Myelofibrosis in a patient with pachydermoperiostosis.
Pachydermoperiostosis (idiopathic or primary hypertrophic osteoarthropathy) is a rare condition of unknown origin involving the skin and the skeleton, with an autosomal dominant transmission. We report a case of anaemia in a patient with pachydermoperiostosis indicating myelofibrosis, and review the literature and the pathogenetic mechanisms.
Bachmeyer
C
C
Service de Médecine Interne, Hôpital Tenon, Paris, France. claude.bachmeyer@tnn.ap-hop-paris.fr
Blum
L
L
Cadranel
J-F
JF
Delfraissy
J-F
JF
D017255:Acitretin / Q000627:therapeutic use; D000328:Adult; D000740:Anemia / Q000188:drug therapy / Q000209:etiology*; D005360:Fibula / Q000000981:diagnostic imaging; D006801:Humans; D007641:Keratolytic Agents / Q000627:therapeutic use; D008297:Male; D010005:Osteoarthropathy, Secondary Hypertrophic / Q000150:complications* / Q000175:diagnosis; D055728:Primary Myelofibrosis / Q000150:complications* / Q000175:diagnosis; D011859:Radiography; D013977:Tibia / Q000000981:diagnostic imaging
D007641:Keratolytic Agents; D017255:Acitretin