Mitral valve repair and cryo-Maze procedure in Ehlers-Danlos syndrome.
A 48-year-old man presented with typical features of Ehlers-Danlos syndrome, such as soft and hyperextensible skin, subcutaneous nodules, clubbed feet, and a mild degree of pigeon chest. In addition, his past history revealed congenital dislocation of the hip joint, retinal detachment, and repeated episodes of congestive heart failure due to severe mitral regurgitation and atrial fibrillation. We subjected the patient to surgical repair of the mitral valve combined with the maze procedure, which proved successful.
Goto
Tomoyuki
T
Department of Cardiovascular Surgery, National Cardiovascular Center, Osaka, Japan.
Kobayashi
Junjiro
J
Nakajima
Hiroyuki
H
Niwaya
Kazuo
K
Tagusari
Osamu
O
Kitamura
Soichiro
S
D001281:Atrial Fibrillation / Q000209:etiology / Q000601:surgery*; D006348:Cardiac Surgical Procedures / Q000379:methods*; D003452:Cryosurgery; D004535:Ehlers-Danlos Syndrome / Q000601:surgery*; D006801:Humans; D008297:Male; D008875:Middle Aged; D008944:Mitral Valve Insufficiency / Q000209:etiology / Q000601:surgery*