[Idiophatic mediastinal fibrosis: a case report].
We herein report a case of a male patient, who presented a mediastinal mass that had a slow growth over the years. After surgery, that made the diagnosis of idiopathic mediastinal fibrosis, the growth stabilized. Four years latter it was observed a substantial increase which lead to the inevitable compression of vital structures which, in turn, led to pulmonary hypertension. Idiopathic mediastinal fibrosis is an extremely rare pathology. There are same cases in which it is associated with other pathologies but has always a fatal prognosis when surgery is not an option.
Canotilho
Maria João
MJ
Interna de Pneumologia, Hospital de Santa Maria, Lisboa.
Sotto-Mayor
Renato
R
Teixeira
Encarnação
E
Manique
Alda
A
Bugalho de Almeida
A
A
D005355:Fibrosis / Q000175:diagnosis; D006801:Humans; D008297:Male; D008482:Mediastinum / Q000473:pathology*; D008875:Middle Aged