Successful liver transplantation for congenital absence of the portal vein complicated by intrapulmonary shunt and brain abscess.
A 27-day-old boy had convulsion associated with brain abscesses and severe hypoxemia at the age of 3 months. Congenital absence of the portal vein (CAPV) and some associated anomalies were detected by radiological examinations. Brain abscess and hypoxemia were thought to be serious complications resulting from CAPV and were successfully corrected by living donor liver transplantation at the age of 4 months. This is the first report of a successful transplantation indicated for intrapulmonary shunt and brain abscess in an infant with CAPV.
Ohnishi
Yasuharu
Y
Department of Transplantation and Immunology, Kyoto University Faculty of Medicine, Kyoto 606-8507, Japan.
Ueda
Mikiko
M
Doi
Hiraku
H
Kasahara
Mureo
M
Haga
Hironori
H
Kamei
Hideya
H
Ogawa
Kohei
K
Ogura
Yasuhiro
Y
Yoshitoshi
Elena Y
EY
Tanaka
Koichi
K
D000015:Abnormalities, Multiple; D000900:Anti-Bacterial Agents / Q000627:therapeutic use; D001049:Apnea / Q000209:etiology; D001284:Atrophy; D001724:Birth Weight; D001921:Brain / Q000473:pathology; D001922:Brain Abscess / Q000188:drug therapy / Q000209:etiology / Q000601:surgery; D003131:Combined Modality Therapy; D004322:Drainage; D005865:Gestational Age; D006344:Heart Septal Defects, Atrial / Q000601:surgery; D006801:Humans; D006849:Hydrocephalus / Q000150:complications / Q000601:surgery; D000860:Hypoxia / Q000209:etiology; D007230:Infant, Low Birth Weight; D007231:Infant, Newborn; D007234:Infant, Premature; D007235:Infant, Premature, Diseases / Q000209:etiology / Q000601:surgery*; D016031:Liver Transplantation; D019520:Living Donors; D008297:Male; D008581:Meningitis / Q000150:complications; D011169:Portal Vein / Q000002:abnormalities*; D012640:Seizures / Q000209:etiology; D013154:Spleen / Q000002:abnormalities; D014682:Vena Cava, Inferior / Q000002:abnormalities; D017287:Ventriculoperitoneal Shunt
D000900:Anti-Bacterial Agents