Secondary renal amyloidosis due to long-standing tubulointerstitial nephritis in a patient with Sjögren syndrome.
A 53-year-old patient with long-standing primary Sjögren syndrome presented with acute renal failure and nephrotic syndrome caused by secondary (AA) renal amyloidosis. Ten years before, he had been admitted because of exacerbation of the systemic disease. At that time, a pseudolymphoma of the kidney was diagnosed. To our knowledge, this is the first report of a patient with primary Sjögren syndrome and secondary (AA) amyloidosis with amyloid deposition in the kidneys causing nephrotic syndrome.
Ooms
Vanessa
V
Department of Nephrology, University Hospitals Leuven, Belgium.
Decupere
Marc
M
Lerut
Evelyne
E
Vanrenterghem
Yves
Y
Kuypers
Dirk R J
DR
D058186:Acute Kidney Injury / Q000209:etiology; D000686:Amyloidosis / Q000209:etiology* / Q000378:metabolism / Q000473:pathology; D001021:Aortic Valve / Q000473:pathology; D001022:Aortic Valve Insufficiency / Q000209:etiology / Q000473:pathology; D004417:Dyspnea / Q000209:etiology; D005355:Fibrosis; D006801:Humans; D007674:Kidney Diseases / Q000209:etiology; D008297:Male; D008875:Middle Aged; D009395:Nephritis, Interstitial / Q000150:complications* / Q000378:metabolism / Q000473:pathology; D009404:Nephrotic Syndrome / Q000209:etiology; D019310:Pseudolymphoma / Q000209:etiology; D000685:Serum Amyloid A Protein / Q000032:analysis; D012859:Sjogren's Syndrome / Q000150:complications*
D000685:Serum Amyloid A Protein