title: Respiratory management of the infant with type 1 spinal muscular atrophy.
abstract: A recent paper has highlighted the differences in the respiratory management offered to infants with type 1 spinal muscular atrophy (SMA-1). Current views appear polarised between those who would offer nothing, to those who would proceed as far even as tracheostomy and long term invasive ventilation for these infants. Here we offer a personal view, as a possible template for managing a vexed and emotional problem. The complex non-respiratory aspects of the holistic care of these infants will not be discussed.
authors.affiliation: Royal Brompton Hospital, Sydney Street, London SW3 6NP, UK. a.bush@rbh.nthames.nhs.uk
authors.forename: A
authors.initials: A
authors.lastname: Bush
authors.forename: J
authors.initials: J
authors.lastname: Fraser
authors.forename: E
authors.initials: E
authors.lastname: Jardine
authors.forename: J
authors.initials: J
authors.lastname: Paton
authors.forename: A
authors.initials: A
authors.lastname: Simonds
authors.forename: C
authors.initials: C
authors.lastname: Wallis
mesh_terms: D006801:Humans; D007223:Infant; D009134:Muscular Atrophy, Spinal / Q000150:complications* / Q000628:therapy; D011175:Positive-Pressure Respiration; D011368:Professional-Family Relations; D012121:Respiration, Artificial / Q000379:methods*; D012131:Respiratory Insufficiency / Q000209:etiology* / Q000628:therapy*