Right ventricular noncompaction in a neonate with complex congenital heart disease.
Ventricular noncompaction is a rare unclassified cardiomyopathy occurring because of arrest of the normal intrauterine compaction of the loose luminal component of the ventricular myocardium. There is limited data regarding its diagnosis and outcome in children. It is recognised, however, that right ventricular involvement is extremely rare. We report a case in which only the right ventricular myocardium was noncompacted, a situation which led to heart failure soon after birth.
Alehan
Dursun
D
Division of Pediatric Cardiology, Hacettepe University Faculty of Medicine, Sihhiye, Ankara, Turkey.
Dogan
Omer Faruk
OF
D004452:Echocardiography; D017809:Fatal Outcome; D005260:Female; D005500:Follow-Up Studies; D006330:Heart Defects, Congenital / Q000150:complications* / Q000175:diagnosis / Q000503:physiopathology; D006333:Heart Failure / Q000175:diagnosis / Q000209:etiology* / Q000503:physiopathology; D006352:Heart Ventricles / Q000002:abnormalities* / Q000000981:diagnostic imaging; D006801:Humans; D007231:Infant, Newborn; D013902:Radiography, Thoracic; D018497:Ventricular Dysfunction, Right / Q000150:complications* / Q000175:diagnosis / Q000503:physiopathology; D017725:Ventricular Pressure