Pneumosinus dilatans and orbital meningioma in neurofibromatosis type 2.
We report on a 9-year-old boy with neurofibromatosis type 2 and a progressive proptosis of the left eye. Imaging studies revealed a pneumosinus dilatans of the left ethmoidal and frontal sinuses and an adjacent left orbital mass. Incision biopsy of the orbital mass showed a meningiothelial meningioma. Orbital and intracranial meningiomas are frequently associated with pneumosinus dilatans. This report illustrates the relationship of pneumosinus dilatans, intra-orbital meningioma and neurofibromatosis type 2.
Vauterin
T
T
Department of Oto-Rhino-Laryngology, Head and Neck Surgery, University Hospital KULeuven, Kapucijnenvoer 33, 3000 Leuven, Belgium.
Mombaerts
I
I
Jorissen
M
M
Sciot
R
R
Legius
E
E
D002648:Child; D004108:Dilatation, Pathologic / Q000175:diagnosis / Q000209:etiology; D004724:Endoscopy; D005094:Exophthalmos / Q000209:etiology; D005500:Follow-Up Studies; D034381:Hearing Loss / Q000209:etiology; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D008579:Meningioma / Q000175:diagnosis*; D016518:Neurofibromatosis 2 / Q000175:diagnosis*; D009918:Orbital Neoplasms / Q000175:diagnosis*; D010254:Paranasal Sinus Diseases / Q000175:diagnosis* / Q000209:etiology; D014057:Tomography, X-Ray Computed; D016896:Treatment Outcome