Rare endocrine tumours of the GI tract.
Functional pancreatic endocrine tumors other than gastrinoma and insulinoma are quite rare. The principles of management include the diagnosis and management of the functional hormonal syndrome, and management of the potentially malignant tumor. Optimally, control of the hormonal syndrome is achieved preoperatively to stabilize the patient status for the operation, however, resection may be an important part of the control of the hormonal syndrome. Ultimately, the only curative treatment for these neoplasms is complete tumour resection, when feasible.
Doherty
Gerard M
GM
Department of Surgery, University of Michigan, 2920 Taubman Center, 1500 East Medical Center Drive, Ann Arbor, MI 48109, USA. gerardd@umich.edu
D000328:Adult; D017677:Age Distribution; D000368:Aged; D000971:Antineoplastic Combined Chemotherapy Protocols / Q000627:therapeutic use; D001707:Biopsy, Needle; D005260:Female; D005935:Glucagonoma / Q000453:epidemiology* / Q000473:pathology / Q000628:therapy; D006801:Humans; D007150:Immunohistochemistry; D015994:Incidence; D008297:Male; D008875:Middle Aged; D009367:Neoplasm Staging; D010180:Pancreatectomy / Q000379:methods; D010190:Pancreatic Neoplasms / Q000453:epidemiology* / Q000473:pathology / Q000628:therapy; D035583:Rare Diseases; D018570:Risk Assessment; D017678:Sex Distribution; D013005:Somatostatinoma / Q000453:epidemiology* / Q000473:pathology / Q000628:therapy; D015996:Survival Rate; D014057:Tomography, X-Ray Computed / Q000379:methods; D016896:Treatment Outcome; D018608:Ultrasonography, Doppler / Q000379:methods; D003969:Vipoma / Q000453:epidemiology* / Q000473:pathology / Q000628:therapy