Benign cutaneous Degos disease.
A 24-year-old woman presented with an 8-year history of a recurrent asymptomatic rash characterized by small erythematous papules which evolved to form atrophic porcelain white scars with a telangectatic rim. She had never had gastrointestinal or neurological symptoms. A short trial of aspirin did not alter the behavior of the disease. Histology confirmed the clinical diagnosis of Degos disease. Degos disease is a rare disorder that has been classified into the benign or malignant variety. The malignant type has a poor prognosis. Gastrointestinal involvement is the most frequent cause of death. The existence of patients with a prolonged, purely cutaneous or benign form has been increasingly recognized. It may be impossible to classify a patient at the time of initial presentation. Her progress is consistent with the benign form.
Zamiri
Mozheh
M
Department of Dermatology, Monklands Hospital, Airdrie, UK. mozhehzamiri@hotmail.com
Jarrett
Paul
P
Snow
John
J
D000328:Adult; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D012867:Skin / Q000473:pathology; D017444:Skin Diseases, Papulosquamous / Q000175:diagnosis*; D017445:Skin Diseases, Vascular / Q000175:diagnosis*; D014657:Vasculitis / Q000175:diagnosis*