title: [Outcome of 30 congenital atrio-ventricular blocks].
abstract: Congenital isolated atrio-ventricular block (CAVB) is a rare pathology, and its management is still rather poorly described through international literature. Within the service of pediatric cardiology leaded by Pr Choussat and Dr Jimenez (Cardiologic Hospital Haut-Lévêque of Bordeaux), we collected from 1980 to 2003, 30 isolated congenital CAVB, constituting the purpose of this retrospective study. Average follow-up is 14 +/- 8.8 years. None death occurred. CAVB are discovered at an average age of 4.8 years old; 6 cases were diagnosed in utero, half of them were associated with maternal lupus. Twenty patients on 30 were fitted with stimulator at an average age of 8.7 +/- 6.9 years old, due to symptoms or bradycardy. Epicardic fitting in VVI mode represents 65% of first approaches, it is followed by endocavitary way for 81% of cases. Cardiac stimulation does not prevent from dilated cardiomyopathy. Among 30 patients 10 were not fitted with stimulator, half of them presents chronotrop insufficiency during effort. As a conclusion, our patients show a good long-term vital prognosis; although CAVB discovered in utero lead to worse prognosis for children.
authors.affiliation: Hôpital d'instruction des armées R. Picqué, Bordeaux.
authors.forename: F
authors.initials: F
authors.lastname: Verdier
authors.forename: M
authors.initials: M
authors.lastname: Jimenez
authors.forename: J M
authors.initials: JM
authors.lastname: Chevalier
authors.forename: J B
authors.initials: JB
authors.lastname: Thambo
authors.forename: F
authors.initials: F
authors.lastname: Bire
authors.forename: J
authors.initials: J
authors.lastname: Clémenty
authors.forename: A
authors.initials: A
authors.lastname: Choussat
mesh_terms: D000293:Adolescent; D000328:Adult; D002311:Cardiomyopathy, Dilated / Q000209:etiology; D002648:Child; D002675:Child, Preschool; D005260:Female; D006327:Heart Block / Q000150:complications / Q000151:congenital* / Q000628:therapy*; D006801:Humans; D008177:Lupus Vulgaris / Q000150:complications; D008297:Male; D010138:Pacemaker, Artificial; D011296:Prenatal Diagnosis; D011379:Prognosis; D012189:Retrospective Studies; D012307:Risk Factors; D016896:Treatment Outcome