[Small round cell desmoplastic tumour presenting as a testicular mass].
The authors report a case of small round cell desmoplastic tumour presenting as a testicular mass. This is a rare tumour arising from serosal tissues, especially the tunica vaginalis. It is characterized by a specific reciprocal translocation t(11;22) (p13;q12) inducing fusion of the EWS and WT1 genes. Treatment of this tumour consists of a combination of surgical resection, as complete as possible, and intensive chemotherapy (P6 protocol or Institut Gustave Roussy protocol) and possibly radiotherapy. However, the prognosis remains very poor.
Clinique urologique, CHU de Nantes, France. simbattisti@club-internet.fr
Simon
S
Battisti
Karine
K
Renaudin
Jérôme
J
Rigaud
Jean-François
JF
Hetet
Guillaume
G
Braud
Jean
J
Kapfer
Annick
A
Vieillefond
Olivier
O
Bouchot
D000328:Adult; D006801:Humans; D008297:Male; D013736:Testicular Neoplasms / Q000473:pathology* / Q000628:therapy