Novel approach to the newborn with hypoplastic left heart syndrome and intact atrial septum.
A prenatally diagnosed fetus with hypoplastic left heart syndrome and intact atrial septum was delivered in the cardiac catheterization suite. Using radio frequency energy, a transseptal perforation of the thickened and intact atrial septum was immediately performed following transcatheter cannulation of the right atrium via the umbilical vein. Serial cutting balloon septostomies followed by static balloon septostomies resulted in effective left atrial decompression, atrial mixing, and optimal pulmonary and systemic perfusion. The child is now thriving after both stage I Norwood and bidirectional Glenn procedures.
Javois
Alexander J
AJ
Heart Institute for Children, Advocate Hope Children's Hospital, Oak Lawn, Illinois 60453, USA. alexjavois@thic.com
Van Bergen
Andrew H
AH
Cuneo
Bettina F
BF
Husayni
Tarek S
TS
D000328:Adult; D006328:Cardiac Catheterization; D017115:Catheter Ablation; D002404:Catheterization; D005260:Female; D006325:Heart Atria / Q000000981:diagnostic imaging; D006346:Heart Septum / Q000000981:diagnostic imaging; D006801:Humans; D018636:Hypoplastic Left Heart Syndrome / Q000000981:diagnostic imaging / Q000601:surgery*; D007231:Infant, Newborn; D011247:Pregnancy; D016216:Ultrasonography, Prenatal