Spontaneous rupture of extrahepatic choledochal cyst: two pediatric cases and literature review.
Spontaneous rupture of extrahepatic choledochal cysts is very rare. Neonatal cases generally present with biliary ascites, and older children with acute abdomen. Although the cause is unclear, accumulation of protein plugs in an anomalous pancreaticobiliary junction, irritation of the cyst wall due to reflux of pancreatic juice, and weakness due to a developmental error such as common channel syndrome have all been suggested to play contributing roles. The treatment of choice is complete excision of the cyst and hepatico-jejunostomy. In newborns who are in a poor condition, the primary treatment should be simple peritoneal drainage.
Arda
I S
IS
Department of Pediatric Surgery, Baskent University Faculty of Medicine, 06490 Bahçelievler Ankara, Turkey. serdara@baskent-ank.edu.tr
Tuzun
M
M
Aliefendioglu
D
D
Hicsonmez
A
A
D000006:Abdomen, Acute / Q000209:etiology; D002648:Child; D015529:Choledochal Cyst / Q000150:complications / Q000175:diagnosis / Q000601:surgery; D002768:Choledochostomy; D002915:Chylous Ascites / Q000209:etiology; D017809:Fatal Outcome; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D012422:Rupture, Spontaneous / Q000175:diagnosis / Q000601:surgery