[Haemoptysis as a complication of Behçet's disease].
Three patients, two Moroccan men aged 27 and 25 and a Turkish man aged 25, presented with haemoptysis caused by pulmonary aneurysm. The aneurysms had formed as a complication of Behçet's disease. Two of them were treated with high doses of corticosteroids. One man recovered and another died as a consequence of massive haemoptysis. The third man underwent emergency thoracotomy and pneumectomy due to massive haemoptysis. Postoperatively he was treated with cyclosporine resulting in full recovery. Behçet's disease is a multisystem vasculitis characterised by orogenital ulcerations and uveitis. In a minority of cases pulmonary aneurysms develop, often causing massive haemoptysis. Aneurysms are often accompanied by venous thrombosis. Treatment consists of immunosuppressive therapy. Nevertheless a considerable number of patients die following massive haemoptysis.
van den Brand
J J G
JJ
St. Antonius Ziekenhuis, Postbus 2500, 3430 EM, Nieuwegein.
van den Bosch
J M M
JM
Seldenrijk
C A
CA
Dercksen
M W
MW
Ruitenberg
H M
HM
Schramel
F M N H
FM
D000305:Adrenal Cortex Hormones / Q000627:therapeutic use; D000328:Adult; D000783:Aneurysm / Q000150:complications* / Q000209:etiology; D001528:Behcet Syndrome / Q000150:complications* / Q000401:mortality / Q000473:pathology; D017809:Fatal Outcome; D006469:Hemoptysis / Q000188:drug therapy / Q000209:etiology*; D006801:Humans; D008297:Male; D011651:Pulmonary Artery; D011655:Pulmonary Embolism / Q000150:complications; D016896:Treatment Outcome
D000305:Adrenal Cortex Hormones