[Susac's syndrome. A rare microangiopathy of cochlea, retina, and brain].
Susac's syndrome is a rare disease characterized by encephalopathy, retinal artery occlusion, and a sensorineural hearing loss. Diagnosis may be difficult since most specialists are not familiar with this angiopathy. However, the typical symptom complex can mimic different pathologies, therefore requiring the attention of radiologists, ENT specialists, and ophthalmologists. We present a rare case of Susac's syndrome unveiled by audiometry results, MR imaging of the brain, and the ophthalmological findings..
Hilgert
E
E
Klinik und Poliklinik für Hals-, Nasen-, Ohrenheilkunde, Klinikum Grosshadern, LMU München. eva.hilgert@med.uni-muenchen.de
Harrèus
U
U
Kramer
M F
MF
Matthias
C
C
D000328:Adult; D000893:Anti-Inflammatory Agents / Q000008:administration & dosage; D001301:Audiometry, Pure-Tone; D001933:Brain Stem / Q000503:physiopathology; D002561:Cerebrovascular Disorders / Q000175:diagnosis / Q000188:drug therapy / Q000209:etiology*; D003051:Cochlea / Q000098:blood supply*; D003072:Cognition Disorders / Q000175:diagnosis / Q000188:drug therapy / Q000209:etiology*; D016057:Evoked Potentials, Auditory, Brain Stem / Q000502:physiology; D005260:Female; D005451:Fluorescein Angiography; D005500:Follow-Up Studies; D046088:Hearing Loss, Unilateral / Q000175:diagnosis / Q000188:drug therapy / Q000209:etiology*; D006801:Humans; D006895:Hydroxyethyl Starch Derivatives / Q000008:administration & dosage; D008833:Microcirculation / Q000503:physiopathology; D011239:Prednisolone / Q000008:administration & dosage; D015356:Retinal Artery Occlusion / Q000175:diagnosis / Q000188:drug therapy / Q000209:etiology*; D042262:Retinoscopy; D013577:Syndrome; D014012:Tinnitus / Q000209:etiology; D014724:Vestibular Function Tests; D014794:Visual Fields / Q000502:physiology
D000893:Anti-Inflammatory Agents; D006895:Hydroxyethyl Starch Derivatives; D011239:Prednisolone