[Unusual association of chylopericardium and aortic hypoplasia in a neonate].
We report the case of a neonate with two very rare anomalies: primary chylopericardium and diffuse hypoplasia of the thoraco-abdominal aorta. The presentation on the 16th post-natal day was with dyspnoea and refusal to feed. The initial clinical examination revealed hepatomegaly and weak femoral pulses. 2D ultrasound gave a diagnosis of a large compressive pericardial effusion combined with moderate hypoplasia of the aortic isthmus. Emergency pericardial drainage removed 80ml of chylous liquid. Following prolonged parenteral nutrition, the pericardial effusion stabilised. A mechanism of diffuse vascular disease affecting the aorta and the lymphatic system is suggested.
Abadir
S
S
Unité de cardiologie pédiatrique médicale et chirurgicale, hôpital des Enfants, Toulouse, France.
Acar
P
P
De Maupeou
F
F
Baunin
C
C
Railhac
J J
JJ
Dulac
Y
Y
Taktak
A
A
Chilon
T
T
Mas
E
E
D001012:Aorta, Abdominal / Q000002:abnormalities* / Q000473:pathology*; D001013:Aorta, Thoracic / Q000002:abnormalities* / Q000473:pathology*; D004322:Drainage; D004452:Echocardiography; D006801:Humans; D007231:Infant, Newborn; D010288:Parenteral Nutrition; D010490:Pericardial Effusion / Q000473:pathology*; D016896:Treatment Outcome