title: Rhabdomyosarcoma arising within congenital cystic adenomatoid malformation.
abstract: Rhabdomyosarcoma arising within a congenital cystic adenomatoid malformation (CCAM) is an unusual entity. The patient underwent a lobectomy of his right lower lobe of lung due to a CCAM at the age of two. One year later, he developed a solid embryonal rhabdomyosarcoma at the same location. He received 1-year period chemotherapy and when the tumor reduced to a resectable size, surgical excision was done. The tumor cells appeared more differentiated after chemotherapy. The patient remains disease free to date, 16 months after surgery.
authors: Department of Pathology, Kaohsiung Medical Center, Chang Gung University and Memorial Hospital, Kaohsiung, Taiwan. shyunpai@cgmh.org.tw
authors: Shyun
authors: S
authors: Pai
authors: Hock-Liew
authors: HL
authors: Eng
authors: Shin-Yi
authors: SY
authors: Lee
authors: Chih-Cheng
authors: CC
authors: Hsiao
authors: Wan-Ting
authors: WT
authors: Huang
authors: Shun-Chen
authors: SC
authors: Huang
mesh_terms: D000971:Antineoplastic Combined Chemotherapy Protocols / Q000627:therapeutic use; D002675:Child, Preschool; D015615:Cystic Adenomatoid Malformation of Lung, Congenital / Q000150:complications*; D018572:Disease-Free Survival; D006801:Humans; D008175:Lung Neoplasms / Q000209:etiology / Q000473:pathology / Q000628:therapy; D008297:Male; D012208:Rhabdomyosarcoma / Q000188:drug therapy / Q000209:etiology* / Q000473:pathology