title: [Moyamoya disease].
abstract: Moyamoya disease is an idiopathic progressive vasculopathy characterized by slowly progressive narrowing involving the distal internal carotid artery and the proximal circle of Willis. Collateral vessels develop to compensate for the slowly progressive stenosis. These enlarged collaterals appear as a "puff of smoke" on angiography, which gives the disease its name. This review discusses the clinical manifestation, imaging findings, and angiographic features.
authors.affiliation: Klinik für Diagnostische und Interventionelle Neuroradiologie, Universitätsklinikum des Saarlandes Homburg/Saar. panagiotis_papanagiotou@hotmail.com
authors.forename: P
authors.initials: P
authors.lastname: Papanagiotou
authors.forename: I Q
authors.initials: IQ
authors.lastname: Grunwald
authors.forename: M
authors.initials: M
authors.lastname: Politi
authors.forename: C
authors.initials: C
authors.lastname: Roth
authors.forename: W
authors.initials: W
authors.lastname: Reith
mesh_terms: D002533:Cerebral Angiography / Q000379:methods*; D002536:Cerebral Arteries / Q000000981:diagnostic imaging*; D006801:Humans; D009072:Moyamoya Disease / Q000000981:diagnostic imaging* / Q000628:therapy*; D017410:Practice Guidelines as Topic; D010818:Practice Patterns, Physicians'; D018570:Risk Assessment / Q000379:methods*; D012307:Risk Factors