title: A case of bronchobiliary fistula in the setting of adult polycystic kidney and liver disease, with a review of the literature.
abstract: A case of bronchobiliary fistula (BBF) was demonstrated in the setting of polycystic kidney and liver disease (PCKLD) by hepatobiliary scintigraphy. High-resolution noncontrast computed tomography through the liver showed a polycystic liver. A calcified cyst adjacent to the dome of the liver appeared to have a fistulous connection with the lung on coronal reconstructions. Hepatobiliary scan confirmed the fistulous connection. In a review of the literature, BBF has been associated with hydatid cyst disease, trauma, postsurgical states, and malignancy. As demonstrated by this case, BBF is difficult to diagnose and requires a high clinical index of suspicion. Hepatobiliary scintigraphy is the imaging modality of choice to confirm BBF, and PCKLD should be added to the list of antecedent etiologies.
authors.affiliation: Department of Radiology, Nuclear Medicine Division, Naval Medical Center San Diego, San Diego, CA 92134-1204, USA.
authors.forename: Robin
authors.initials: R
authors.lastname: Bird
authors.forename: Kimberly
authors.initials: K
authors.lastname: Fagen
authors.forename: Danielle
authors.initials: D
authors.lastname: Taysom
authors.forename: Eugene D
authors.initials: ED
authors.lastname: Silverman
mesh_terms: D000368:Aged; D001658:Biliary Fistula / Q000000981:diagnostic imaging* / Q000209:etiology; D001983:Bronchial Fistula / Q000000981:diagnostic imaging* / Q000209:etiology; D002114:Calcinosis / Q000150:complications / Q000000981:diagnostic imaging*; D005260:Female; D006801:Humans; D008107:Liver Diseases / Q000150:complications / Q000000981:diagnostic imaging*; D007690:Polycystic Kidney Diseases / Q000150:complications / Q000000981:diagnostic imaging*; D011877:Radionuclide Imaging