Differences in dental and bone maturation in regions with or without hemihypertrophy in two patients with Russell-Silver syndrome.
Hemihypertrophy (hemihyperplasia) is defined as asymmetric body overgrowth of one or more body parts. Hemihypertrophy can be isolated or be part of well-defined syndromes, such as Russell-Silver syndrome (RSS). RSS is characterized by severe intrauterine growth retardation, postnatal short stature, asymmetry of the face, body, and limbs, short and incurved fifth fingers, broad forehead, pointed small triangular shaped face, girdle nose, normal psychomotor development, variations in the pattern of sexual development, and dental and oral abnormalities. The aim of this study was to determine whether or not there was any difference in the maturity of bone in left and right hand-wrist radiographs and dental development in the right and left jaws of two patients with RSS. In addition, the clinical features of the syndrome are discussed.
Orbak
Zerrin
Z
Department of Pediatrics, Faculty of Medicine, Ataturk University, Erzurum, Turkey.
Orbak
Recep
R
Kara
Cankat
C
Kavrut
Fahri
F
D000293:Adolescent; D001846:Bone Development; D002648:Child; D005260:Female; D005317:Fetal Growth Retardation; D006130:Growth Disorders / Q000000981:diagnostic imaging / Q000473:pathology*; D006801:Humans; D015576:Hyperostosis / Q000000981:diagnostic imaging / Q000473:pathology*; D007568:Jaw / Q000000981:diagnostic imaging / Q000473:pathology; D011859:Radiography; D014070:Tooth / Q000000981:diagnostic imaging / Q000254:growth & development* / Q000473:pathology