Freeman-Sheldon syndrome: dental and orthodontic implications.
The manifestations of the Freeman-Sheldon syndrome (FSS) in four members of a South African family of Xhosa stock have been documented. Orofacial manifestations are a major syndromic component and warrant early, specialized orthodontic intervention. Our protocol for dental management is outlined and suggestions for holistic oro-dental care are provided.
Roberts
T
T
Faculty of Dentistry, University of the Western Cape, Cape Town, South Africa.
Stephen
L
L
Naidoo
T
T
Fieggen
K
K
Beighton
P
P
D000328:Adult; D003729:Dental Care; D019066:Facies; D005260:Female; D006228:Hand Deformities, Congenital / Q000000981:diagnostic imaging; D006801:Humans; D007223:Infant; D019767:Maxillofacial Abnormalities / Q000000981:diagnostic imaging / Q000628:therapy*; D008865:Microstomia / Q000628:therapy*; D010347:Patient Care Planning; D011859:Radiography; D013577:Syndrome