title: Pulmonary agenesis associated with dextrocardia, sternal defects, and ectopic kidney.
abstract: Pulmonary agenesis is a rare embryological defect, usually unilateral, and is associated with skeletal, cardiovascular, and other anomalies. A 22-month-old girl was admitted to our clinic with recurrent pulmonary infections. A chest X-ray and multidetector computed tomography (MDCT) revealed pulmonary agenesis with dextrocardia, sternal defects, and a right pelvic ectopic kidney. We report on the first known case of right-sided pulmonary agenesis combined with isolated dextrocardia, sternal defects, and an ectopic kidney. The importance of MDCT for the diagnosis of pulmonary agenesis and associated other anomalies is demonstrated.
authors.affiliation: Department of Thoracic Surgery, Faculty of Medicine, Ataturk University, Erzurum, Turkey. atilaerglu@hotmail.com
authors.forename: Atilla
authors.initials: A
authors.lastname: Eroglu
authors.forename: Fatih
authors.initials: F
authors.lastname: Alper
authors.forename: Atila
authors.initials: A
authors.lastname: Turkyilmaz
authors.forename: Nurettin
authors.initials: N
authors.lastname: Karaoglanoglu
authors.forename: Adnan
authors.initials: A
authors.lastname: Okur
mesh_terms: D003914:Dextrocardia / Q000000981:diagnostic imaging*; D005260:Female; D006801:Humans; D007223:Infant; D007668:Kidney / Q000002:abnormalities* / Q000000981:diagnostic imaging; D008168:Lung / Q000002:abnormalities* / Q000000981:diagnostic imaging; D011651:Pulmonary Artery / Q000002:abnormalities* / Q000000981:diagnostic imaging; D011859:Radiography; D012008:Recurrence; D012141:Respiratory Tract Infections / Q000209:etiology; D013249:Sternum / Q000002:abnormalities* / Q000000981:diagnostic imaging