title: Awake nasotracheal intubation using fiberoptic bronchoscope in a pediatric patient with Freeman-Sheldon syndrome.
abstract: The Freeman-Sheldon syndrome is a congenital disease primarily affecting the facial, limb and respiratory muscles that give rise to classical clinical features including typical whistling face and short webbed neck associated with difficult intubation. We present successful awake nasotracheal intubation in a 6-year-old patient with typical clinical features of Freeman-Sheldon syndrome by using fiberoptic bronchoscope on two separate occasions.
authors.affiliation: Department of Anesthesia and Pain Medicine, Ajou University School of Medicine, Wonchon-Dong, Yongtong-Gu, Suwon, Kyungki-Do, Korea. jskane@ajou.ac.kr
authors.forename: J S
authors.initials: JS
authors.lastname: Kim
authors.forename: S Y
authors.initials: SY
authors.lastname: Park
authors.forename: S K
authors.initials: SK
authors.lastname: Min
authors.forename: J H
authors.initials: JH
authors.lastname: Kim
authors.forename: S Y
authors.initials: SY
authors.lastname: Lee
authors.forename: B K
authors.initials: BK
authors.lastname: Moon
mesh_terms: D020680:Bronchoscopes; D003025:Clubfoot / Q000601:surgery; D005145:Face / Q000002:abnormalities*; D005260:Female; D006801:Humans; D007442:Intubation, Intratracheal; D017880:Limb Deformities, Congenital; D008297:Male; D018482:Muscle, Skeletal / Q000002:abnormalities; D013577:Syndrome