[Superior-canal dehiscence syndrome].
Superior-canal dehiscence syndrome (SCDS) was first described in 1998; it manifests as symptoms of dizziness and oscillopsia when a sound or pressure stimulus is given to the ear concerned. SCDS is caused by dehiscence ofpetrosal bone overlying the superior, vertical semicircular canal, creating a 'third mobile window' to the labyrinth, in addition to the oval and round windows. Characteristic for this syndrome are eye movements with a vertical-torsion direction, evoked by sound stimuli, or pressure changes via the external ear canal and the Valsalva manoeuvre. The anomaly of the bony structure is visible on a CT scan. With its specific symptoms and characteristics, SCDS is an abnormality of the vestibular system that is relatively easy to diagnose. The syndrome may be treated with conservative or surgical means.
Goumans
J
J
Afd. Keel-, Neus- en Oorheelkunde, Erasmus MC, Postbus 2040, 3000 CA Rottterdam. j.goumans@erasmusmc.nl
Boumans
L J J M
LJ
van der Steen
J
J
Feenstra
L
L
D004432:Ear, Middle / Q000503:physiopathology; D006801:Humans; D007427:Intracranial Pressure; D009759:Nystagmus, Pathologic / Q000209:etiology* / Q000503:physiopathology; D012665:Semicircular Canals / Q000000981:diagnostic imaging / Q000473:pathology*; D013016:Sound; D013577:Syndrome; D014057:Tomography, X-Ray Computed; D014717:Vertigo / Q000209:etiology* / Q000503:physiopathology; D014786:Vision Disorders / Q000209:etiology* / Q000503:physiopathology