Lymphomatoid granulomatosis: a rare mimicker of vasculitis.
Lymphomatoid granulomatosis (LG) is a rare Epstein-Barr virus-associated lymphoproliferative disorder, with a propensity for blood vessel destruction. Although it most commonly affects the lung, it can affect multiple extrapulmonary sites (i.e., skin, nervous system, gastrointestinal tract, liver, spleen, kidney, and heart). Since LG often mimics systemic vasculitis, it presents a diagnostic clinical challenge. We describe a case of LG with no pulmonary involvement, which was thought to be systemic vasculitis on the basis of multiorgan involvement and biopsy findings.
Wu
Sherry M
SM
Division of Rheumatology, Olive View-UCLA Medical Center, David Geffen School of Medicine, Los Angeles, CA 91342, USA.
Min
Yoon
Y
Ostrzega
Nora
N
Clements
Philip J
PJ
Wong
Andrew L
AL
D003937:Diagnosis, Differential; D017809:Fatal Outcome; D006801:Humans; D008223:Lymphoma / Q000473:pathology*; D008230:Lymphomatoid Granulomatosis / Q000473:pathology*; D008297:Male; D008875:Middle Aged; D014057:Tomography, X-Ray Computed; D014657:Vasculitis / Q000473:pathology*