title: Testis sparing surgery for steroid unresponsive testicular tumors of the congenital adrenal hyperplasia.
abstract: The association between testicular tumors/nodules and congenital adrenal hyperplasia (CAH) has been recognized for many years. Tumors are considered to be an aberrant adrenal tissue that has descended with the testes and has become hyperplastic due to ACTH stimulation. The recommended treatment consists of increasing the glucocorticoid dose to suppress ACTH secretions. If the testicular size is not reduced after suppression therapy or a side effect of glucocorticoid dose is noted, surgical intervention should be considered. We diagnosed steroid unresponsive testicular tumors of the CAH in two patients who were treated by testicular sparing tumor enucleation. We believe that testis sparing surgery is the procedure of choice for all patients with testicular adrenal rest tumor, since it maximizes future fertility potential.
authors.affiliation: Pediatric Surgery Clinic, Social Security Institution Children's Hospital, Ankara, Turkey. httiryaki@hotmail.com
authors.forename: Tuğrul
authors.initials: T
authors.lastname: Tiryaki
authors.forename: Zehra
authors.initials: Z
authors.lastname: Aycan
authors.forename: Sema
authors.initials: S
authors.lastname: Hücümenoğlu
authors.forename: Halil
authors.initials: H
authors.lastname: Atayurt
mesh_terms: D000293:Adolescent; D000312:Adrenal Hyperplasia, Congenital / Q000150:complications*; D000314:Adrenal Rest Tumor / Q000150:complications / Q000175:diagnosis / Q000188:drug therapy / Q000601:surgery*; D002648:Child; D006801:Humans; D007984:Leydig Cell Tumor / Q000175:diagnosis; D008297:Male; D013736:Testicular Neoplasms / Q000150:complications / Q000175:diagnosis / Q000188:drug therapy / Q000601:surgery*