Klippel-Trenaunay syndrome with small vessel pulmonary arterial hypertension.
A patient with Klippel-Trenaunay syndrome and pulmonary arterial hypertension not associated with chronic thrombo-embolic pulmonary hypertension is described. It is hypothesised that pulmonary arterial hypertension is another complication associated with the Klippel-Trenaunay syndrome, possibly due to haemodynamic changes of small vessel abnormalities.
Ulrich
S
S
Departement of Internal Medicine, University Hospital of Zurich, Switzerland. silvia.ulrich@usz.ch
Fischler
M
M
Walder
B
B
Pfammatter
T
T
Speich
R
R
D006801:Humans; D006976:Hypertension, Pulmonary / Q000209:etiology*; D007715:Klippel-Trenaunay-Weber Syndrome / Q000150:complications*; D008297:Male; D008833:Microcirculation; D008875:Middle Aged; D011655:Pulmonary Embolism / Q000209:etiology*