Surgical management of Ebstein's anomaly in the adult.
Ebstein's anomaly is a rare cardiac malformation that affects the tricuspid valve, right ventricle, and right atrioventricular junction. These anatomical and functional abnormalities cause important tricuspid regurgitation that results in right atrial and right ventricular dilatation and atrial and ventricular arrhythmias. Diagnosis is made by echocardiography. Operation includes tricuspid valve repair or replacement, closure of any interatrial communications, and appropriate antiarrhythmia procedures. Repair of Ebstein's anomaly eliminates right-to-left intracardiac shunting, improves exercise tolerance and functional class, and reduces supraventricular arrhythmias. In addition, quality of life and longevity are improved.
Dearani
Joseph A
JA
Division of Cardiovascular Surgery, Mayo Clinic College of Medicine, Rochester, Minnesota 55902, USA. jdearani@mayo.edu
Danielson
Gordon K
GK
D000328:Adult; D000889:Anti-Arrhythmia Agents / Q000627:therapeutic use; D001281:Atrial Fibrillation / Q000150:complications / Q000188:drug therapy; D001282:Atrial Flutter / Q000150:complications / Q000188:drug therapy; D004437:Ebstein Anomaly / Q000145:classification / Q000150:complications / Q000175:diagnosis / Q000601:surgery*; D019918:Heart Valve Prosthesis Implantation; D006801:Humans; D014261:Tricuspid Valve / Q000601:surgery
D000889:Anti-Arrhythmia Agents