Sturge Weber syndrome.
A variant of hemangioma and an uncommon congenital condition, the Sturge Weber syndrome (SWS), also called encephalo trigeminal angiomatosis, is a neurocutaneous disorder with angiomas involving the skin of the face (cutaneous angioma) and pia arachnoid (leptomeningeal angioma). It occurs typically in the ophthalmic and maxillary distributions of the trigeminal nerve (1,2). Here we present a case of a 14 year old girl.
Dorothy
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A
Department of Oral Pathology and Microbiology, College of Dental Surgery, Kasturba Medical College, Mangalore. dorothyaithal@yahoo.com
Kamboj
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Reddy
B S
BS
Mahajan
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Boaz
K
K
D000293:Adolescent; D005153:Facial Neoplasms / Q000473:pathology; D005260:Female; D019214:Gingival Overgrowth / Q000473:pathology; D006801:Humans; D012535:Scalp / Q000473:pathology; D012878:Skin Neoplasms / Q000473:pathology; D013341:Sturge-Weber Syndrome / Q000175:diagnosis* / Q000473:pathology