[Unilateral auditory neuropathy. A rare differential diagnosis of unilateral deafness].
Auditory neuropathy presents with normal otoacoustic emissions combined with pathological findings in brainstem evoked response audiometry. Normally, the auditory neuropathy is bilateral. We report about a 9 year old child where we could diagnose a unilateral deafness in spite of regular TEOAE and DPOAE. No reproducible biosignals were seen when the right ear was stimulated with alternating click stimuli at a level of 80 dB. On the left side, the latency of the potentials was normal. A cranial MRI showed normal anatomy. In order to determine a unilateral deafness, objective tests (e.g., OAE, BERA) and subjective tests should be used.
Kothe
C
C
Klinik und Poliklinik für Hals-, Nasen- und Ohrenheilkunde, Universitätsklinikum Hamburg-Eppendorf, Hamburg, Germany. c.kothe@uke.uni-hamburg.de
Fleischer
S
S
Breitfuss
A
A
Hess
M
M
D001304:Auditory Diseases, Central / Q000150:complications* / Q000175:diagnosis*; D002648:Child; D003638:Deafness / Q000175:diagnosis* / Q000209:etiology*; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D035583:Rare Diseases / Q000175:diagnosis / Q000209:etiology