title: [Feminizing testicular syndrome with multiple hamartomas and bilateral paratesticular leiomyomas].
abstract: BACKGROUND
  Complete androgen insensitivity syndrome or testicular feminization syndrome (TF) is the most common form of male pseudohermaphrodism, caused by a failure of androgen receptor binding. Patient with male genotype 46 XY, has a female morphotype with well developed external sexual organs.
  
  
  METHODS
  - We report the case of a 29 year-old girl with a TF syndrome discovered during the exploration of a primary amenorrhoea. Bilateral orchidectomy was performed. The testis were immature; they showed bilateral leiomyoma of the tunica albuginea and multiple hamartomas on the right side.
  
  
  CONCLUSIONS
  Benign tumors are developped in 80% of cases of TF and they are generally hamartomatous nodules of testis. Association of paratesticular leiomyoma to synchronous hamartoma has never been described, its histogenesis is discussed.
authors.affiliation: Service d'anatomie et de cytologique pathologiques, CHU H. Bourguiba, 3029, Sfax, Tunisie. akabdelmajid@yahoo.fr
authors.forename: S
authors.initials: S
authors.lastname: Krichen Makni
authors.forename: L
authors.initials: L
authors.lastname: Mnif Hachicha
authors.forename: S
authors.initials: S
authors.lastname: Ellouze
authors.forename: M
authors.initials: M
authors.lastname: Mnif
authors.forename: A
authors.initials: A
authors.lastname: Khabir
authors.forename: H
authors.initials: H
authors.lastname: Ketata
authors.forename: M
authors.initials: M
authors.lastname: Abid
authors.forename: T
authors.initials: T
authors.lastname: Sellami Boudawara
mesh_terms: D000328:Adult; D000568:Amenorrhea / Q000209:etiology; D013734:Androgen-Insensitivity Syndrome; D005260:Female; D007839:Functional Laterality; D006222:Hamartoma / Q000473:pathology*; D006801:Humans; D007889:Leiomyoma / Q000473:pathology*; D008297:Male; D013736:Testicular Neoplasms / Q000473:pathology*