title: Successful surgical treatment of a neonate with prenatal diagnosis of severe Ebstein's anomaly.
abstract: We present a case of a patient with a severe form of Ebstein's anomaly diagnosed in a 36th week of gestation through prenatal echocardiographic evaluation. The emergency surgery consisted of closure of the tricuspid valve and creation of a residual atriventricular communication, enlargement of interatrial communication, closure of the pulmonary artery, and construction of an aortopulmonary shunt. Subsequently, the patient underwent the hemiFontan and Fontan operation. We conclude that prenatal echocardiographic diagnosis is crucial for the survival of children with a severe form of Ebstein's anomaly, which is a neonatal emergency and requires prompt decision mating to initiate surgical management.
authors.affiliation: Department of Pediatric Cardiac Surgery, Polish-American Children's Hospital Collegium Medicum Jagiellonian University, 30-663 Kraków, ul., Wielicka, 265, Poland. mimalec@cyf-kr.edu.pl
authors.forename: E
authors.initials: E
authors.lastname: Malec
authors.forename: J
authors.initials: J
authors.lastname: Dangel
authors.forename: T
authors.initials: T
authors.lastname: Mroczek
authors.forename: M
authors.initials: M
authors.lastname: Procelewska
authors.forename: K
authors.initials: K
authors.lastname: Januszewska
authors.forename: J
authors.initials: J
authors.lastname: Ko Cz
mesh_terms: D000328:Adult; D001166:Arteriovenous Shunt, Surgical; D004437:Ebstein Anomaly / Q000000981:diagnostic imaging / Q000601:surgery*; D005260:Female; D006352:Heart Ventricles / Q000000981:diagnostic imaging / Q000601:surgery; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D011247:Pregnancy; D016216:Ultrasonography, Prenatal