Narrow duplicated internal auditory canal: radiological findings and review of the literature.
Narrow duplicated internal auditory canal (IAC) is a rare malformation of the temporal bone that is associated with ipsilateral congenital sensorineural hearing loss. This may be an isolated finding or a part of a syndrome. Radiological examination should demonstrate aplasia or hypoplasia of the neural components of the narrow IAC, to guide the surgical approach. We report a 7-year-old boy with Klippel-Feil syndrome with a narrow double IAC with no sensorineural hearing loss but with conductive hearing loss. In this patient, the IAC consisted of two separate narrow bony canals clearly seen on 3D temporal bone CT and one nerve that was delineated on MRI. The contralateral external auditory canal was stenotic and the ossicles were dysplastic.
Demir
Ozgün Ilhan
OI
Department of Radiology, Faculty of Medicine, Dokuz Eylül University, 35340 Balçova, Izmir, Turkey. oilhandemir@yahoo.com.tr
Cakmakci
Handan
H
Erdag
Taner Kemal
TK
Men
Süleyman
S
D000015:Abnormalities, Multiple; D002648:Child; D004424:Ear Canal / Q000002:abnormalities / Q000000981:diagnostic imaging; D007758:Ear, Inner / Q000002:abnormalities* / Q000000981:diagnostic imaging*; D005154:Facial Nerve / Q000002:abnormalities / Q000000981:diagnostic imaging; D006314:Hearing Loss, Conductive / Q000151:congenital / Q000000981:diagnostic imaging; D006801:Humans; D021621:Imaging, Three-Dimensional; D007714:Klippel-Feil Syndrome / Q000000981:diagnostic imaging; D008279:Magnetic Resonance Imaging; D008297:Male; D013701:Temporal Bone / Q000002:abnormalities / Q000000981:diagnostic imaging; D014057:Tomography, X-Ray Computed