Clinical response to sildenafil in pulmonary hypertension associated with Gaucher disease.
There are few reports of pulmonary hypertension in Gaucher disease. We report a patient who showed significant clinical improvement after treatment with sildenafil.
Fernandes
C J C
CJ
Pulmonary Division, Pulmonary Hypertension Unit, University of São Paulo Medical School, Brazil.
Jardim
C
C
Carvalho
L A S
LA
Farias
A Q
AQ
Filho
M Terra
MT
Souza
R
R
D000328:Adult; D004452:Echocardiography; D005260:Female; D005776:Gaucher Disease / Q000188:drug therapy*; D006801:Humans; D006976:Hypertension, Pulmonary / Q000188:drug therapy / Q000473:pathology*; D010879:Piperazines / Q000494:pharmacology / Q000627:therapeutic use*; D011687:Purines; D000068677:Sildenafil Citrate; D013450:Sulfones; D016896:Treatment Outcome; D014665:Vasodilator Agents / Q000494:pharmacology / Q000627:therapeutic use*
D010879:Piperazines; D011687:Purines; D013450:Sulfones; D014665:Vasodilator Agents; D000068677:Sildenafil Citrate