New dental findings in the median cleft facial syndrome.
BACKGROUND
The main features of median cleft facial syndrome are hypertelorism, cranium bifidum occultum, widow's peak, and midine clefting of the nose, upper lip and palate. Since this pathology was first described in 1967, many cases have been reported in the literature, but none of these reports has addressed oral anomalies in depth.


METHODS
The authors present the case of a female patient aged 4 years and 7 months who was diagnosed with median cleft facial syndrome. In this case, the patient had an abnormal number of teeth, owing to fusion or agenesis of teeth, supernumerary teeth and ectopic eruption of some teeth. These oral anomalies had not been described before in the literature as being associated with this syndrome.


CONCLUSIONS
Median cleft facial syndrome is a rare pathology; however, dentists should know its possible alterations at an oral level, because children with this syndrome need dental treatment to achieve good esthetics and correct occlusion.
Haro Montero
Manuela M
MM
Department of Children's Dental Clinics, Dental School, University of Murcia, Spain. manuelaharo@hotmail.com
Romero Maroto
Martin
M
Bravo Gonzalez
Luis Alberto
LA
Sanchez del Pozo
Jaime
J
D000848:Anodontia / Q000209:etiology*; D002675:Child, Preschool; D019465:Craniofacial Abnormalities / Q000150:complications*; D005260:Female; D005671:Fused Teeth / Q000209:etiology*; D006801:Humans; D006972:Hypertelorism / Q000150:complications; D009666:Nose / Q000002:abnormalities; D013577:Syndrome; D014079:Tooth Eruption, Ectopic / Q000209:etiology*; D014096:Tooth, Supernumerary / Q000209:etiology*