Ichthyosiform mycosis fungoides: report of a case associated with IgA nephropathy.
We report a case of ichthyosiform mycosis fungoides (MF) associated with IgA nephropathy. Histological examination showed a dense atypical lymphocytic infiltrate admixed with epithelioid cells and giant cells in the dermis associated with the features of epidermotropism and folliculotropism. Reported cases of ichthyosiform MF are reviewed and histopathological characters of ichthyosiform MF are summarized. We suggest a histiocyte/dendritic-cell-rich infiltrate, or granulomatous features of infiltrate may be another characteristic of ichthyosiform MF. This case was associated with IgA nephropathy, which is uncommon. Such a presentation has never been reported in the literature.
Sato
Madoka
M
Department of Dermatology, Dokkyo University School of Medicine, Tochigi, Japan. satomad@excite.co.jp
Sohara
Masaaki
M
Kitamura
Yohei
Y
Hatamochi
Atsushi
A
Yamazaki
Soji
S
D000305:Adrenal Cortex Hormones / Q000627:therapeutic use; D001707:Biopsy, Needle; D003131:Combined Modality Therapy; D005922:Glomerulonephritis, IGA / Q000150:complications / Q000188:drug therapy / Q000473:pathology*; D006801:Humans; D007057:Ichthyosis / Q000473:pathology*; D007150:Immunohistochemistry; D008297:Male; D008875:Middle Aged; D009182:Mycosis Fungoides / Q000150:complications / Q000188:drug therapy / Q000473:pathology*; D011701:PUVA Therapy / Q000379:methods; D011379:Prognosis; D035583:Rare Diseases; D012720:Severity of Illness Index; D012878:Skin Neoplasms / Q000150:complications / Q000188:drug therapy / Q000473:pathology*; D016896:Treatment Outcome
D000305:Adrenal Cortex Hormones