title: Nevus psiloliparus and aplasia cutis: a further possible example of didymosis.
abstract: Nevus psiloliparus is a distinct type of mesodermal nevus of the scalp characterized by absence or paucity of hair, and presence of an excessive amount of fatty tissue. It is considered a hallmark of encephalocraniocutaneous lipomatosis, a rare disorder comprising a variety of cutaneous, ophthalmologic, and neurologic defects. We report two infants with encephalocraniocutaneous lipomatosis with nevus psiloliparus on the scalp in close association with aplasia cutis congenita. This unusual association may be considered a further example of didymosis, for which we propose the term, didymosis aplasticopsilolipara.
authors.affiliation: Department of Dermatology, Hospital del Nino Jesús, Madrid, Spain. atorrelo@aedv.es
authors.forename: Antonio
authors.initials: A
authors.lastname: Torrelo
authors.forename: María del C
authors.initials: Mdel C
authors.lastname: Boente
authors.forename: Olga
authors.initials: O
authors.lastname: Nieto
authors.forename: Raúl
authors.initials: R
authors.lastname: Asial
authors.forename: Isabel
authors.initials: I
authors.lastname: Colmenero
authors.forename: Beatriz
authors.initials: B
authors.lastname: Winik
authors.forename: Antonio
authors.initials: A
authors.lastname: Zambrano
authors.forename: Rudolf
authors.initials: R
authors.lastname: Happle
mesh_terms: D000273:Adipose Tissue; D000505:Alopecia / Q000209:etiology; D003937:Diagnosis, Differential; D004476:Ectodermal Dysplasia / Q000150:complications / Q000175:diagnosis*; D005260:Female; D006801:Humans; D007223:Infant; D008297:Male; D009506:Nevus / Q000150:complications / Q000151:congenital / Q000175:diagnosis*; D012536:Scalp Dermatoses / Q000150:complications / Q000151:congenital / Q000175:diagnosis*