title: Successful liver transplantation for congenital absence of the portal vein complicated by intrapulmonary shunt and brain abscess.
abstract: A 27-day-old boy had convulsion associated with brain abscesses and severe hypoxemia at the age of 3 months. Congenital absence of the portal vein (CAPV) and some associated anomalies were detected by radiological examinations. Brain abscess and hypoxemia were thought to be serious complications resulting from CAPV and were successfully corrected by living donor liver transplantation at the age of 4 months. This is the first report of a successful transplantation indicated for intrapulmonary shunt and brain abscess in an infant with CAPV.
authors.affiliation: Department of Transplantation and Immunology, Kyoto University Faculty of Medicine, Kyoto 606-8507, Japan.
authors.forename: Yasuharu
authors.initials: Y
authors.lastname: Ohnishi
authors.forename: Mikiko
authors.initials: M
authors.lastname: Ueda
authors.forename: Hiraku
authors.initials: H
authors.lastname: Doi
authors.forename: Mureo
authors.initials: M
authors.lastname: Kasahara
authors.forename: Hironori
authors.initials: H
authors.lastname: Haga
authors.forename: Hideya
authors.initials: H
authors.lastname: Kamei
authors.forename: Kohei
authors.initials: K
authors.lastname: Ogawa
authors.forename: Yasuhiro
authors.initials: Y
authors.lastname: Ogura
authors.forename: Elena Y
authors.initials: EY
authors.lastname: Yoshitoshi
authors.forename: Koichi
authors.initials: K
authors.lastname: Tanaka
mesh_terms: D000015:Abnormalities, Multiple; D000900:Anti-Bacterial Agents / Q000627:therapeutic use; D001049:Apnea / Q000209:etiology; D001284:Atrophy; D001724:Birth Weight; D001921:Brain / Q000473:pathology; D001922:Brain Abscess / Q000188:drug therapy / Q000209:etiology / Q000601:surgery; D003131:Combined Modality Therapy; D004322:Drainage; D005865:Gestational Age; D006344:Heart Septal Defects, Atrial / Q000601:surgery; D006801:Humans; D006849:Hydrocephalus / Q000150:complications / Q000601:surgery; D000860:Hypoxia / Q000209:etiology; D007230:Infant, Low Birth Weight; D007231:Infant, Newborn; D007234:Infant, Premature; D007235:Infant, Premature, Diseases / Q000209:etiology / Q000601:surgery*; D016031:Liver Transplantation; D019520:Living Donors; D008297:Male; D008581:Meningitis / Q000150:complications; D011169:Portal Vein / Q000002:abnormalities*; D012640:Seizures / Q000209:etiology; D013154:Spleen / Q000002:abnormalities; D014682:Vena Cava, Inferior / Q000002:abnormalities; D017287:Ventriculoperitoneal Shunt
chemical_list: D000900:Anti-Bacterial Agents