[Small round cell desmoplastic tumour presenting as a testicular mass].
The authors report a case of small round cell desmoplastic tumour presenting as a testicular mass. This is a rare tumour arising from serosal tissues, especially the tunica vaginalis. It is characterized by a specific reciprocal translocation t(11;22) (p13;q12) inducing fusion of the EWS and WT1 genes. Treatment of this tumour consists of a combination of surgical resection, as complete as possible, and intensive chemotherapy (P6 protocol or Institut Gustave Roussy protocol) and possibly radiotherapy. However, the prognosis remains very poor.
Battisti
Simon
S
Clinique urologique, CHU de Nantes, France. simbattisti@club-internet.fr
Renaudin
Karine
K
Rigaud
Jérôme
J
Hetet
Jean-François
JF
Braud
Guillaume
G
Kapfer
Jean
J
Vieillefond
Annick
A
Bouchot
Olivier
O
D000328:Adult; D006801:Humans; D008297:Male; D013736:Testicular Neoplasms / Q000473:pathology* / Q000628:therapy