Pulmonary alveolar proteinosis and end-stage pulmonary fibrosis: a rare association.
We present the high resolution CT features of marked pulmonary fibrosis in a patient known to have pulmonary alveolar proteinosis (PAP) confirmed on open lung biopsy. Significant fibrosis in PAP is an extremely rare occurrence with only a few case reports. Our case demonstrated a predominantly central distribution, which has not been described previously.
Agarwal
Prachi P
PP
Department of Diagnostic Imaging, The Ottawa Hospital, Ottawa, Ontario, Canada.
Seely
Jean M
JM
Perkins
D Garth
DG
Matzinger
Fred R
FR
Alikhan
Qasim
Q
D000328:Adult; D001706:Biopsy; D005260:Female; D006801:Humans; D010784:Photomicrography; D011649:Pulmonary Alveolar Proteinosis / Q000150:complications* / Q000000981:diagnostic imaging / Q000473:pathology; D011658:Pulmonary Fibrosis / Q000150:complications* / Q000000981:diagnostic imaging / Q000473:pathology; D014057:Tomography, X-Ray Computed