Successful management of concomitant omphalocele, accessory hepatic lobe, and biliary atresia in a 44-day-old boy.
We report the second case in literature of a boy with the association of large omphalocele, accessory hepatic lobe, and biliary atresia, and the first successful treatment. The patient was submitted to a surgical treatment at 44 days of life, including Kasai procedure, correction of the remnant abdominal wall defect, and removal of a hepatic accessory lobe. The boy evolved with normalization of hepatic function tests. After 15 years of follow-up, the patient is completely healthy, weights 45 kg, and is 1.64 m tall.
Pereira
Regina Maria
RM
Department of Pediatrics, School of Medicine, Federal University of Minas Gerais (UFMG), Belo Horizonte, Gerais 30140-061, Brazil.
Simões e Silva
Ana Cristina
AC
Leite
Virgínia Hora Rios
VH
Lanna
José Carlos Brandão Duarte
JC
Guimarães
José Teixeira
JT
D001656:Biliary Atresia / Q000150:complications* / Q000601:surgery*; D005500:Follow-Up Studies; D006554:Hernia, Umbilical / Q000150:complications* / Q000601:surgery*; D006801:Humans; D007223:Infant; D008099:Liver / Q000002:abnormalities* / Q000601:surgery*; D008297:Male; D012074:Remission Induction