Complete agenesis of the right and left pulmonary arteries, with main pulmonary artery originating from the right ventricle, presenting as primary pulmonary hypertension of the newborn: case report.
A female infant who had been misdiagnosed as having primary pulmonary hypertension of the newborn was found to have agenesis of the branch pulmonary arteries with collateral-dependent pulmonary circulation. The intracardiac anatomy was completely normal. Unifocalization of branch pulmonary artery was done, followed by stenting of the ductus arteriosus.
Mehta
H
H
Department of Pediatric Cardiology and Cardiovascular Surgery, Schneider Children's Hospital, 261-01 76th Ave, New Hyde Park, NY 11040, USA.
Giglia
T
T
Parnell
V A
VA
Kholwadwala
D
D
D003937:Diagnosis, Differential; D005260:Female; D006330:Heart Defects, Congenital / Q000175:diagnosis* / Q000601:surgery; D006352:Heart Ventricles; D006801:Humans; D006976:Hypertension, Pulmonary / Q000175:diagnosis*; D007231:Infant, Newborn; D011651:Pulmonary Artery / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000601:surgery; D011859:Radiography; D012039:Regional Blood Flow; D015607:Stents