Surgical aspects of intussusception secondary to Peutz-Jeghers syndrome.
Peutz-Jeghers syndrome (PJS) is a familial condition characterized by the presence of pigmented mucocutaneous spots and intestinal polyposis. Intussusception is the most frequent abdominal complication, but it is very rare. In our country, this is the second known report. In this article we present four cases of PJS associated with intussusception. All the patients were female and all underwent a surgical procedure. The intussusception was located in the ileum and colon. There are no more than 20 reported cases in the world where these two entities are associated. Children with PJS have a high risk of suffering from ileo-ileal or jejuno-ileal intussusception that will frequently require a special surgical procedure.
Baeza-Herrera
Carlos
C
Academia Mexicana de Cirugía, UNAM, Departamento de Cirugía, Hospital Pediátrico Moctezuma, Mexico.
García-Cabello
Luis Manuel
LM
Nájera-Garduño
Heladio M
HM
Sánchez-Fernández
Luis Angel
LA
Mora-Hernández
Francisco
F
Ortiz-Zúñiga
Alejandra I
AI
D000293:Adolescent; D002648:Child; D002675:Child, Preschool; D005260:Female; D006801:Humans; D007077:Ileal Diseases / Q000000981:diagnostic imaging / Q000209:etiology* / Q000601:surgery*; D007080:Ileocecal Valve; D007081:Ileostomy; D007443:Intussusception / Q000000981:diagnostic imaging / Q000209:etiology* / Q000601:surgery*; D007579:Jejunal Diseases / Q000000981:diagnostic imaging / Q000209:etiology* / Q000601:surgery*; D007813:Laparotomy; D008297:Male; D010580:Peutz-Jeghers Syndrome / Q000150:complications*; D011860:Radiography, Abdominal; D016896:Treatment Outcome