title: Sudden death in a case of cardiac amyloidosis immediately after pacemaker implantation for complete atrioventricular block.
abstract: We report a patient with cardiac involvement associated with primary amyloidosis presenting marked left ventricular (LV) wall thickening, severely decreased systolic and diastolic function, and complete atrioventricular block (CAVB), who died suddenly of cardiac arrest caused by electro-mechanical uncoupling occurring immediately after permanent pacemaker implantation. Post mortem examination showed no procedural complications such as cardiac or venous perforation. The heart was densely infiltrated with amyloid fibrils, especially in the extracellular tissues surrounding the papillary vessels.
authors.affiliation: First Department of Internal Medicine, Nippon Medical School, 1-1-5 Sendagi, Bunkyo-ku, Tokyo 113-8603, Japan.
authors.forename: Michio
authors.initials: M
authors.lastname: Ogano
authors.forename: Hitoshi
authors.initials: H
authors.lastname: Takano
authors.forename: Nagaharu
authors.initials: N
authors.lastname: Fukuma
authors.forename: Morimasa
authors.initials: M
authors.lastname: Takayama
authors.forename: Teruo
authors.initials: T
authors.lastname: Takano
authors.forename: Yasuo
authors.initials: Y
authors.lastname: Miyagi
authors.forename: Masami
authors.initials: M
authors.lastname: Ochi
authors.forename: Kazuo
authors.initials: K
authors.lastname: Shimizu
authors.forename: Hiroshi
authors.initials: H
authors.lastname: Kitamura
mesh_terms: D000368:Aged; D000686:Amyloidosis / Q000150:complications*; D009202:Cardiomyopathies / Q000150:complications*; D016757:Death, Sudden, Cardiac; D006327:Heart Block / Q000209:etiology / Q000628:therapy*; D006801:Humans; D008297:Male; D010138:Pacemaker, Artificial / Q000009:adverse effects*