Pulmonary vascular manifestations of mixed connective tissue disease.
Mixed connective tissue disease (MCTD) refers to a disease process with combined clinical features characteristic of systemic lupus erythematous, scleroderma, and polymyositis-dermatomyositis. This article focuses on the pulmonary vasculature manifestations of MCTD. We briefly discuss associations between MCTD and interstitial lung disease, pleural disease, and alveolar hemorrhage.
Bull
Todd M
TM
Division of Pulmonary Sciences and Critical Care Medicine, Pulmonary Hypertension Center, University of Colorado School of Medicine, 4200 East Ninth Avenue, Box C-272, Denver, CO 80262, USA. Todd.Bull@UCHSC.edu
Fagan
Karen A
KA
Badesch
David B
DB
D006801:Humans; D006976:Hypertension, Pulmonary / Q000188:drug therapy / Q000209:etiology* / Q000503:physiopathology; D017563:Lung Diseases, Interstitial / Q000209:etiology; D008947:Mixed Connective Tissue Disease / Q000150:complications* / Q000503:physiopathology; D010995:Pleural Diseases / Q000209:etiology; D011650:Pulmonary Alveoli; D011652:Pulmonary Circulation / Q000502:physiology