title: Four different airway-management strategies in patient with Launois-Bensaude syndrome or Madelung's disease undergoing surgical excision of neck lipomatosis with a complicated postoperative course.
abstract: Launois-Bensaude syndrome, otherwise known as Madelung's disease, is a rare disorder characterized by fatty accumulations of the upper trunk, neck and head, causing serious cosmetic deformity and neck immobility. We report a case of a patient with Launois-Bensaude syndrome who required 4 different airway management strategies during his hospitalization for postoperative complications after an elective surgical excision of a severe neck lipomatosis. Anesthesiologists who treat patients with Madelung's disease should be aware of 2 major problems: difficult airway and increased frequency of postoperative bleeding. A proper choice of airway management technique is therefore necessary, including a safe intubation and extubation plan to reduce the consequences of airway complications.
authors.affiliation: Department of Anesthesiology, Institute of Oncology, 1000 Ljubljana, Slovenia. tstopar@onko-i.si
authors.forename: Tatjana
authors.initials: T
authors.lastname: Stopar
authors.forename: Vesna
authors.initials: V
authors.lastname: Novak Jankovic
authors.forename: Andrea
authors.initials: A
authors.lastname: Casati
mesh_terms: D006801:Humans; D007442:Intubation, Intratracheal / Q000379:methods*; D017214:Laryngeal Masks; D008069:Lipomatosis, Multiple Symmetrical / Q000601:surgery*; D008297:Male; D008875:Middle Aged; D019106:Postoperative Hemorrhage / Q000209:etiology*