title: Coarctation of the thoraco-abdominal aorta associated with mucopolysaccharidosis VII in a child.
abstract: Herein we describe a case of atypical coarctation of the thoraco-abdominal aorta associated with mucopolysaccharidosis VII in a 4-year-old girl. Aortography showed diffuse narrowing of the descending aorta. An extra-anatomic bypass was constructed using an 8-mm Dacron graft (Meadox Medicals Inc, Oakland, NJ) between the proximal and distal portion of the descending aorta. Balloon angioplasty was necessary to treat stenoses in the infrarenal abdominal aorta. Two years postoperatively at age 6, aortography revealed no stenosis at the anastomotic sites or in the prosthesis, but the hypoplastic segment of the descending aorta between the anstomoses was completely occluded.
authors.affiliation: Department of Cardiovascular Surgery, Okayama University Graduate School of Medicine and Dentistry, Okayama City, Japan.
authors.forename: Osami
authors.initials: O
authors.lastname: Honjo
authors.forename: Kozo
authors.initials: K
authors.lastname: Ishino
authors.forename: Masaaki
authors.initials: M
authors.lastname: Kawada
authors.forename: Shin-Ichi
authors.initials: S
authors.lastname: Ohtsuki
authors.forename: Shunji
authors.initials: S
authors.lastname: Sano
mesh_terms: D000800:Angioplasty, Balloon; D001017:Aortic Coarctation / Q000150:complications* / Q000601:surgery; D019917:Blood Vessel Prosthesis Implantation; D002675:Child, Preschool; D005260:Female; D006801:Humans; D016538:Mucopolysaccharidosis VII / Q000150:complications*