Mitral valve replacement for mitral stenosis secondary to Hunter's syndrome.
Hunter's syndrome is a rare, X-linked recessive, mucopolysaccharidosis. Survival into adulthood is uncommon. Mitral valve disease, predominantly regurgitation, has been reported in these patients. We have found no reports of mitral valve replacement for mitral stenosis secondary to Hunter's syndrome in the English literature. We report that mitral valve replacement for this pathology is a viable treatment option in an adult patient; however, specific precautions must be considered.
Bhattacharya
Kausik
K
Department of Cardiothoracic Surgery, Western Infirmary, Glasgow, United Kingdom. k.bhattacharya@clinmed.gla.ac.uk
Gibson
Simon C
SC
Pathi
Vivek L
VL
D000328:Adult; D019918:Heart Valve Prosthesis Implantation / Q000379:methods*; D006801:Humans; D008297:Male; D008943:Mitral Valve; D008946:Mitral Valve Stenosis / Q000209:etiology* / Q000473:pathology / Q000601:surgery; D016532:Mucopolysaccharidosis II / Q000150:complications*