Congenital pouch colon with prune belly syndrome and megalourethra.
Congenital pouch colon (CPC), an unusual high anorectal malformation in which a varying length of colon is replaced by a dilated pouch, has appeared in a number of case reports and series published in the English literature. There is only one case report of its association with prune belly syndrome (also known as triad syndrome, Eagle-Barrett syndrome, and abdominal muscle deficiency syndrome). We report the description and management of this rare association in a male neonate with CPC, prune belly syndrome, and congenital megalourethra.
Bangroo
A K
AK
Department of Pediatric Surgery, 1.3 Administration Block, St. Stephen's Hospital, Tis Hazari, Delhi 110054, India. abangroo@yahoo.com
Tiwari
Shashi
S
Khetri
Ramji
R
Sahni
Mohit
M
D003106:Colon / Q000002:abnormalities*; D006801:Humans; D007081:Ileostomy; D007231:Infant, Newborn; D008297:Male; D011535:Prune Belly Syndrome / Q000150:complications*; D014521:Urethra / Q000002:abnormalities* / Q000601:surgery