title: Staged correction of double discordance, situs inversus, and absence of true pulmonary arteries.
abstract: The case of a young boy with an extremely rare and complex cardiac malformation is described. Situs inversus, dextrocardia, double discordance with pulmonary atresia, absence of true pulmonary arteries, and systemico-pulmonary collateral arteries was the original diagnosis. Three preparatory operations were necessary to reconstruct and unifocalize the pulmonary vascular tree. At the age of 7 years complete correction with intraoperative stenting of the left neopulmonary artery was successfully performed. After more than 3 years from the definitive operation, the patient is alive with no physical limitations.
authors.affiliation: Division of Cardiac Surgery, Private Non-Profit Hospital Poliambulanza, Brescia, Italy. cch-segreteria.poli@poliambulanza.it
authors.forename: Federico
authors.initials: F
authors.lastname: Brunelli
authors.forename: Andrea
authors.initials: A
authors.lastname: Amaducci
authors.forename: Giordano
authors.initials: G
authors.lastname: Tasca
authors.forename: Zen
authors.initials: Z
authors.lastname: Mhagna
authors.forename: Bruno
authors.initials: B
authors.lastname: Amari
mesh_terms: D002648:Child; D006330:Heart Defects, Congenital / Q000601:surgery*; D006801:Humans; D007223:Infant; D008297:Male; D011651:Pulmonary Artery / Q000002:abnormalities* / Q000601:surgery; D012086:Reoperation