title: Case and management of incidentalomas in patients with Von Hippel-Lindau disease.
abstract: Adrenal incidentalomas, those adrenal masses discovered on imaging studies undertaken for other indications, represent an evaluation and management conundrum. Evaluating every incidentaloma for functional status and/or resecting all incidentalomas would not be cost-effective because the vast majority of incidentalomas are benign, non-functioning adenomas. Current management strategies focus on size, functionality and imaging characteristics. These strategies do not take into account individual patient characteristics, for example, comorbid hereditary syndromes. In this article we report a case of a pheochromocytoma presenting as a small incidentaloma in a patient with Von Hippel-Lindau disease. We review the current literature describing the appropriate evaluation and management of adrenal incidentalomas and investigate the nuances of evaluation of these masses in patients with Von Hippel-Lindau disease.
authors.affiliation: Department of Urology, SUNY at Stony Brook, Stony Brook, NY 11794-8093, USA.
authors.forename: Rebecca
authors.initials: R
authors.lastname: O'Malley
authors.forename: Bilal
authors.initials: B
authors.lastname: Chughtai
authors.forename: Troy
authors.initials: T
authors.lastname: Sukkarieh
authors.forename: Alex
authors.initials: A
authors.lastname: Kirschenbaum
authors.forename: Rohan
authors.initials: R
authors.lastname: Naik
authors.forename: Ahmed
authors.initials: A
authors.lastname: Sawas
authors.forename: S Ali
authors.initials: SA
authors.lastname: Khan
authors.forename: Jamil
authors.initials: J
authors.lastname: Rehman
mesh_terms: D000310:Adrenal Gland Neoplasms / Q000473:pathology / Q000601:surgery*; D000315:Adrenalectomy / Q000379:methods*; D000328:Adult; D003937:Diagnosis, Differential; D005500:Follow-Up Studies; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D009367:Neoplasm Staging; D010673:Pheochromocytoma / Q000175:diagnosis / Q000473:pathology / Q000601:surgery*; D011230:Precancerous Conditions / Q000473:pathology*; D018570:Risk Assessment; D016896:Treatment Outcome; D006623:von Hippel-Lindau Disease / Q000175:diagnosis*