Case of symptomatic propriospinal myoclonus evolving toward acute "myoclonic status".
Propriospinal myoclonus is a rare motor disorder consisting of involuntary spinal-generated muscular jerks. Here, we report a severe and uncommon case of propriospinal myoclonus that appeared after a vertebral fracture of T11. In this patient, the polysomnographic investigation showed continuing focal myoclonic activity in axial muscles during stable sleep and an acute progression into a myoclonic "status" associated with respiratory failure and loss of consciousness. It is necessary to consider this severe progression and support it with prompt emergency maneuvers and adequate pharmacotherapy.
Manconi
Mauro
M
Department of Neurology, Vita-Salute University, Istituto di Ricovero e Cura a Carattere Scientifico San Raffaele-Turro, Milan, Italy. manconi.mauro@hsr.it
Sferrazza
Barbara
B
Iannaccone
Sandro
S
Massimo
Antonio
A
Zucconi
Marco
M
Ferini-Strambi
Luigi
L
D000927:Anticonvulsants / Q000627:therapeutic use; D002998:Clonazepam / Q000627:therapeutic use; D018450:Disease Progression; D004576:Electromyography / Q000379:methods; D004831:Epilepsies, Myoclonic / Q000188:drug therapy / Q000209:etiology / Q000473:pathology / Q000503:physiopathology*; D005073:Evoked Potentials, Somatosensory / Q000502:physiology / Q000528:radiation effects; D005133:Eye Movements / Q000502:physiology; D005260:Female; D006801:Humans; D008279:Magnetic Resonance Imaging / Q000379:methods; D008875:Middle Aged; D018482:Muscle, Skeletal / Q000187:drug effects / Q000503:physiopathology / Q000528:radiation effects; D009431:Neural Conduction / Q000528:radiation effects; D016103:Spinal Fractures / Q000150:complications / Q000473:pathology; D013127:Spinal Nerves / Q000187:drug effects / Q000473:pathology / Q000503:physiopathology*; D050781:Transcranial Magnetic Stimulation / Q000379:methods
D000927:Anticonvulsants; D002998:Clonazepam