[Dermatofibrosarcoma protuberans of Darier and Ferranda study of 28 cases in adult].
Dermatofibrosarcoma protuberans of Darier and Ferrand is a mesenchymatous skin tumor of intermediate malignant potential, characterised by slow growth, local malignancy and a high rate of recurrence. It is a rare tumor, accounting for approximately 0.1% to 0.18% of all malignant skin tumors. Peak incidence of the disease is between 20 to 40 years of age. We report a retrospective study of 28 cases of dermatofibrosarcoma protuberans. We reviewed the clinical features, histopathological and immunohistochemical aspects of this tumor.
Sana
Triki
T
Service de Dermatologie de L'hôpital Charles Nicolle, Tunis.
Bécima
Fazaa
F
Rachida
Zermani
Z
Olfa
Khouildi
K
Faten
Zeglaoui
Z
Nadia
El Fekih
el F
Insaf
Mokhtar
M
Sarrah
Ben Jilani
BJ
Mohamed-Ridha
Kamoun
K
D000293:Adolescent; D000328:Adult; D000368:Aged; D018223:Dermatofibrosarcoma / Q000175:diagnosis / Q000473:pathology / Q000601:surgery; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D007150:Immunohistochemistry; D008297:Male; D008875:Middle Aged; D009364:Neoplasm Recurrence, Local; D011446:Prospective Studies; D012867:Skin / Q000473:pathology; D012878:Skin Neoplasms / Q000175:diagnosis / Q000473:pathology / Q000601:surgery; D013997:Time Factors