Camptodactyly-arthropathy-coxa vara-pericarditis syndrome versus juvenile idiopathic arthropathy.
OBJECTIVE
The objective of our article was to highlight the important clinical and radiographic features of camptodactyly-arthropathy-coxa vara-pericarditis (CACP) syndrome. In particular, we emphasize those features that allow differentiation of CACP syndrome from juvenile idiopathic arthropathy.


CONCLUSIONS
CACP syndrome should be considered in all patients who present with a noninflammatory arthropathy or with "atypical juvenile idiopathic arthritis," particularly if radiographs reveal an absence of erosions. In the correct clinical setting, large acetabular cysts on pelvic radiographs may be considered pathognomonic of CACP syndrome.
Offiah
Amaka C
AC
Department of Radiology, Great Ormond Street Hospital for Children, Great Ormond St., London WC1N 3JH, UK.
Woo
Pat
P
Prieur
Anne-Marie
AM
Hasson
Nathan
N
Hall
Christine M
CM
D000293:Adolescent; D000328:Adult; D001171:Arthritis, Juvenile / Q000175:diagnosis*; D002648:Child; D003286:Contracture / Q000000981:diagnostic imaging*; D003937:Diagnosis, Differential; D005260:Female; D005385:Fingers / Q000000981:diagnostic imaging*; D006621:Hip Joint / Q000000981:diagnostic imaging*; D006801:Humans; D007592:Joint Diseases / Q000000981:diagnostic imaging*; D008297:Male; D010493:Pericarditis / Q000175:diagnosis*; D011859:Radiography; D013577:Syndrome