title: Isolated left ventricular noncompaction of the myocardium as a cause of embolic superior mesenteric artery occlusion.
abstract: Isolated noncompaction of the left ventricular (LV) myocardium is a rare congenital disorder resulting from an arrest of the compaction process of the myocardial trabeculae during normal embryogenesis. It is characterized by the presence of prominent LV myocardial trabeculations and deep intertrabecular recesses that are in continuity with the LV cavity. The most common clinical presentation includes progressive LV dysfunction, life-threatening tachyarrhythmias, and the risk for severe cardioembolic events. We describe a case where isolated noncompaction of the LV myocardium was diagnosed after an embolic occlusion of the superior mesenteric artery in a 40-year-old Caucasian woman.
authors.affiliation: Department of Cardiology, University of Heidelberg, Heidelberg, Germany. erwin_blessing@med.uni-heidelberg.de
authors.forename: Erwin
authors.initials: E
authors.lastname: Blessing
authors.forename: Wolfgang
authors.initials: W
authors.lastname: Rottbauer
authors.forename: Derliz
authors.initials: D
authors.lastname: Mereles
authors.forename: Waldemar
authors.initials: W
authors.lastname: Hosch
authors.forename: Andreas
authors.initials: A
authors.lastname: Benz
authors.forename: Helmut
authors.initials: H
authors.lastname: Friess
authors.forename: Frank
authors.initials: F
authors.lastname: Autschbach
authors.forename: Martina
authors.initials: M
authors.lastname: Müller
authors.forename: Wolfgang
authors.initials: W
authors.lastname: Stremmel
authors.forename: Hugo
authors.initials: H
authors.lastname: Katus
mesh_terms: D000328:Adult; D001157:Arterial Occlusive Diseases / Q000000981:diagnostic imaging* / Q000209:etiology; D004617:Embolism / Q000000981:diagnostic imaging* / Q000209:etiology; D005260:Female; D006352:Heart Ventricles / Q000002:abnormalities* / Q000000981:diagnostic imaging*; D006801:Humans; D017379:Hypertrophy, Left Ventricular / Q000150:complications / Q000151:congenital / Q000000981:diagnostic imaging; D017538:Mesenteric Artery, Superior / Q000000981:diagnostic imaging*; D014463:Ultrasonography; D018487:Ventricular Dysfunction, Left / Q000150:complications / Q000151:congenital* / Q000000981:diagnostic imaging*