title: Surgical aspects of intussusception secondary to Peutz-Jeghers syndrome.
abstract: Peutz-Jeghers syndrome (PJS) is a familial condition characterized by the presence of pigmented mucocutaneous spots and intestinal polyposis. Intussusception is the most frequent abdominal complication, but it is very rare. In our country, this is the second known report. In this article we present four cases of PJS associated with intussusception. All the patients were female and all underwent a surgical procedure. The intussusception was located in the ileum and colon. There are no more than 20 reported cases in the world where these two entities are associated. Children with PJS have a high risk of suffering from ileo-ileal or jejuno-ileal intussusception that will frequently require a special surgical procedure.
authors.affiliation: Academia Mexicana de Cirugía, UNAM, Departamento de Cirugía, Hospital Pediátrico Moctezuma, Mexico.
authors.forename: Carlos
authors.initials: C
authors.lastname: Baeza-Herrera
authors.forename: Luis Manuel
authors.initials: LM
authors.lastname: García-Cabello
authors.forename: Heladio M
authors.initials: HM
authors.lastname: Nájera-Garduño
authors.forename: Luis Angel
authors.initials: LA
authors.lastname: Sánchez-Fernández
authors.forename: Francisco
authors.initials: F
authors.lastname: Mora-Hernández
authors.forename: Alejandra I
authors.initials: AI
authors.lastname: Ortiz-Zúñiga
mesh_terms: D000293:Adolescent; D002648:Child; D002675:Child, Preschool; D005260:Female; D006801:Humans; D007077:Ileal Diseases / Q000000981:diagnostic imaging / Q000209:etiology* / Q000601:surgery*; D007080:Ileocecal Valve; D007081:Ileostomy; D007443:Intussusception / Q000000981:diagnostic imaging / Q000209:etiology* / Q000601:surgery*; D007579:Jejunal Diseases / Q000000981:diagnostic imaging / Q000209:etiology* / Q000601:surgery*; D007813:Laparotomy; D008297:Male; D010580:Peutz-Jeghers Syndrome / Q000150:complications*; D011860:Radiography, Abdominal; D016896:Treatment Outcome