Nitric oxide in pulmonary arteriovenous malformations and Fontan procedure.
Pulmonary arteriovenous malformations are a well documented complication of superior cavopulmonary (Glenn) connections. We report the successful management of a case of severe hypoxemia in the early postoperative period of a patient who underwent the Fontan operation. The patient had previously been diagnosed with pulmonary arteriovenous malformations; the use of inhaled nitric oxide was followed up with reversal of life-threatening hypoxemia. At 6-month postoperative follow-up, the patient was asymptomatic with near normal aortic saturation.
Department of Pediatrics, Pontificial Catholic University of Chile, Santiago, Chile. gurcelay@manquehue.net
Gonzalo E
GE
Urcelay
Arturo J
AJ
Borzutzky
Pedro A
PA
Becker
Maria E
ME
Castillo
D000015:Abnormalities, Multiple; D000280:Administration, Inhalation; D001165:Arteriovenous Malformations / Q000150:complications*; D018376:Cardiovascular Abnormalities; D013504:Cardiovascular Surgical Procedures; D002675:Child, Preschool; D005260:Female; D018729:Fontan Procedure / Q000009:adverse effects*; D006801:Humans; D000860:Hypoxia / Q000209:etiology / Q000628:therapy; D009569:Nitric Oxide / Q000008:administration & dosage*; D011651:Pulmonary Artery / Q000002:abnormalities; D013577:Syndrome; D014665:Vasodilator Agents / Q000008:administration & dosage*
D014665:Vasodilator Agents; D009569:Nitric Oxide