title: [A child with pulmonary hypertension: from etiological study to therapeutic decisions].
abstract: Pulmonary hypertension is a rare but devastating disease, with poor prognosis and high mortality. The disease may present as Primary Pulmonary Hypertension where no clear aetiology can be identified, or be related to a variety of underlying conditions. This is a rare disease in paediatric age. The authors present the clinical case of a 4 years old child, admitted in Paediatric Department of S. João Hospital for syncope episode. The diagnosis of pulmonary hypertension was made by echocardiogram. Ulterior studies revealed pulmonary disease (obliterans bronchiolitis). The treatment included a calcium channel blocker (diltiazem), an endothelin antagonist (bosentan) and supplemental oxygen. This is the first case of obliterans bronchiolitis diagnosed during etiological study for pulmonary hypertension, in our Pediatrics Department. In this case we could not determine the pulmonary disease precipitating event.
authors: Interna Complementar de Pediatria - Serviço de Pediatria, Hospital de S. João. mguardiano@hotmail.com
authors: Micaela
authors: M
authors: Guardiano
authors: Ana Maria
authors: AM
authors: Maia
authors: Cíntia
authors: C
authors: Correia
authors: Inês
authors: I
authors: Azevedo
authors: Ana Rosa
authors: AR
authors: Lopes
authors: Eduardo Dias
authors: ED
authors: da Silva
authors: Conceição Souto
authors: CS
authors: Moura
authors: António
authors: A
authors: Marinho
mesh_terms: D001989:Bronchiolitis Obliterans / Q000150:complications* / Q000473:pathology; D002675:Child, Preschool; D005260:Female; D006801:Humans; D006976:Hypertension, Pulmonary / Q000188:drug therapy / Q000209:etiology* / Q000473:pathology