Cystoid macular edema in gyrate atrophy of the choroid and retina: a fluorescein angiography and optical coherence tomography evaluation.
OBJECTIVE
To analyze the importance f optical coherence tomography (OCT) to diagnose the cystoid macular edema in a case of gyrate atrophy.


METHODS
Observational case report.


METHODS
A 12-year-old boy presenting with gyrate atrophy of the choroid and retina underwent ophthalmologic, clinical, and laboratory tests.


RESULTS
Plasma ornithine level was 735 mumol/l. Fluorescein angiography showed bilateral hyperfluorescence involving the central region of the macula. Optical coherence tomography (OCT) disclosed bilateral intraretinal cysts areas of low reflectivity with occasional high-signal elements bridging the retinal layers and intraretinal thickening.


CONCLUSIONS
Both fluorescein angiography and OCT were helpful to confirm the diagnosis of macular involvement as a complication of gyrate atrophy of the choroid and retina in a patient who presented without any clinical evidence of cystoid macular edema, except a decrease in visual acuity.
Oliveira
Tâmara L
TL
Vision Institute-IPEPO, Department of Ophthalmology, Federal University of São Paulo, Brazil.
Andrade
Rafael E
RE
Muccioli
Cristina
C
Sallum
Juliana
J
Belfort
Rubens
R
D002648:Child; D002829:Choroid / Q000473:pathology*; D005451:Fluorescein Angiography / Q000379:methods; D015799:Gyrate Atrophy / Q000150:complications* / Q000175:diagnosis; D006801:Humans; D008269:Macular Edema / Q000175:diagnosis* / Q000209:etiology*; D008297:Male; D009952:Ornithine / Q000097:blood; D012160:Retina / Q000473:pathology*; D041623:Tomography, Optical Coherence / Q000379:methods
D009952:Ornithine