Successful treatment of solid-pseudopapillary tumor of the pancreas with multiple liver metastases.
The solid-pseudopapillary tumor (SPT) is a very rare pancreatic neoplasm that predominantly affects young females. About 450 cases have been described in the world literature and approximately 20% of the reported patients were children. The occurrence of SPT with distant metastases in children is extremely rare with only two previously reported cases. We now report a 16-year-old Asian girl with a large SPT and synchronous multiple liver metastases who was successfully treated in a 2-step strategy, including initial pylorus-preserving partial duodenopancreatectomy, right hemicolectomy, resection and allografting of the portal vein and secondary resection of 12 liver metastases. The patient is disease free after a follow-up of 18 months after resection of the primary tumor, suggesting that an aggressive surgical treatment might also be justified for metastasized SPT.
Hassan
I
I
Department of Surgery, Institute of Theoretical Surgery, Philipps University of Marburg, Marburg, Germany.
Celik
I
I
Nies
C
C
Zielke
A
A
Gerdes
B
B
Moll
R
R
Ramaswamy
A
A
Wagner
H-J
HJ
Bartsch
D K
DK
D000293:Adolescent; D002291:Carcinoma, Papillary / Q000556:secondary* / Q000601:surgery*; D005260:Female; D006801:Humans; D008113:Liver Neoplasms / Q000556:secondary* / Q000601:surgery*; D008279:Magnetic Resonance Imaging; D010190:Pancreatic Neoplasms / Q000473:pathology* / Q000601:surgery*; D014057:Tomography, X-Ray Computed