title: Myelofibrosis in a patient with pachydermoperiostosis.
abstract: Pachydermoperiostosis (idiopathic or primary hypertrophic osteoarthropathy) is a rare condition of unknown origin involving the skin and the skeleton, with an autosomal dominant transmission. We report a case of anaemia in a patient with pachydermoperiostosis indicating myelofibrosis, and review the literature and the pathogenetic mechanisms.
authors.affiliation: Service de Médecine Interne, Hôpital Tenon, Paris, France. claude.bachmeyer@tnn.ap-hop-paris.fr
authors.forename: C
authors.initials: C
authors.lastname: Bachmeyer
authors.forename: L
authors.initials: L
authors.lastname: Blum
authors.forename: J-F
authors.initials: JF
authors.lastname: Cadranel
authors.forename: J-F
authors.initials: JF
authors.lastname: Delfraissy
mesh_terms: D017255:Acitretin / Q000627:therapeutic use; D000328:Adult; D000740:Anemia / Q000188:drug therapy / Q000209:etiology*; D005360:Fibula / Q000000981:diagnostic imaging; D006801:Humans; D007641:Keratolytic Agents / Q000627:therapeutic use; D008297:Male; D010005:Osteoarthropathy, Secondary Hypertrophic / Q000150:complications* / Q000175:diagnosis; D055728:Primary Myelofibrosis / Q000150:complications* / Q000175:diagnosis; D011859:Radiography; D013977:Tibia / Q000000981:diagnostic imaging
chemical_list: D007641:Keratolytic Agents; D017255:Acitretin