title: [Unusual association of chylopericardium and aortic hypoplasia in a neonate].
abstract: We report the case of a neonate with two very rare anomalies: primary chylopericardium and diffuse hypoplasia of the thoraco-abdominal aorta. The presentation on the 16th post-natal day was with dyspnoea and refusal to feed. The initial clinical examination revealed hepatomegaly and weak femoral pulses. 2D ultrasound gave a diagnosis of a large compressive pericardial effusion combined with moderate hypoplasia of the aortic isthmus. Emergency pericardial drainage removed 80ml of chylous liquid. Following prolonged parenteral nutrition, the pericardial effusion stabilised. A mechanism of diffuse vascular disease affecting the aorta and the lymphatic system is suggested.
authors.affiliation: Unité de cardiologie pédiatrique médicale et chirurgicale, hôpital des Enfants, Toulouse, France.
authors.forename: S
authors.initials: S
authors.lastname: Abadir
authors.forename: P
authors.initials: P
authors.lastname: Acar
authors.forename: F
authors.initials: F
authors.lastname: De Maupeou
authors.forename: C
authors.initials: C
authors.lastname: Baunin
authors.forename: J J
authors.initials: JJ
authors.lastname: Railhac
authors.forename: Y
authors.initials: Y
authors.lastname: Dulac
authors.forename: A
authors.initials: A
authors.lastname: Taktak
authors.forename: T
authors.initials: T
authors.lastname: Chilon
authors.forename: E
authors.initials: E
authors.lastname: Mas
mesh_terms: D001012:Aorta, Abdominal / Q000002:abnormalities* / Q000473:pathology*; D001013:Aorta, Thoracic / Q000002:abnormalities* / Q000473:pathology*; D004322:Drainage; D004452:Echocardiography; D006801:Humans; D007231:Infant, Newborn; D010288:Parenteral Nutrition; D010490:Pericardial Effusion / Q000473:pathology*; D016896:Treatment Outcome