title: Clinical response to sildenafil in pulmonary hypertension associated with Gaucher disease.
abstract: There are few reports of pulmonary hypertension in Gaucher disease. We report a patient who showed significant clinical improvement after treatment with sildenafil.
authors.affiliation: Pulmonary Division, Pulmonary Hypertension Unit, University of São Paulo Medical School, Brazil.
authors.forename: C J C
authors.initials: CJ
authors.lastname: Fernandes
authors.forename: C
authors.initials: C
authors.lastname: Jardim
authors.forename: L A S
authors.initials: LA
authors.lastname: Carvalho
authors.forename: A Q
authors.initials: AQ
authors.lastname: Farias
authors.forename: M Terra
authors.initials: MT
authors.lastname: Filho
authors.forename: R
authors.initials: R
authors.lastname: Souza
mesh_terms: D000328:Adult; D004452:Echocardiography; D005260:Female; D005776:Gaucher Disease / Q000188:drug therapy*; D006801:Humans; D006976:Hypertension, Pulmonary / Q000188:drug therapy / Q000473:pathology*; D010879:Piperazines / Q000494:pharmacology / Q000627:therapeutic use*; D011687:Purines; D000068677:Sildenafil Citrate; D013450:Sulfones; D016896:Treatment Outcome; D014665:Vasodilator Agents / Q000494:pharmacology / Q000627:therapeutic use*
chemical_list: D010879:Piperazines; D011687:Purines; D013450:Sulfones; D014665:Vasodilator Agents; D000068677:Sildenafil Citrate