title: Scimitar syndrome associated with absence of the right pulmonary artery and a persistent primitive hepatic venous plexus.
abstract: An 18-month-old boy, referred because of an infection of the airways, was found to have a right-sided heart, a hypoplastic right lung, absence of the right pulmonary artery, and persistence of the hepatic venous plexus. The benign association of this unusual variant of the scimitar syndrome and persistence of the hepatic venous plexus needs to be recognised in order to avoid extensive investigations and surgery involving the inferior caval vein.
authors.affiliation: Service de Cardiologie Pédiatrique, Necker Enfants Malades, 75743 Paris, France. gabriella.agnoletti@nck.ap-hop-paris.fr
authors.forename: Gabriella
authors.initials: G
authors.lastname: Agnoletti
authors.forename: Damien
authors.initials: D
authors.lastname: Bonnet
authors.forename: Jacques
authors.initials: J
authors.lastname: De Blic
mesh_terms: D000015:Abnormalities, Multiple / Q000175:diagnosis / Q000628:therapy; D006503:Hepatic Veins / Q000002:abnormalities*; D006801:Humans; D007223:Infant; D008297:Male; D011651:Pulmonary Artery / Q000002:abnormalities*; D012587:Scimitar Syndrome / Q000175:diagnosis / Q000628:therapy