title: Successful management of concomitant omphalocele, accessory hepatic lobe, and biliary atresia in a 44-day-old boy.
abstract: We report the second case in literature of a boy with the association of large omphalocele, accessory hepatic lobe, and biliary atresia, and the first successful treatment. The patient was submitted to a surgical treatment at 44 days of life, including Kasai procedure, correction of the remnant abdominal wall defect, and removal of a hepatic accessory lobe. The boy evolved with normalization of hepatic function tests. After 15 years of follow-up, the patient is completely healthy, weights 45 kg, and is 1.64 m tall.
authors.affiliation: Department of Pediatrics, School of Medicine, Federal University of Minas Gerais (UFMG), Belo Horizonte, Gerais 30140-061, Brazil.
authors.forename: Regina Maria
authors.initials: RM
authors.lastname: Pereira
authors.forename: Ana Cristina
authors.initials: AC
authors.lastname: Simões e Silva
authors.forename: Virgínia Hora Rios
authors.initials: VH
authors.lastname: Leite
authors.forename: José Carlos Brandão Duarte
authors.initials: JC
authors.lastname: Lanna
authors.forename: José Teixeira
authors.initials: JT
authors.lastname: Guimarães
mesh_terms: D001656:Biliary Atresia / Q000150:complications* / Q000601:surgery*; D005500:Follow-Up Studies; D006554:Hernia, Umbilical / Q000150:complications* / Q000601:surgery*; D006801:Humans; D007223:Infant; D008099:Liver / Q000002:abnormalities* / Q000601:surgery*; D008297:Male; D012074:Remission Induction