title: Cystoid macular edema in gyrate atrophy of the choroid and retina: a fluorescein angiography and optical coherence tomography evaluation.
abstract: OBJECTIVE
  To analyze the importance f optical coherence tomography (OCT) to diagnose the cystoid macular edema in a case of gyrate atrophy.
  
  
  METHODS
  Observational case report.
  
  
  METHODS
  A 12-year-old boy presenting with gyrate atrophy of the choroid and retina underwent ophthalmologic, clinical, and laboratory tests.
  
  
  RESULTS
  Plasma ornithine level was 735 mumol/l. Fluorescein angiography showed bilateral hyperfluorescence involving the central region of the macula. Optical coherence tomography (OCT) disclosed bilateral intraretinal cysts areas of low reflectivity with occasional high-signal elements bridging the retinal layers and intraretinal thickening.
  
  
  CONCLUSIONS
  Both fluorescein angiography and OCT were helpful to confirm the diagnosis of macular involvement as a complication of gyrate atrophy of the choroid and retina in a patient who presented without any clinical evidence of cystoid macular edema, except a decrease in visual acuity.
authors.affiliation: Vision Institute-IPEPO, Department of Ophthalmology, Federal University of São Paulo, Brazil.
authors.forename: Tâmara L
authors.initials: TL
authors.lastname: Oliveira
authors.forename: Rafael E
authors.initials: RE
authors.lastname: Andrade
authors.forename: Cristina
authors.initials: C
authors.lastname: Muccioli
authors.forename: Juliana
authors.initials: J
authors.lastname: Sallum
authors.forename: Rubens
authors.initials: R
authors.lastname: Belfort
mesh_terms: D002648:Child; D002829:Choroid / Q000473:pathology*; D005451:Fluorescein Angiography / Q000379:methods; D015799:Gyrate Atrophy / Q000150:complications* / Q000175:diagnosis; D006801:Humans; D008269:Macular Edema / Q000175:diagnosis* / Q000209:etiology*; D008297:Male; D009952:Ornithine / Q000097:blood; D012160:Retina / Q000473:pathology*; D041623:Tomography, Optical Coherence / Q000379:methods
chemical_list: D009952:Ornithine