title: Klippel-Trenaunay syndrome with small vessel pulmonary arterial hypertension.
abstract: A patient with Klippel-Trenaunay syndrome and pulmonary arterial hypertension not associated with chronic thrombo-embolic pulmonary hypertension is described. It is hypothesised that pulmonary arterial hypertension is another complication associated with the Klippel-Trenaunay syndrome, possibly due to haemodynamic changes of small vessel abnormalities.
authors.affiliation: Departement of Internal Medicine, University Hospital of Zurich, Switzerland. silvia.ulrich@usz.ch
authors.forename: S
authors.initials: S
authors.lastname: Ulrich
authors.forename: M
authors.initials: M
authors.lastname: Fischler
authors.forename: B
authors.initials: B
authors.lastname: Walder
authors.forename: T
authors.initials: T
authors.lastname: Pfammatter
authors.forename: R
authors.initials: R
authors.lastname: Speich
mesh_terms: D006801:Humans; D006976:Hypertension, Pulmonary / Q000209:etiology*; D007715:Klippel-Trenaunay-Weber Syndrome / Q000150:complications*; D008297:Male; D008833:Microcirculation; D008875:Middle Aged; D011655:Pulmonary Embolism / Q000209:etiology*