Lucia S F
ML
Teixeira
Manoel Jacobsen
MJ
Barbosa
Egberto Reis
ER
Carvalho
Rodrigo C
RC
Scaff
Milberto
M
Werneck
Lineu César
LC
D000328:Adult; D002648:Child; D003402:Creatine Kinase / Q000097:blood; D020821:Dystonic Disorders / Q000097:blood / Q000188:drug therapy* / Q000601:surgery*; D004599:Electric Stimulation Therapy; D006801:Humans; D008297:Male; D008875:Middle Aged; D013238:Stereotaxic Techniques; D016896:Treatment Outcome
D003402:Creatine Kinase