[Acute abdomen from ruptured adrenal pheochromocytoma: case report].
The pheochromocytoma is a very rare neoplasm, which originates in 98% of cases in the adrenal medulla; it is often bilateral in familial syndromes. It is more frequent in syndromes like MEN2, von Hippel-Lindau disease, and neuofribromatosis type 1. In this article the Authors report a case of a young woman with a large adrenal pheochromocytoma, that presented by an acute abdomen; the treatment was explorative laparotomy with unilateral adrenalectomy. Therapy of this tumour is founded on surgery, plus chemiotherapy radiotherapy or treatment with 131I-MIBG (iodine-131-metaiodobenzylguanidine in malignant cases (10%). According with the absence of a correlation between pathological findings and clinical behaviour, a long-term follow up is indispensable.
Bronzino
P
P
Struttura Complessa Chirurgia Generale, Ospedale Santa Croce, Mondovì (CN).
Abbo
L
L
Barisone
P
P
Dezzani
C
C
Genovese
A M
AM
Iannucci
P
P
Ippoliti
M
M
Sacchi
M
M
Aimo
I
I
D000006:Abdomen, Acute / Q000209:etiology*; D000310:Adrenal Gland Neoplasms / Q000150:complications* / Q000000981:diagnostic imaging / Q000601:surgery; D000315:Adrenalectomy; D000328:Adult; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D007150:Immunohistochemistry; D010673:Pheochromocytoma / Q000150:complications* / Q000000981:diagnostic imaging / Q000601:surgery; D011860:Radiography, Abdominal; D012422:Rupture, Spontaneous; D013997:Time Factors; D014057:Tomography, X-Ray Computed; D014463:Ultrasonography