Ischemic retinopathy and uveitis in a patient with tetralogy of Fallot.
OBJECTIVE
To describe ischemic retinopathy in a patient with tetralogy of Fallot.


METHODS
Interventional case report.


METHODS
Clinical and imaging evaluation.


METHODS
Clinical, imaging, and laboratory findings in a patient with tetralogy of Fallot.


RESULTS
A 20-year-old female patient with tetralogy of Fallot had progressive visual loss of 3 weeks duration. Bilateral examination revealed dilated, tortuous, conjunctival vessels; prominent anterior chamber reaction; iris neovascularization; posterior synechia; retinal vascular tortuosity in both eyes; and inferior exudative retinal detachment. Fluorescein angiography revealed delayed retinal and choroidal filling. The working diagnosis was ischemic retinopathy with uveitis. The patient was treated for 6 months with a high-dose oral corticosteroid combined with a topical corticosteroid, a topical mydriatic, and panretinal photocoagulation. Conjunctival, vascular congestion subsided with a decrease in anterior chamber reaction. The inferior, exudative retinal detachment resolved, and vision was restored.


CONCLUSIONS
Retinal ischemic syndrome combined with uveitis can develop in patients with tetralogy of Fallot. Treatment can restore vision in such patients.
Wu
Wei-Chi
WC
Department of Ophthalmology, Chang Gung Memorial Hospital, Taoyuan, Taiwan.
Lai
Chi-Chung
CC
Su
Wen-Jen
WJ
Chen
Tun-Lu
TL
Hwang
Yih-Shiou
YS
Lin
Ken-Kuo
KK
Kao
Ling-Yuh
LY
D000284:Administration, Oral; D000287:Administration, Topical; D000328:Adult; D004359:Drug Therapy, Combination; D005260:Female; D005451:Fluorescein Angiography; D005938:Glucocorticoids / Q000627:therapeutic use; D006801:Humans; D007511:Ischemia / Q000175:diagnosis / Q000188:drug therapy / Q000209:etiology*; D011239:Prednisolone / Q000031:analogs & derivatives / Q000627:therapeutic use; D012171:Retinal Vessels / Q000473:pathology*; D013771:Tetralogy of Fallot / Q000150:complications* / Q000175:diagnosis / Q000188:drug therapy; D014331:Tropicamide / Q000008:administration & dosage; D014605:Uveitis / Q000175:diagnosis / Q000188:drug therapy / Q000209:etiology*
D005938:Glucocorticoids; C009935:prednisolone acetate; D011239:Prednisolone; D014331:Tropicamide