title: A patient with congenital defect of nasal cartilaginous septal and vomeral bone reconstructed with costal cartilaginous graft.
abstract: We present a 64-year-old woman who had a congenital defect of the nasal septal cartilage and vomeral bone. She noticed her nasal tip was collapsed approximately 2 months before consultation. Computed tomography showed the absence of cartilaginous septum and vomeral bone, and radiograph showed a depression in the anterior nasal floor and hypoplasia of anterior nasal spine. She had no history of maxillofacial trauma, disease, or surgery in the midface. Fiberendoscopic examination of nasal cavity showed normal mucosa without signs of chronic inflammatory diseases such as Wegener's granulomatosis. Her intelligence was normal, and no anomaly was observed in the cranial region. Blood examination showed negative including serologic tests for syphilis. No other systemic findings were found, and none of her relatives were similarly afflicted. From these findings, we concluded that the patient did not have Binder's syndrome (or she has, at least, a new variant of Binder's syndrome). Rhinoplasty with cantilever costal cartilaginous graft was performed. The "hook-shaped part" was carved on the dorsal graft, which served to reduce the collapsed lateral cartilage. Eight months postoperatively, the flattened nose was well corrected with acceptable projection.
authors.affiliation: Department of Plastic and Reconstructive Surgery, Graduate School of Medicine, University of Tokyo, Hongo, Tokyo, Japan. okazaki-m@umin.ac.jp
authors.forename: Mutsumi
authors.initials: M
authors.lastname: Okazaki
authors.forename: Shunji
authors.initials: S
authors.lastname: Sarukawa
authors.forename: Norio
authors.initials: N
authors.lastname: Fukuda
mesh_terms: D000368:Aged; D002356:Cartilage / Q000637:transplantation*; D004724:Endoscopy; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D009295:Nasal Bone / Q000002:abnormalities / Q000601:surgery; D009296:Nasal Cavity / Q000002:abnormalities; D009300:Nasal Septum / Q000002:abnormalities* / Q000601:surgery; D012225:Rhinoplasty / Q000379:methods*; D014057:Tomography, X-Ray Computed; D016896:Treatment Outcome