Familial atrial standstill in association with dilated cardiomyopathy.
. Atrial standstill is an extremely uncommon arrhythmia that rarely appears to be familial and genetically determined. Atrial standstill has been associated with several conditions including, but not restricted to, congenital heart disease, valvular heart disease, conduction disturbances, Brugada syndrome, myocardial infarction, and amyloidosis. Only a few cases of familial clustering of atrial standstill have been reported so far. This report represents a family with atrial standstill associated with syncope, dilated cardiomyopathy, and sudden cardiac death.
Fazelifar
Amir Farjam
AF
Department of Pacemaker and Electrophysiology, Rajaie Cardiovascular Medical Center, Iran University of Medical Sciences, Mellat Park, Vali-Asr Avenue, Tehran 1996911151, Iran.
Arya
Arash
A
Haghjoo
Majid
M
Sadr-Ameli
Mohammad Ali
MA
D000328:Adult; D002311:Cardiomyopathy, Dilated / Q000235:genetics*; D016757:Death, Sudden, Cardiac; D004562:Electrocardiography; D005260:Female; D006325:Heart Atria / Q000002:abnormalities*; D006329:Heart Conduction System / Q000002:abnormalities*; D006801:Humans; D008297:Male; D010375:Pedigree; D013575:Syncope / Q000235:genetics*