title: Multiple intrahepatic vascular shunts causing hyperammoniaemic encephalopathy in a patient without liver cirrhosis.
abstract: The very rare case of a non-cirrhotic patient with multiple intrahepatic portosystemic and arteriosystemic vascular shunts, presenting with hyperammoniaemic type B encephalopathy and hypoalbuminaemia due to proteinuria, is reported. The correct diagnosis, suspected by abdominal ultrasound and colour-Doppler imaging, was confirmed by hepatic and superior mesenteric angiography. A comparison with the few similar cases existing in the literature is offered.
authors.affiliation: Gastrointestinal Unit, Belcolle Hospital, Strada Sammartinese, 01100 Viterbo, Italy. e.caturelli@tiscalinet.it
authors.forename: E
authors.initials: E
authors.lastname: Caturelli
authors.forename: G
authors.initials: G
authors.lastname: Ghittoni
authors.forename: G A
authors.initials: GA
authors.lastname: Niro
authors.forename: R
authors.initials: R
authors.lastname: Clemente
authors.forename: L
authors.initials: L
authors.lastname: Accadia
authors.forename: M
authors.initials: M
authors.lastname: Nardella
authors.forename: A
authors.initials: A
authors.lastname: Andriulli
authors.forename: M
authors.initials: M
authors.lastname: Anti
mesh_terms: D000368:Aged; D000792:Angiography; D006499:Hepatic Artery / Q000000981:diagnostic imaging; D006501:Hepatic Encephalopathy / Q000150:complications* / Q000000981:diagnostic imaging*; D006801:Humans; D022124:Hyperammonemia / Q000000981:diagnostic imaging* / Q000209:etiology*; D008103:Liver Cirrhosis; D008297:Male; D017538:Mesenteric Artery, Superior / Q000000981:diagnostic imaging; D011169:Portal Vein / Q000000981:diagnostic imaging; D018615:Ultrasonography, Doppler, Color