title: [Dermatofibrosarcoma protuberans of Darier and Ferranda study of 28 cases in adult].
abstract: Dermatofibrosarcoma protuberans of Darier and Ferrand is a mesenchymatous skin tumor of intermediate malignant potential, characterised by slow growth, local malignancy and a high rate of recurrence. It is a rare tumor, accounting for approximately 0.1% to 0.18% of all malignant skin tumors. Peak incidence of the disease is between 20 to 40 years of age. We report a retrospective study of 28 cases of dermatofibrosarcoma protuberans. We reviewed the clinical features, histopathological and immunohistochemical aspects of this tumor.
authors.affiliation: Service de Dermatologie de L'hôpital Charles Nicolle, Tunis.
authors.forename: Triki
authors.initials: T
authors.lastname: Sana
authors.forename: Fazaa
authors.initials: F
authors.lastname: Bécima
authors.forename: Zermani
authors.initials: Z
authors.lastname: Rachida
authors.forename: Khouildi
authors.initials: K
authors.lastname: Olfa
authors.forename: Zeglaoui
authors.initials: Z
authors.lastname: Faten
authors.forename: El Fekih
authors.initials: el F
authors.lastname: Nadia
authors.forename: Mokhtar
authors.initials: M
authors.lastname: Insaf
authors.forename: Ben Jilani
authors.initials: BJ
authors.lastname: Sarrah
authors.forename: Kamoun
authors.initials: K
authors.lastname: Mohamed-Ridha
mesh_terms: D000293:Adolescent; D000328:Adult; D000368:Aged; D018223:Dermatofibrosarcoma / Q000175:diagnosis / Q000473:pathology / Q000601:surgery; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D007150:Immunohistochemistry; D008297:Male; D008875:Middle Aged; D009364:Neoplasm Recurrence, Local; D011446:Prospective Studies; D012867:Skin / Q000473:pathology; D012878:Skin Neoplasms / Q000175:diagnosis / Q000473:pathology / Q000601:surgery; D013997:Time Factors