[T-cell acute lymphoblastic leukemia /orbital lymphoblastic lymphoma in children].
METHODS
The authors report a case of an 6-year-old pediatric patient with a history of acute onset of proptosis of his right eye. He was admitted at hospital 6 months ago for proptosis concomitant with orbital trauma. Computed tomography scan demonstrated a mass involving the right orbit, right maxillary sinus, and zygoma with endocranial extension.


RESULTS
Incisional biopsy of the mass revealed after of histopathologic and immuno-histochemical evaluation a T-cell lymphoblastic lymphoma. Systemic examination and bone marrow aspirate show a acute lymphoblastic leukemia. The patient was treated with LMT96 Protocol. A complete Remission was observed after 13 months of follow up.


CONCLUSIONS
Primary T-cell lymphoblastic lymphoma of the orbit is a rare entity in any age group, but it is very rare in children. When tumors occurs in the orbit, it presents a challenging diagnosis problem, especially in pediatric patients.
Abdelouahed
K
K
Service Ophtalmologie A, Rabat, Maroc.
Laghmari
M
M
Tachfouti
S
S
Cherkaoui
W
W
Khorassani
M
M
M'Seffer
F Alaoui
FA
Mohcine
Z
Z
D002648:Child; D006801:Humans; D015459:Leukemia-Lymphoma, Adult T-Cell / Q000175:diagnosis; D008297:Male; D009378:Neoplasms, Multiple Primary / Q000175:diagnosis; D009918:Orbital Neoplasms / Q000175:diagnosis; D054198:Precursor Cell Lymphoblastic Leukemia-Lymphoma / Q000175:diagnosis