Von Recklinghausen's disease with urogenital manifestation.
Neurofibromatosis or Von Recklinghausen's disease is a rare disease that affects the urogenital system in its visceral form. We report on one case where the patient had a recurring mass located in the vesicouterine space that caused irritative urinary symptoms, which was confirmed as uterine cervix neurofibroma following surgery and immunohistochemical study. We stress the importance of a wide resection of such tumors and the need for long-term follow-up due to the high recurrence index and the risk of malignant transformation.
Nunes
Thiago F
TF
Amaral Carvalho Hospital, Jau, São Paulo, Brazil. thiago@hnet.com.br
Costa
Renato P
RP
Navarro
Fabio C
FC
D000328:Adult; D005260:Female; D006801:Humans; D007150:Immunohistochemistry; D009456:Neurofibromatosis 1 / Q000150:complications* / Q000473:pathology; D012008:Recurrence; D002583:Uterine Cervical Neoplasms / Q000473:pathology / Q000601:surgery*