Dysphagia lusoria caused by aberrant right subclavian artery, Kommerell's diverticulum, legamentum ring, right descending aorta, and absent left pulmonary artery: a report of a unique vascular congenital disease undetected until adulthood and a review of the literature.
An active otherwise healthy and middle-aged woman presented with left supraclavicular pulsation, right upper extremity claudication, and mild dysphagia. Evaluation revealed an aberrant right subclavian artery, Kommerell's diverticulum with aneurysmal degeneration, legamentum arteriosum completing vascular ring, and absent left pulmonary artery with multiple collateral supply to the left lung. She underwent successful surgical repair via right thoracotomy, including division of the vascular ring, resection of the diverticulum and aneurysm, and finally reimplantation of the right subclavian artery to the aortic arch. Her symptoms resolved completely, and she was able to resume normal activities.
Hassan
W
W
King Faisal Heart Institute, King Faisal Specialist Hospital and Research Center, P.O. Box 3354, Riyadh, 11211, Saudi Arabia. hassanw@kfshrc.edu.sa
Omrani
A Al
AA
Neimatallah
M
M
Fadley
F Al
FA
Halees
Z Al
ZA
D001015:Aortic Arch Syndromes / Q000000981:diagnostic imaging / Q000601:surgery; D003680:Deglutition Disorders / Q000209:etiology*; D004936:Diverticulum, Esophageal / Q000150:complications* / Q000000981:diagnostic imaging; D005260:Female; D006801:Humans; D008875:Middle Aged; D011651:Pulmonary Artery / Q000002:abnormalities* / Q000601:surgery; D011859:Radiography; D013348:Subclavian Artery / Q000002:abnormalities* / Q000637:transplantation; D013908:Thoracotomy; D014652:Vascular Diseases / Q000151:congenital* / Q000000981:diagnostic imaging