Rhabdomyosarcoma arising within congenital cystic adenomatoid malformation.
Rhabdomyosarcoma arising within a congenital cystic adenomatoid malformation (CCAM) is an unusual entity. The patient underwent a lobectomy of his right lower lobe of lung due to a CCAM at the age of two. One year later, he developed a solid embryonal rhabdomyosarcoma at the same location. He received 1-year period chemotherapy and when the tumor reduced to a resectable size, surgical excision was done. The tumor cells appeared more differentiated after chemotherapy. The patient remains disease free to date, 16 months after surgery.
Pai
Shyun
S
Department of Pathology, Kaohsiung Medical Center, Chang Gung University and Memorial Hospital, Kaohsiung, Taiwan. shyunpai@cgmh.org.tw
Eng
Hock-Liew
HL
Lee
Shin-Yi
SY
Hsiao
Chih-Cheng
CC
Huang
Wan-Ting
WT
Huang
Shun-Chen
SC
D000971:Antineoplastic Combined Chemotherapy Protocols / Q000627:therapeutic use; D002675:Child, Preschool; D015615:Cystic Adenomatoid Malformation of Lung, Congenital / Q000150:complications*; D018572:Disease-Free Survival; D006801:Humans; D008175:Lung Neoplasms / Q000209:etiology / Q000473:pathology / Q000628:therapy; D008297:Male; D012208:Rhabdomyosarcoma / Q000188:drug therapy / Q000209:etiology* / Q000473:pathology