Arthrogryposis multiplex congenita.
Since much confusion exists regarding arthrogryposis multiplex congenita (AMC), the President of the IFSSH commissioned the AMC Committee to compile a report on the various aspects of this condition. This report discusses all the facets of AMC, including definition, terminology, dermographics, aetiology, classification, clinical features, management, prognosis and further studies. Manipulation of the deformities starting soon after birth improves the range of motion, which, if surgery needs to be done, makes the operation less extensive. Sometimes surgery may not even be necessary. Early one-stage corrective surgery between 3 and 12 months of age is encouraged. This results in improved function and near normal cosmetic appearance. Late, piece-meal surgery results in disappointing outcome.
Mennen
Ulrich
U
Department of Hand Surgery, Medical University of South Africa, Pretoria, South Africa. umennen@icon.co.za
van Heest
Ann
A
Ezaki
Mary-Beth
MB
Tonkin
Michael
M
Gericke
George
G
D001176:Arthrogryposis / Q000145:classification / Q000175:diagnosis / Q000209:etiology* / Q000601:surgery*; D006801:Humans; D019637:Orthopedic Procedures; D011379:Prognosis; D009626:Terminology as Topic