title: Successful treatment of solid-pseudopapillary tumor of the pancreas with multiple liver metastases.
abstract: The solid-pseudopapillary tumor (SPT) is a very rare pancreatic neoplasm that predominantly affects young females. About 450 cases have been described in the world literature and approximately 20% of the reported patients were children. The occurrence of SPT with distant metastases in children is extremely rare with only two previously reported cases. We now report a 16-year-old Asian girl with a large SPT and synchronous multiple liver metastases who was successfully treated in a 2-step strategy, including initial pylorus-preserving partial duodenopancreatectomy, right hemicolectomy, resection and allografting of the portal vein and secondary resection of 12 liver metastases. The patient is disease free after a follow-up of 18 months after resection of the primary tumor, suggesting that an aggressive surgical treatment might also be justified for metastasized SPT.
authors.affiliation: Department of Surgery, Institute of Theoretical Surgery, Philipps University of Marburg, Marburg, Germany.
authors.forename: I
authors.initials: I
authors.lastname: Hassan
authors.forename: I
authors.initials: I
authors.lastname: Celik
authors.forename: C
authors.initials: C
authors.lastname: Nies
authors.forename: A
authors.initials: A
authors.lastname: Zielke
authors.forename: B
authors.initials: B
authors.lastname: Gerdes
authors.forename: R
authors.initials: R
authors.lastname: Moll
authors.forename: A
authors.initials: A
authors.lastname: Ramaswamy
authors.forename: H-J
authors.initials: HJ
authors.lastname: Wagner
authors.forename: D K
authors.initials: DK
authors.lastname: Bartsch
mesh_terms: D000293:Adolescent; D002291:Carcinoma, Papillary / Q000556:secondary* / Q000601:surgery*; D005260:Female; D006801:Humans; D008113:Liver Neoplasms / Q000556:secondary* / Q000601:surgery*; D008279:Magnetic Resonance Imaging; D010190:Pancreatic Neoplasms / Q000473:pathology* / Q000601:surgery*; D014057:Tomography, X-Ray Computed