Isolated left-sided scimitar vein connecting all left pulmonary veins to the right inferior vena cava.
When the common pulmonary vein fails to develop, the embryonic connections of the pulmonary veins to one or more of the systemic veins almost always persist. Anomalous pulmonary venous connections to the inferior vena cava (IVC) are typically characterized by hypoplasia of the involved pulmonary veins and pulmonary artery, as well as abnormal parenchyma of the involved lung. Such cases have been described as "scimitar syndrome." We report the case of a young female patient in whom all the left pulmonary veins converged into a common vessel that drained into the IVC but who had a normal left pulmonary artery and left lung. Surgical intervention was successful, and our patient is still alive.
Department of Pathology, Children's Hospital Boston, 300 Longwood Avenue, Boston, MA 02115, USA.
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AL
Juraszek
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H
Cohn
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R
Van Praagh
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S
Van Praagh
D000328:Adult; D000714:Anastomosis, Surgical; D005260:Female; D006330:Heart Defects, Congenital / Q000000981:diagnostic imaging / Q000601:surgery*; D006801:Humans; D018810:Magnetic Resonance Angiography; D011667:Pulmonary Veins / Q000002:abnormalities* / Q000601:surgery; D011859:Radiography; D012587:Scimitar Syndrome / Q000000981:diagnostic imaging / Q000601:surgery*; D014682:Vena Cava, Inferior / Q000002:abnormalities* / Q000601:surgery