title: A parturient with neurofibromatosis type 2: anesthetic and obstetric considerations for delivery.
abstract: Neurofibromatosis type 2 is an extremely rare form of neurofibromatosis characterized by central nervous system involvement with bilateral vestibular schwannomas and spinal tumors. Anesthetic management of a parturient with neurofibromatosis type 2 has not been fully reported, and the condition is challenging to obstetric anesthesiologists due to the presence of intracranial and intraspinal canal neurofibromas. We present a case of neurofibromatosis type 2 referred for delivery. Because of central neuraxial involvement, regional anesthesia was avoided, and the patient delivered by cesarean section under general anesthesia. The importance of pre-operative diagnosis and multidisciplinary management for neurofibromatosis type 2 is emphasized and anesthetic and obstetric considerations for delivery are presented.
authors.affiliation: Department of Anesthesiology, Magee Women's Hospital, University of Pittsburgh School of Medicine, Pittsburgh, PA 15213, USA.
authors.forename: T
authors.initials: T
authors.lastname: Sakai
authors.forename: M C
authors.initials: MC
authors.lastname: Vallejo
authors.forename: K T
authors.initials: KT
authors.lastname: Shannon
mesh_terms: D000328:Adult; D000768:Anesthesia, General; D000773:Anesthesia, Obstetrical; D016543:Central Nervous System Neoplasms; D002585:Cesarean Section; D005260:Female; D006801:Humans; D016518:Neurofibromatosis 2; D011247:Pregnancy; D011252:Pregnancy Complications, Neoplastic