Subaortic obstruction and complete atrioventricular block in Behçet's disease.
Left ventricular outflow tract obstruction may be dynamic, most commonly associated with hypertrophic cardiomyopathy, and, uncommonly, by congenital anomalies such as discrete subaortic stenosis. We describe a patient with Behçet's disease, presenting with a systolic murmur, fever, and syncope, in whom a diagnosis of subaortic obstruction caused by a pseudo-aneurysm dissecting the interventricular septum and associated with a complete atrioventricular block was made.
Unger
Philippe
P
Department of Cardiology, Erasme Hospital, Université Libre de Bruxelles, 808 route de Lennik, B-1070 Brussels, Belgium. punger@ulb.ac.be
de Cannière
Didier
D
Preumont
Nicolas
N
Fesler
Pierre
P
Cogan
Elie
E
D000328:Adult; D001528:Behcet Syndrome / Q000150:complications*; D021922:Discrete Subaortic Stenosis / Q000150:complications* / Q000000981:diagnostic imaging / Q000601:surgery; D017548:Echocardiography, Transesophageal; D004562:Electrocardiography; D005260:Female; D006327:Heart Block / Q000000981:diagnostic imaging / Q000209:etiology* / Q000601:surgery; D006801:Humans; D014694:Ventricular Outflow Obstruction / Q000000981:diagnostic imaging / Q000209:etiology* / Q000601:surgery