title: Pseudoexstrophy with epispadias.
abstract: The exstrophy variants are uncommon anomalies. The variants of the exstrophy complex have all the stigmata of the classical exstrophy such as divergent recti, widened symphysis pubis, and low-set umbilicus; however, the urinary tract is intact to a varying degree. Pseudoexstrophy, an exstrophy variant, is very rarely associated with epispadias. We report an unusual case of pseudoexstrophy with epispadias, in whom the intact bladder was initially covered by a mucous membrane which later epithelialized. The epispadias was repaired using a penile disassembly technique with posterior and ventral placement of bladder neck and urethra. Although the urethral meatus was hypospadiac, the child had achieved dry intervals with occasional stress incontinence.
authors.affiliation: Department of Pediatric Surgery, Advanced Pediatric Center, Postgraduate Institute of Medical Education and Research (PGIMER), Chandigarh, India. jkmahajanjk@sify.com
authors.forename: J K
authors.initials: JK
authors.lastname: Mahajan
authors.forename: Sunita
authors.initials: S
authors.lastname: Ojha
authors.forename: K L N
authors.initials: KL
authors.lastname: Rao
mesh_terms: D001746:Bladder Exstrophy / Q000145:classification / Q000150:complications / Q000601:surgery*; D004842:Epispadias / Q000150:complications / Q000601:surgery*; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D016896:Treatment Outcome; D013521:Urologic Surgical Procedures, Male / Q000379:methods*