Sciatic nerve enlargement in the Klippel-Trenaunay-Weber syndrome.
The case of a 35-year-old woman with Klippel-Trenaunay-Weber syndrome (KTWS) showing clinical symptoms of a peroneal nerve lesion is presented. An immense nerve enlargement along most of the sciatic, peroneal and tibial nerve was found to be due to a lipoma arising from the epi- and perineurium. Treatment consisted of extensive microsurgical neurolysis and excision of the tumor resulting in decompression of the affected nerves. Although rare, a perineural lipoma should be kept in mind in patients with KTWS showing neurological abnormalities.
Meirer
Romed
R
Department of Plastic and Reconstructive Surgery and the Ludwig-Boltzmann Institute for Quality Control in Plastic and Reconstructive Surgery, Leopold-Franzens University, Anichstrasse 35, A-6020 Innsbruck, Austria. romed.meirer@uibk.ac.at
Huemer
Georg M
GM
Shafighi
Maziar
M
Kamelger
Florian S
FS
Hussl
Heribert
H
Piza-Katzer
Hildegunde
H
D000328:Adult; D019299:Decompression, Surgical / Q000379:methods; D005260:Female; D006801:Humans; D007715:Klippel-Trenaunay-Weber Syndrome / Q000175:diagnosis / Q000601:surgery*; D008067:Lipoma / Q000175:diagnosis / Q000601:surgery*; D008866:Microsurgery / Q000379:methods; D020427:Peroneal Neuropathies / Q000175:diagnosis / Q000601:surgery; D020426:Sciatic Neuropathy / Q000175:diagnosis / Q000601:surgery*